KEGG   Delphinapterus leucas (beluga whale): 111180820
Entry
111180820         CDS       T05885                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
dle  Delphinapterus leucas (beluga whale)
Pathway
dle00280  Valine, leucine and isoleucine degradation
dle00640  Propanoate metabolism
dle00785  Lipoic acid metabolism
dle01100  Metabolic pathways
dle01210  2-Oxocarboxylic acid metabolism
Module
dle_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:dle00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    111180820 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    111180820 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    111180820 (BCKDHA)
Enzymes [BR:dle01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     111180820 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N DDE_Tnp_IS66
Other DBs
NCBI-GeneID: 111180820
NCBI-ProteinID: XP_022441286
UniProt: A0A2Y9P7R8
LinkDB
Position
Unknown
AA seq 445 aa
MAVAAAAARVWGSSRGLGRVGLLLLRRSGARGLARSHPQRQQQHFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPTQL
RKQQESLARHLQTYGEHYPLDHFEK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgctgcggcgagggtttggggatcaagtcgaggcttgggccgggtt
ggccttctccttctgcggcggtcaggggctcgtgggctggctagatcacatccccagagg
cagcagcagcacttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaatcccagcgaggatccccacctgccccaggag
aaggtgctcaagttctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcagccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactaccccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcgtcatctgttacttcggagagggcgcg
gccagtgagggggacgcccacgccggcttcaacttcgccgccaccctcgagtgccccgtc
atcttcttctgccggaacaacggctatgccatctccacgcccacctccgagcagtaccgc
ggggacggcatcgcggctcgaggccccggatacggcatcctgtccatccgcgtggatggc
aatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagcgac
gacagctcagcgtaccgctcagtggatgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
ctgaagcccagccccagcctgctcttctcagatgtgtatcaggagatgcctacccagctc
cgcaagcagcaggagtctttggcccgtcacctccagacctatggggaacactaccccctg
gatcacttcgagaagtga

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