VARIANT: 4126v1
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Entry
4126v1 Variant
Name
MANBA mutation
Type
Loss of function
Gene
MANBA
beta-mannosidase precursor [KO:
K01192
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
609489
Network
nt06551
Lysosome
Disease
H00140
beta-Mannosidosis
Reference
PMID:
9384606
Authors
Alkhayat AH, Kraemer SA, Leipprandt JR, Macek M, Kleijer WJ, Friderici KH
Title
Human beta-mannosidase cDNA characterization and first identification of a mutation associated with human beta-mannosidosis.
Journal
Hum Mol Genet 7:75-83 (1998)
DOI:
10.1093/hmg/7.1.75
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