KEGG   DISEASE: 正常圧水頭症
エントリ  
H01676                                                             
名称    
正常圧水頭症
概要    
Normal pressure hydrocephalus (NPH) is a progressive brain disease characterized by gait impairment, urinary incontinence, and dementia, and by ventricular enlargement in the absence of elevated intracranial pressure. NPH can be secondary to disease processes that cause inflammation of the arachnoid, such as subarachnoid hemorrhage, traumatic brain injury, or meningitis. As many as half of patients with NPH have no identifiable risk factor, and it is called idiopathic normal pressure hydrocephalus (INPH). Although INPH is usually considered an acquired form of hydrocephalus because the onset of symptoms is not until late in life, it has been reported that a subset of patients with INPH may actually have congenital hydrocephalus. Symptoms can be alleviated with a cerebrospinal fluid (CSF) shunt.
カテゴリ  
神経系疾患
階層分類  
ICD-11 による疾患分類 [BR:jp08403]
 08 神経系の疾患
  髄液圧または髄液流の疾患
   8D64  水頭症
    H01676  正常圧水頭症
リンク   
ICD-11: 8D64.04
MeSH: D006850
OMIM: 236690 611808
文献    
  著者
Golz L, Ruppert FH, Meier U, Lemcke J
  タイトル
Outcome of modern shunt therapy in patients with idiopathic normal pressure hydrocephalus 6 years postoperatively.
  雑誌
J Neurosurg 121:771-5 (2014)
DOI:10.3171/2014.6.JNS131211
文献    
  著者
Wilson RK, Williams MA
  タイトル
Evidence that congenital hydrocephalus is a precursor to idiopathic normal pressure hydrocephalus in only a subset of patients.
  雑誌
J Neurol Neurosurg Psychiatry 78:508-11 (2007)
DOI:10.1136/jnnp.2006.108761
文献    
PMID:16239882 (treatment)
  著者
McGirt MJ, Woodworth G, Coon AL, Thomas G, Williams MA, Rigamonti D
  タイトル
Diagnosis, treatment, and analysis of long-term outcomes in idiopathic normal-pressure hydrocephalus.
  雑誌
Neurosurgery 57:699-705; discussion 699-705 (2005)
DOI:10.1227/01.NEU.0000175724.00147.10
文献    
  著者
Zhang J, Williams MA, Rigamonti D
  タイトル
Heritable essential tremor-idiopathic normal pressure hydrocephalus (ETINPH).
  雑誌
Am J Med Genet A 146A:433-9 (2008)
DOI:10.1002/ajmg.a.31958
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