KEGG   Cavia porcellus (domestic guinea pig): 100731951
Entry
100731951         CDS       T07777                                 
Symbol
Bckdhb
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
cpoc  Cavia porcellus (domestic guinea pig)
Pathway
cpoc00280  Valine, leucine and isoleucine degradation
cpoc00640  Propanoate metabolism
cpoc00785  Lipoic acid metabolism
cpoc01100  Metabolic pathways
cpoc01210  2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:cpoc00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100731951 (Bckdhb)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100731951 (Bckdhb)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100731951 (Bckdhb)
Enzymes [BR:cpoc01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100731951 (Bckdhb)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C
Other DBs
NCBI-GeneID: 100731951
NCBI-ProteinID: XP_003474801
Ensembl: ENSCPOG00000010332
UniProt: H0VGN2
LinkDB
Position
Unknown
AA seq 392 aa
MAAAVASAGRLLRLRAAQAERHWRRLRGAGLAQGFLQPASAGKDAVQTRHVTHFTFQPDP
ESQDHGQTQKMNLFQAITSALDNSLARDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRAPWGCVGHGALYHSQCPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYSIPLSQAEVLQEGSDITLVAWGTQVHVIREVASMAREKLGVSCE
IIDLRTIIPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcggccgcagtggcgagtgcgggccggctgctgaggctccgtgcggcccaagcagag
aggcactggcgtcggctacgcggtgcgggtctggctcagggctttctgcagcctgcctcc
gctggcaaggatgcggttcagacgcggcacgtgactcacttcactttccagccggacccg
gagtcccaggatcacgggcaaactcagaaaatgaatctttttcaggcaataacaagtgcc
ttggacaactcattagccagagatcctactgcagtaatatttggtgaagatgttgccttt
ggtggagtcttcagatgcactgtaggcttgcgagacaaatacggaaaagacagagttttt
aataccccgttgtgtgaacaaggaatcgttggatttggaattggaattgcagtcactggt
gctactgccattgccgaaattcagtttgcagattatattttccctgcttttgatcaaatt
gttaatgaagctgccaagtatcgttaccgctctggggatctttttaactgcggaagcctc
acgatcagagctccttggggctgtgttggtcatggggctctctatcattctcagtgtcct
gaagctttttttgcccattgccctggaatcaaggtggttatacccagaagcccttttcag
gctaagggacttcttctgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactctacagggcagcagtggaacaggttcctgtagaaccctacagtattccactg
tcacaagctgaagtcctacaggaaggaagtgatattactctagttgcctggggcactcag
gttcatgtgatcagggaagtagcttctatggcaagagaaaagcttggagtgtcttgtgaa
ataattgatctaaggactattataccttgggatgtggatacagtttgcaagtctgtgatc
aaaacgggtcgacttttaatcagtcacgaggctcccttgacaggtggttttgcatccgag
atcagctccacagttcaggaagaatgtttcttgaacctagaagctcctatatccagagta
tgtggctatgacacaccatttcctcacatttttgaacccttttatatcccagataaatgg
aaatgctatgatgcccttcgaaaaatgatcaactattga

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