KEGG   Eumetopias jubatus (Steller sea lion): 114202542
Entry
114202542         CDS       T07240                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
eju  Eumetopias jubatus (Steller sea lion)
Pathway
eju00280  Valine, leucine and isoleucine degradation
eju00640  Propanoate metabolism
eju00785  Lipoic acid metabolism
eju01100  Metabolic pathways
eju01210  2-Oxocarboxylic acid metabolism
Module
eju_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:eju00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    114202542 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    114202542 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    114202542 (BCKDHA)
Enzymes [BR:eju01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     114202542 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 114202542
NCBI-ProteinID: XP_027951602
LinkDB
Position
Unknown
AA seq 448 aa
MAVAAAAAAARIWGSSRGLGQAGLLLLRRPGAWGLARSLPQRRAQQHFPSLDDKPQFPGA
SAEFVDKLEFIQPNVISGIPVYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDR
ILYESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQ
CYGNASDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFG
EGAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIR
VDGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVSYWDKQ
DHPISRLRHHLQSRGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPSPSLLFSDVYQEMP
PQLRKQQEALARHLQTYGEHYPLDHFEK
NT seq 1347 nt   +upstreamnt  +downstreamnt
atggcggtggcggcggcggctgcagcagcgaggatctggggctcaagtcgaggcttgggc
caggctggcctcctgcttctgcggcggcctggggcttggggtctggctagatctctcccc
cagagacgggcacagcagcacttcccgtccctggatgacaagccccagttcccgggggcc
tcggcggagtttgtagacaagctggaattcatccagcccaatgtcatctctgggatccct
gtctaccgcgtcatggatcgccagggccagatcatcaaccccagcgaggatccccacctg
ccccaggagaaggtgctcaagttctacaagagcatgactctgctcaacaccatggaccgc
atcctctatgagtcccagcgacagggccggatctccttctacatgaccaactacggtgag
gaggggacgcacgtggggagcgcagcggcgctggacaacacggacctggtgttcggccag
taccgggaggcaggtgtgctcatgtaccgggactaccccctggagctgttcatggcccag
tgctacggcaacgcgagtgacctgggcaagggccgccagatgcccgtgcactatggctgc
aaggagcgccatttcgtcaccatctcctctccgctggccacgcagatcccgcaggcggtg
ggggcggcctacgctgccaagcgggccaacgccaacagggtggtcatctgctactttggg
gagggggcagccagcgagggggacgcacacgccggcttcaacttcgccgccaccctcgag
tgccccatcatcttcttctgccggaacaacggctatgccatctccacgcccacctcggag
cagtaccgcggggacggcatcgccgcccgaggccccggctacggcatcatgtccatccgc
gtggatggcaacgacgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgcgct
gtggcggagaaccagcccttcctcatcgaggccatgacctacaggatcggccaccacagc
actagtgatgacagctcagcctaccgctcggtggacgaggtcagttactgggacaagcaa
gaccaccccatctcgcggctgcgccaccacctgcagagccggggctggtgggacgaggag
caggagaaggcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggcg
gagcggaagccaaagcccagccccagcctgctcttctcagacgtgtaccaggagatgccc
ccccagctccgcaagcagcaggaggccctggcccggcacctccagacctacggggagcac
taccccctggaccactttgagaagtga

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