KEGG   DISEASE: 乳幼児肝血管腫
エントリ  
H01875                                                             
名称    
乳幼児肝血管腫
概要    
Infantile hepatic hemangioma (IHH), although rare, is the most common benign hepatic vascular tumor in the first year of age. They are sub-classified in focal, multiple and diffuse lesions, based on degree of unaffected liver parenchyma. Most lesions are clinically silent and self-limiting, whereas others can become symptomatic, manifesting as cardiac failure, fulminant hepatic failure and abdominal compartment syndrome. The term IHH is preferred to "hemangioendothelioma" because the clinical and biologic behavior is similar to infantile hemangiomas [DS:H01482] that affect the skin and other parts of the body.
カテゴリ  
新生物
階層分類  
ICD-11 による疾患分類 [BR:jp08403]
 02 腫瘍
  良性腫瘍, ただしリンパ, 造血, 中枢神経系または関連組織を除く
   良性間葉系腫瘍
    2E81  良性血管性腫瘍
     H01875  乳幼児肝血管腫
指定難病 [jp08407.html]
 H01875
リンク   
ICD-11: 2E81.2Y
ICD-10: D18.00
MeSH: D006391
文献    
  著者
Kassarjian A, Zurakowski D, Dubois J, Paltiel HJ, Fishman SJ, Burrows PE
  タイトル
Infantile hepatic hemangiomas: clinical and imaging findings and their correlation with therapy.
  雑誌
AJR Am J Roentgenol 182:785-95 (2004)
DOI:10.2214/ajr.182.3.1820785
文献    
  著者
Christison-Lagay ER, Burrows PE, Alomari A, Dubois J, Kozakewich HP, Lane TS, Paltiel HJ, Klement G, Mulliken JB, Fishman SJ
  タイトル
Hepatic hemangiomas: subtype classification and development of a clinical practice algorithm and registry.
  雑誌
J Pediatr Surg 42:62-7; discussion 67-8 (2007)
DOI:10.1016/j.jpedsurg.2006.09.041
文献    
  著者
Vergine G, Marsciani A, Pedini A, Brocchi S, Marsciani M, Desiderio E, Bertelli S, Vecchi V
  タイトル
Efficacy of propranolol treatment in thyroid dysfunction associated with severe infantile hepatic hemangioma.
  雑誌
Horm Res Paediatr 78:256-60 (2012)
DOI:10.1159/000337253
文献    
  著者
Varrasso G, Schiavetti A, Lanciotti S, Sapio M, Ferrara E, Grazia A, Clerico A
  タイトル
Propranolol as first-line treatment for life-threatening diffuse infantile hepatic hemangioma: A case report.
  雑誌
Hepatology 66:283-285 (2017)
DOI:10.1002/hep.29028
文献    
  著者
Hsi Dickie B, Fishman SJ, Azizkhan RG
  タイトル
Hepatic vascular tumors.
  雑誌
Semin Pediatr Surg 23:168-72 (2014)
DOI:10.1053/j.sempedsurg.2014.06.018
文献    
  著者
Gnarra M, Behr G, Kitajewski A, Wu JK, Anupindi SA, Shawber CJ, Zavras N, Schizas D, Salakos C, Economopoulos KP
  タイトル
History of the infantile hepatic hemangioma: From imaging to generating a differential diagnosis.
  雑誌
World J Clin Pediatr 5:273-80 (2016)
DOI:10.5409/wjcp.v5.i3.273
LinkDB    

» English version

DBGET integrated database retrieval system