Cavia porcellus (domestic guinea pig): 100715185
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Entry
100715185 CDS
T07777
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
cpoc
Cavia porcellus (domestic guinea pig)
Pathway
cpoc00280
Valine, leucine and isoleucine degradation
cpoc00640
Propanoate metabolism
cpoc00785
Lipoic acid metabolism
cpoc01100
Metabolic pathways
cpoc01210
2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:
cpoc00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100715185 (Bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100715185 (Bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100715185 (Bckdha)
Enzymes [BR:
cpoc01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100715185 (Bckdha)
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Ortholog
Paralog
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
100715185
NCBI-ProteinID:
XP_003462030
Ensembl:
ENSCPOG00000000333
UniProt:
H0UTP1
LinkDB
All DBs
Position
Unknown
AA seq
446 aa
AA seq
DB search
MAIAACATRVLGQSRGLGQVALLLLRWPGVRGLARSNPHRQQQQTFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEEVLKFYRSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNMSDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANTNRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTYEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLVSRGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPNPYLLFSDVYQEMPAR
LRKQRESLAQHLQTYGEHYPLDHFDK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcgatagcggcctgcgcgacgagagtcttgggccaaagccgaggcctgggccaggtt
gcccttctgttgctgcggtggcctggggttcgggggttggctagatctaatccccacagg
cagcagcaacagactttctcctccctggatgacaaaccccagttcccaggggcctcagca
gagttcatagacaagcttgagttcatccagcccaatgtcatctctgggatccccatctac
cgtgtcatggaccgccaaggccagatcatcaaccccagcgaggacccccacctgccccag
gaggaggtgctgaagttctacaggagtatgacgctcctcaacaccatggatagaatcctc
tatgagtcccagcgacagggccggatctccttctacatgaccaactatggagaagagggc
acgcatgtgggcagtgcagctgccctggatagcacggacctggtgtttggccagtaccgg
gaggcaggtgtgctgatgtaccgggactaccccctggagctgttcatggcccagtgttac
ggcaatatgagtgacccaggcaaggggcgccagatgcctgtccactatggctgcaaggag
cgccactttgtcaccatctcctccccactggccacacagatccctcaggctgtaggggca
gcctacgcggccaagcgggccaacaccaacagagttgtcatctgttatttcggtgagggg
gctgccagtgagggagatgcacatgctggcttcaatttcgctgccactcttgagtgcccc
atcatcttcttctgccggaacaatggctacgctatctccacgcccacctatgagcagtac
cgaggagacggcatcgcggcccgaggtcctggatatggcatcatgtccatccgtgtggat
ggcaatgatgtgttcgctgtgtacaacgctaccaaggaggcccggcggcgggctgtggca
gagaaccagcccttcctcattgaagccatgacctacagaattgggcaccacagcaccagt
gatgacagctcggcgtaccgctcggtagatgaggttaattactgggacaagcaggaccac
cccatctcacggctaaggcattacctggtgagccgaggctggtgggatgaggaacaagag
aaagcctggcggaagcagtcacgcaagaaggtgatggaggccttcgaacaggctgagcgg
aagctgaagcccaacccctacctgctcttctctgatgtgtaccaggagatgcctgctcgg
ctccgcaagcagcgggagtctctggcccagcacctgcagacctatggggagcactatccc
ttggaccacttcgacaagtga
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