Entry |
|
Symbol |
BCKDHA
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
ggo Gorilla gorilla gorilla (western lowland gorilla)
|
Pathway |
ggo00280 | Valine, leucine and isoleucine degradation |
ggo01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
ggo_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:ggo00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
101128832 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
101128832 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
101128832 (BCKDHA)
Enzymes [BR:ggo01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
101128832 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
20:join(53077835..53077942,53090639..53090818,53090925..53091011,53094047..53094155,53099151..53099312,53102161..53102367,53102626..53102767,53102995..53103166,53104434..53104604)
|
AA seq |
445 aa
MAVAIAAARVWRPNRGLSQAALLLLRRPGARGLARSHPRRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLDHFDK |
NT seq |
1338 nt +upstreamnt +downstreamnt
atggcggtagcgatcgctgcagcgagggtctggcggccaaaccgtggtctgagccaggct
gccctcctgctgctgcggcggcctggggctcggggactggctagatctcacccccgcagg
cagcagcagcagttttcatctctggatgacaagccccagttcccaggggcctcggcggag
tttatagataagttggaattcatccagcccaacgtcatctctggaatccccatctaccgc
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccgaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggtgaggagggcacg
cacgtggggagtgccgccgccctggacaacacggacctggtatttggccagtaccgggag
gcaggtgtgctgatgtatcgggactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcgccagatgcccgtccactacggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacgcagatccctcaggcggtgggggcggcg
tacgcagccaagcgggccaatgccaacagggtcgtcatctgttacttcggcgagggggcg
gccagtgagggggacgcccatgccggcttcaacttcgctgccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcattgcagcacgaggccccgggtatggcatcatgtcaatccgcgtggatggt
aatgatgtgtttgccgtatacaacgccacaaaggaggcccgacggcgggctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcagcataccgctcggtggatgaggtcaattactgggataaacaggaccacccc
atctcccggctgcggcactatctgctgagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtctctggcccgccacctgcagacctacggggagcactacccactg
gatcacttcgataagtga |