VARIANT: 5836v1
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Entry
5836v1 Variant
Name
PYGL deficiency
Gene
PYGL
glycogen phosphorylase L [KO:
K00688
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
613741
Network
nt06017
Glycogen metabolism
Disease
H01944
Glycogen storage disease type VI
Reference
PMID:
9529348
Authors
Burwinkel B, Bakker HD, Herschkovitz E, Moses SW, Shin YS, Kilimann MW
Title
Mutations in the liver glycogen phosphorylase gene (PYGL) underlying glycogenosis type VI.
Journal
Am J Hum Genet 62:785-91 (1998)
DOI:
10.1086/301790
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