KEGG   Heterocephalus glaber (naked mole-rat): 101705928
Entry
101705928         CDS       T02812                                 
Symbol
Bckdha
Name
(RefSeq) branched chain keto acid dehydrogenase E1, alpha polypeptide
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
hgl  Heterocephalus glaber (naked mole-rat)
Pathway
hgl00280  Valine, leucine and isoleucine degradation
hgl00640  Propanoate metabolism
hgl00785  Lipoic acid metabolism
hgl01100  Metabolic pathways
hgl01210  2-Oxocarboxylic acid metabolism
Module
hgl_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:hgl00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    101705928 (Bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    101705928 (Bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    101705928 (Bckdha)
Enzymes [BR:hgl01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     101705928 (Bckdha)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 101705928
NCBI-ProteinID: XP_004873055
UniProt: A0A0P6JFL4
LinkDB
Position
Un
AA seq 444 aa
MAAAVSAASVWRQSLAQAALLLLRRPGVRGLARSQSHRQQQQAFSSLDDKPQFPGASAEF
IDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYRSMTLLNTMDRILYE
SQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRDYPLELFMAQCYGN
MSDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRIVICYFGEGAA
SEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTYEQYRGDGIAARGPGYGIMSIRVDGN
DVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPI
SRLRHYLVSHGWWDEDQEKTWRKQSRKMVMEAFAQAERKLKPNPNLLFSDVYQEMPAQLR
KQQESLAQHLQTYGEHYPLDHFDK
NT seq 1335 nt   +upstreamnt  +downstreamnt
atggcggcagcggtctccgcggcgagcgtctggaggcaaagcctggcccaggctgccctc
ctactgctgcggcggcctggggttcgggggttggctagatctcaatcccacaggcagcag
cagcaggccttctcctccctggatgacaaaccccagttcccaggggcctccgcagagttc
atagacaagctcgagttcatccagcccaatgtcatctccgggatccccatctaccgagtc
atggaccgccaaggccagatcatcaaccccagcgaggaccctcatcttccccaggagaag
gtgctgaagttctacaggagcatgacactgctcaacaccatggaccgcatcctctatgag
tcccagcggcagggccggatctccttctacatgaccaactatggagaggaggggacgcat
gtgggcagtgcagctgccctagacagcacagacctggtgtttggccagtaccgggaggca
ggtgtgctgatgtaccgggactaccccctggagctgttcatggcccagtgctacggcaac
atgagtgatccaggcaagggccgccagatgcctgtccactacggctgcaaggagcgccac
tttgtcaccatctcctctccgctggccacacagatccctcaggctgtgggggcggcctac
gcggccaagcgggccaatgccaacaggattgtcatctgttattttggtgagggggcagcc
agcgagggggatgcccatgctggcttcaacttcgctgccacccttgagtgccccatcatc
ttcttctgcaggaacaatggctatgccatctccacacccacctatgagcagtaccgcggg
gatggcatcgcagcccgaggccctgggtatggcatcatgtccatccgtgtggatggcaat
gacgtgttcgctgtgtacaatgccaccaaggaggcccggcggcgggctgtggcagagaac
cagcccttcctcatcgaagccatgacctacaggattgggcaccacagcaccagtgatgac
agctcggcataccgctcggtggatgaggttaattactgggacaagcaggaccatcctatc
tcacggctgaggcactacctggtgagccacggctggtgggatgaggaccaagagaagacc
tggcggaagcaatctcggaagatggtgatggaagcctttgcgcaggccgagcggaagcta
aagcccaaccccaacctgctgttctctgatgtgtaccaggagatgcctgcccagctccgt
aagcagcaggagtctctggcccagcatctgcagacctatggggagcactatcccctggac
cactttgacaagtga

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