VARIANT: 875v1
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Entry
875v1 Variant
Name
CBS deficiency
Type
Loss of function
Gene
CBS
cystathionine beta-synthase [KO:
K01697
]
Organism
hsa_var Human gene variants (Homo sapiens)
Variation
mutations
OmimVar:
613381
Network
nt06030
Methionine metabolism
Disease
H00183
Homocystinuria
Reference
PMID:
7506602
Authors
Hu FL, Gu Z, Kozich V, Kraus JP, Ramesh V, Shih VE
Title
Molecular basis of cystathionine beta-synthase deficiency in pyridoxine responsive and nonresponsive homocystinuria.
Journal
Hum Mol Genet 2:1857-60 (1993)
DOI:
10.1093/hmg/2.11.1857
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