KEGG   Cavia porcellus (domestic guinea pig): 100715185
Entry
100715185         CDS       T07777                                 
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
cpoc  Cavia porcellus (domestic guinea pig)
Pathway
cpoc00280  Valine, leucine and isoleucine degradation
cpoc00640  Propanoate metabolism
cpoc00785  Lipoic acid metabolism
cpoc01100  Metabolic pathways
cpoc01210  2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:cpoc00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100715185 (Bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100715185 (Bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100715185 (Bckdha)
Enzymes [BR:cpoc01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100715185 (Bckdha)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 100715185
NCBI-ProteinID: XP_003462030
Ensembl: ENSCPOG00000000333
UniProt: H0UTP1
LinkDB
Position
Unknown
AA seq 446 aa
MAIAACATRVLGQSRGLGQVALLLLRWPGVRGLARSNPHRQQQQTFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEEVLKFYRSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNMSDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANTNRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTYEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLVSRGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPNPYLLFSDVYQEMPAR
LRKQRESLAQHLQTYGEHYPLDHFDK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcgatagcggcctgcgcgacgagagtcttgggccaaagccgaggcctgggccaggtt
gcccttctgttgctgcggtggcctggggttcgggggttggctagatctaatccccacagg
cagcagcaacagactttctcctccctggatgacaaaccccagttcccaggggcctcagca
gagttcatagacaagcttgagttcatccagcccaatgtcatctctgggatccccatctac
cgtgtcatggaccgccaaggccagatcatcaaccccagcgaggacccccacctgccccag
gaggaggtgctgaagttctacaggagtatgacgctcctcaacaccatggatagaatcctc
tatgagtcccagcgacagggccggatctccttctacatgaccaactatggagaagagggc
acgcatgtgggcagtgcagctgccctggatagcacggacctggtgtttggccagtaccgg
gaggcaggtgtgctgatgtaccgggactaccccctggagctgttcatggcccagtgttac
ggcaatatgagtgacccaggcaaggggcgccagatgcctgtccactatggctgcaaggag
cgccactttgtcaccatctcctccccactggccacacagatccctcaggctgtaggggca
gcctacgcggccaagcgggccaacaccaacagagttgtcatctgttatttcggtgagggg
gctgccagtgagggagatgcacatgctggcttcaatttcgctgccactcttgagtgcccc
atcatcttcttctgccggaacaatggctacgctatctccacgcccacctatgagcagtac
cgaggagacggcatcgcggcccgaggtcctggatatggcatcatgtccatccgtgtggat
ggcaatgatgtgttcgctgtgtacaacgctaccaaggaggcccggcggcgggctgtggca
gagaaccagcccttcctcattgaagccatgacctacagaattgggcaccacagcaccagt
gatgacagctcggcgtaccgctcggtagatgaggttaattactgggacaagcaggaccac
cccatctcacggctaaggcattacctggtgagccgaggctggtgggatgaggaacaagag
aaagcctggcggaagcagtcacgcaagaaggtgatggaggccttcgaacaggctgagcgg
aagctgaagcccaacccctacctgctcttctctgatgtgtaccaggagatgcctgctcgg
ctccgcaagcagcgggagtctctggcccagcacctgcagacctatggggagcactatccc
ttggaccacttcgacaagtga

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