Hylobates moloch (silvery gibbon): 116480645
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Entry
116480645 CDS
T08803
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X3
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
hmh
Hylobates moloch (silvery gibbon)
Pathway
hmh00280
Valine, leucine and isoleucine degradation
hmh00640
Propanoate metabolism
hmh00785
Lipoic acid metabolism
hmh01100
Metabolic pathways
hmh01210
2-Oxocarboxylic acid metabolism
Module
hmh_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
hmh00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
116480645 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
116480645 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
116480645 (BCKDHA)
Enzymes [BR:
hmh01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
116480645 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
116480645
NCBI-ProteinID:
XP_032028715
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All DBs
Position
Unknown
AA seq
445 aa
AA seq
DB search
MAVAIVAARVWRPNRGLSQAALLLLRRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPTQL
RKQQESLARHLQTYGEHYPLEHFDK
NT seq
1338 nt
NT seq
+upstream
nt +downstream
nt
atggcggtagcgatcgttgcagcgagggtctggcggccaaaccgtggcctgagccaggct
gccctcctgctgctgcggcggcctggggctcgaggactggctagatctcacccccacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggcagag
tttatagacaagttggaattcatccagcccaacgtcatctctggaatccccatctaccgc
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccgaaggag
aaggtgctgaagctctataagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggtgaggaaggcacg
cacgtggggagtgctgccgccctggacaacacggatctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgggactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcgccagatgcccgtccactacggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacgcagatccctcaggcagtgggggcggcc
tatgcagccaagcgggccaacgccaacagggtggtcatctgttactttggcgagggggcg
gccagcgaaggggacgcccatgccggcttcaacttcgctgccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcattgcagcacgaggccctgggtatggcatcatgtcaatccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacgccgggctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggattgggcaccacagcaccagtgac
gacagttcagcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggctgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtttatcaagagatgcccacccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcacttcgataagtga
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