Entry |
|
Symbol |
BCKDHB
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X2
|
KO |
K00167 | 2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4] |
|
Organism |
ggo Gorilla gorilla gorilla (western lowland gorilla)
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Pathway |
ggo00280 | Valine, leucine and isoleucine degradation |
ggo01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
ggo_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:ggo00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
101132793 (BCKDHB)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
101132793 (BCKDHB)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
101132793 (BCKDHB)
Enzymes [BR:ggo01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
101132793 (BCKDHB)
|
SSDB |
|
Motif |
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Other DBs |
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LinkDB |
|
Position |
5:join(104245070..104245265,104271928..104272005,104273516..104273584,104312027..104312160,104313587..104313742,104315994..104316102,104346016..104346113,104348187..104348297,104418343..104418429,104489108..104489248)
|
AA seq |
392 aa
MAVVAAAAGWLLRLRAAGAEGHWRRLPGAGLARGFLHPAATVEDAAQRRQVAHFTFQPDP
EPREYGQTQKMNLFQSVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAAEEVPIEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAKEKLGVSCE
VIDLRTIIPWDVDTICKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY |
NT seq |
1179 nt +upstreamnt +downstreamnt
atggcggttgtagcggcggctgctggctggctactgaggctcagggcggcaggggctgag
gggcactggcgtcggctccctggcgcggggctggcgcggggttttctgcaccccgccgcg
actgtcgaggatgcggcccagaggcggcaggtggctcattttactttccagccagatccg
gagccccgggagtatgggcaaactcagaaaatgaatcttttccagtcagtaacaagtgcc
ttggataactcattggccaaagatcctactgcagtaatatttggtgaagatgttgccttt
ggtggagtctttagatgcactgttggcttgcgagacaaatatggaaaagatagagttttt
aataccccattgtgtgaacaaggaattgttggatttggaatcggaattgcggtcactgga
gctactgccattgcggaaattcagttcgcagattatattttccctgcatttgatcagatt
gttaatgaagctgccaagtatcgctatcgctctggggatctttttaactgtggaagcctc
actatccggtccccttggggctgtgttggtcatggggctctctatcattctcagagtcct
gaagcattttttgcccattgcccaggaatcaaggtggttatacccagaagccctttccag
gccaaaggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagcggaagaggtccctatagaaccatacaacatcccactg
tcccaggccgaagtcatacaggaagggagtgatgttactctagttgcctggggcactcag
gttcatgtgatccgagaggtagcttccatggcaaaagaaaagcttggagtgtcttgtgaa
gtcattgatctgaggactataataccttgggatgtggacacaatttgtaagtctgtgatc
aaaacagggcgactgctaatcagtcacgaggctcccttgacaggcggctttgcatcggaa
atcagctctacagttcaggaggaatgtttcttgaacctagaggctcctatatcaagagta
tgtggttatgacacaccatttcctcacatttttgaaccattctacatcccagacaaatgg
aagtgttatgatgcccttcgaaaaatgatcaactattga |