KEGG   Callorhinchus milii (elephant shark): 103172759
Entry
103172759         CDS       T03088                                 
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
cmk  Callorhinchus milii (elephant shark)
Pathway
cmk00280  Valine, leucine and isoleucine degradation
cmk00640  Propanoate metabolism
cmk00785  Lipoic acid metabolism
cmk01100  Metabolic pathways
cmk01210  2-Oxocarboxylic acid metabolism
Module
cmk_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:cmk00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    103172759 (bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    103172759 (bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    103172759 (bckdha)
Enzymes [BR:cmk01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     103172759 (bckdha)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N PolC_DP2_central
Other DBs
NCBI-GeneID: 103172759
NCBI-ProteinID: XP_042201342
UniProt: V9KWK1
LinkDB
Position
Unknown
AA seq 447 aa
MAAVAAALGRLGRRWSGLGRCGPRGLSRPHLATASGPRRSLSASQEFTSLDEKPKFPGAS
AEFVDSLNFIQPNVISGIPIYRVMDRQGQIMNTSEDPKLPKDMVLKFYQKMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHIGSAAALNATDLVFGQYREAGVLMYRGYPLELFMGQC
YANAKDEGKGRQMPVHYGSNIHHFVTISSPLATQIPQAVGAAYSFKMAQGDRAVICYFGE
GAASEGDAHAGFNFSATLECPIIFFCRNNGYAISTPTHEQYRGDGIAARGPGYGIMSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKKD
HPISRLRHYMVSKGWWDEEQEKAWRKQSRKRVMEAFEEAERCLKPKLENMFTDVYEDMPP
QLKKQQESLGRHLKMYGEHYPIDLFDK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggcggtggcggcggcgctcgggcggttgggccggagatggagcggcctcggcagg
tgcggcccccgcggcctctcccggcctcacctcgccacggcctccgggcccaggcgctca
ctgtccgcctcacaggagttcacatcgctggacgagaagcccaagttcccgggagcctcg
gctgagtttgtggacagcctgaattttattcaaccgaatgtcatctccggcatccccatt
tacagagtcatggaccggcaagggcagatcatgaacacgagtgaagatcccaagctgccg
aaagacatggtgctgaagttttaccagaagatgactctgctgaacacgatggaccgtata
ctgtacgaatctcagcggcagggccggatctccttctacatgaccaattacggggaggag
ggcacacacatcggcagcgcagcggctctgaatgccaccgacctcgtgtttgggcagtac
agggaagcgggcgtcctcatgtaccgcggctaccccctggagctcttcatgggccagtgt
tacgccaacgccaaggacgagggcaaaggccggcagatgccggttcactacggcagcaac
atccaccactttgtcaccatctcctctcctctggccacgcaaattccccaagccgtggga
gccgcctactccttcaagatggctcagggcgaccgggccgtgatctgctacttcggggaa
ggagccgccagtgaaggggacgcccacgctggcttcaacttctccgccaccctcgagtgt
cccatcatcttcttctgcaggaacaacggctacgccatctccaccccaacccacgagcag
tacaggggcgacggcatcgctgccagaggccctggttatggtatcatgtcgatccgagtt
gacggtaacgacgtcttcgccgtttacaacgccaccaaagaggcgcggcggagagcggtg
gcggaaaaccagcccttcctcatcgaggctatgacctacaggatcggccatcacagcacc
agcgacgacagctcagcctatcggtcggtggatgaggtcaactactgggacaagaaggac
caccccatctccaggctccggcactacatggtgagcaagggctggtgggacgaggagcag
gagaaggcctggaggaagcagtccaggaagcgggtcatggaggccttcgaggaggccgag
cggtgcctgaagcccaagctggagaacatgttcaccgacgtgtacgaggacatgcctccc
cagctgaagaagcagcaggagtctctgggaaggcacctgaagatgtacggggagcattac
cccatcgacctcttcgacaaataa

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