VARIANT: 2176v1
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Entry
2176v1 Variant
Name
FANCC mutation
Type
Loss of function
Gene
FANCC
FA complementation group C [KO:
K10890
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
613899
Network
nt06508
Interstrand crosslink repair
Disease
H00238
Fanconi anemia
Reference
PMID:
8103176
Authors
Murer-Orlando M, Llerena JC Jr, Birjandi F, Gibson RA, Mathew CG
Title
FACC gene mutations and early prenatal diagnosis of Fanconi's anaemia.
Journal
Lancet 342:686 (1993)
DOI:
10.1016/0140-6736(93)91800-2
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