VARIANT: 35v1
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Entry
35v1 Variant
Name
ACADS deficiency
Type
Loss of function
Gene
ACADS
acyl-CoA dehydrogenase short chain [KO:
K00248
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
606885
Network
nt06020
beta-Oxidation in mitochondria
Disease
H01980
SCAD deficiency
Reference
PMID:
2808706
Authors
Naito E, Indo Y, Tanaka K
Title
Short chain acyl-coenzyme A dehydrogenase (SCAD) deficiency. Immunochemical demonstration of molecular heterogeneity due to variant SCAD with differing stability.
Journal
J Clin Invest 84:1671-4 (1989)
DOI:
10.1172/JCI114346
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