KEGG   Hylobates moloch (silvery gibbon): 116480645
Entry
116480645         CDS       T08803                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X3
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
hmh  Hylobates moloch (silvery gibbon)
Pathway
hmh00280  Valine, leucine and isoleucine degradation
hmh00640  Propanoate metabolism
hmh00785  Lipoic acid metabolism
hmh01100  Metabolic pathways
hmh01210  2-Oxocarboxylic acid metabolism
Module
hmh_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:hmh00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    116480645 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    116480645 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    116480645 (BCKDHA)
Enzymes [BR:hmh01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     116480645 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 116480645
NCBI-ProteinID: XP_032028715
LinkDB
Position
Unknown
AA seq 445 aa
MAVAIVAARVWRPNRGLSQAALLLLRRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPTQL
RKQQESLARHLQTYGEHYPLEHFDK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtagcgatcgttgcagcgagggtctggcggccaaaccgtggcctgagccaggct
gccctcctgctgctgcggcggcctggggctcgaggactggctagatctcacccccacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggcagag
tttatagacaagttggaattcatccagcccaacgtcatctctggaatccccatctaccgc
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccgaaggag
aaggtgctgaagctctataagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggtgaggaaggcacg
cacgtggggagtgctgccgccctggacaacacggatctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgggactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcgccagatgcccgtccactacggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacgcagatccctcaggcagtgggggcggcc
tatgcagccaagcgggccaacgccaacagggtggtcatctgttactttggcgagggggcg
gccagcgaaggggacgcccatgccggcttcaacttcgctgccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcattgcagcacgaggccctgggtatggcatcatgtcaatccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacgccgggctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggattgggcaccacagcaccagtgac
gacagttcagcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggctgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtttatcaagagatgcccacccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcacttcgataagtga

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