Entry |
|
Symbol |
BCKDHB
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
|
KO |
K00167 | 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4] |
|
Organism |
ecb Equus caballus (horse)
|
Pathway |
ecb00280 | Valine, leucine and isoleucine degradation |
ecb01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
ecb_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:ecb00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100065300 (BCKDHB)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100065300 (BCKDHB)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100065300 (BCKDHB)
Enzymes [BR:ecb01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100065300 (BCKDHB)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
10:35121968..35379410
|
AA seq |
392 aa
MAVAAAIACRLLRLRAAGAGGHWRRLRGAGLPRGFLQPASAGEDAAQWRRVAHFTFQPDP
EPLEYGQTQKMNLFQAVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRAPWGCVGHGAVYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCE
VIDLRTIIPWDVDTVCKSVIKTGRLLVSHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHVFEPFYIPDKWKCYDALRKMINY |
NT seq |
1179 nt +upstreamnt +downstreamnt
atggcggtcgcagcagcgattgcgtgccggctgttgaggctccgtgcagccggggccggg
ggacactggcgtcggctgcgtggcgcggggctgccgcggggcttcctgcagcccgcctcg
gccggcgaggatgctgcccagtggcggcgggtggctcacttcactttccagccggacccg
gagcccctggagtacgggcaaactcagaaaatgaatcttttccaggcagtaacaagtgcc
ttggacaactcattggctaaagatcctactgcagtaatatttggtgaagatgttgccttt
ggtggagtctttagatgtactgttggcttgcgagacaaatatggaaaagatagagttttt
aacactccattgtgtgaacaaggaattgttgggtttggaattggaattgcagtcactggt
gccactgccattgcagaaattcagtttgcagattatattttccctgcttttgatcagatt
gttaacgaagccgccaagtatcgctatcgctctggggatctttttaattgtggaagcctc
accatccgggccccttggggctgtgttggccatggggctgtctaccattctcagagtccg
gaagctttttttgcacactgcccaggaatcaaggtggttgtacccagaagccctttccag
gccaagggacttcttttgtcgtgcatagaggataaaaatccttgtatattttttgaacct
aagatactttaccgggcagcagtggagcaggttcctgtggaaccgtataacattcccctc
tcccaggccgaagtcatccaggaagggagcgatgttactctggttgcctggggcactcag
gttcatgtgatccgagaggtcgcttccatggctcaggaaaagctcggagtgtcttgtgaa
gtcattgacctgaggactataataccttgggatgtggatacggtttgcaagtctgtgatc
aaaacagggcgactgctggtcagtcacgaggctcccttgacgggcggctttgcttccgag
atcagctcgaccgttcaggaagaatgtttcctgaacctagaggctcctatatcaagagta
tgtgggtacgacacaccatttccccacgtttttgagcctttctacatcccagacaaatgg
aagtgctatgatgcccttcgaaagatgatcaactattga |