KEGG   Cyclopterus lumpus (lumpfish): 117741328
Entry
117741328         CDS       T09199                                 
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
clum  Cyclopterus lumpus (lumpfish)
Pathway
clum00280  Valine, leucine and isoleucine degradation
clum00640  Propanoate metabolism
clum00785  Lipoic acid metabolism
clum01100  Metabolic pathways
clum01210  2-Oxocarboxylic acid metabolism
Module
clum_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:clum00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    117741328 (bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    117741328 (bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    117741328 (bckdha)
Enzymes [BR:clum01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     117741328 (bckdha)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C Spore_III_AB
Other DBs
NCBI-GeneID: 117741328
NCBI-ProteinID: XP_034404191
Ensembl: ENSCLMG00005009609
UniProt: A0A8C2XS55
LinkDB
Position
13:complement(12231117..12236126)
AA seq 447 aa
MAAAVRSVNKMYGVCFNASRQTTGLTASRLLQHRAFRVGAVRRQQSFDSTLEKPQFPGAS
AEFVDELKFIQPNVISGIPVYRVMDRQGNIINPSQDPQLSKETVLNFYQKMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHIGSAAALDPSDLVFGQYREAGVLMYRGFPLDMFMAQC
YANADDLGKGRQMPVHYGSKDLNFVTISSPLATQIPQAAGAAYAIKRENMNRAVICYFGE
GAASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMLSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYMTTRGWWSEDDERSWRKQSRKTVMEAFEKAEKRLKPSPELMFTDVYEEMTP
NLNKQREAMWRHVQQYKEHYPLDQYEK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggcggctgtgaggagtgtgaacaaaatgtatggagtgtgcttcaacgcttcccgt
cagacgacaggactgacggcgtctcggttgcttcaacacagagccttcagagtcggtgcc
gtgcgccggcagcagtcctttgactcaacactggaaaagccccagttccctggagcctca
gccgagtttgtggatgagcttaagttcatccagcccaacgtcatctctgggatcccagtg
taccgggtgatggacaggcagggcaacatcatcaacccttctcaagatcctcagctctcc
aaagaaacggttctgaacttctatcagaagatgactctgctgaacacaatggaccgcatt
ctttacgagtcacagagacagggtcggatctccttctatatgaccaactacggcgaggag
ggcacacacattggcagcgctgctgctctcgacccaagcgacttagtcttcggtcaatac
agagaagctggagtgctgatgtaccgcggcttccctctggacatgttcatggctcagtgc
tacgccaacgccgatgacctcggcaagggccggcagatgcccgtgcactatggctccaaa
gatctgaacttcgtcaccatctcctctcctctggccactcagatccctcaggcggccgga
gctgcatacgccatcaagagagagaacatgaaccgtgccgtgatttgttactttggcgag
ggggcggccagcgaaggggacgcacacgccggcttcaacttctctgccaccctggagtgc
cctctgatattcttctgccgtaacaatggctacgccatctccacccccaccaacgagcag
tacaggggcgatggcatcgccgctcgtgggccagggtatggcatgctgtccatccgtgtc
gatggcaacgacgtgtttgccgtgtacaatgctacgaaggaggcgcgccgcagagccgtg
gccgagaaccagcccttcctcattgaagcgatgacctacagaattggccaccacagcacc
agtgacgacagctcggcctaccgctcggtggacgaggtgaactactgggacaagcaggac
caccccatctcccggctgagacattacatgacgacccgaggctggtggagtgaggacgac
gagaggagctggcggaagcagtctcgcaagacggtgatggaggcgttcgagaaggccgag
aaacgcctcaagcccagccccgagctgatgtttacggacgtgtacgaggagatgacaccc
aatctgaacaaacagagagaggccatgtggaggcacgtgcagcagtacaaggagcactac
ccactcgaccagtatgagaaatga

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