Hyla sarda (Sardinian treefrog): 130290329
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Entry
130290329 CDS
T11475
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
hsq Hyla sarda (Sardinian treefrog)
Pathway
hsq00280
Valine, leucine and isoleucine degradation
hsq00640
Propanoate metabolism
hsq00785
Lipoic acid metabolism
hsq01100
Metabolic pathways
hsq01210
2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:
hsq00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
130290329 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
130290329 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
130290329 (BCKDHA)
Enzymes [BR:
hsq01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
130290329 (BCKDHA)
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Motif
Pfam:
E1_dh
DXP_synthase_N
TPP_enzyme_C
Motif
Other DBs
NCBI-GeneID:
130290329
NCBI-ProteinID:
XP_056393787
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Position
9:complement(136894696..136916636)
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AA seq
431 aa
AA seq
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MAALRTLLRVRAAVGWRIVGGRQATRSRSEFTSLEEKPQFPGASAVFVDSLEFIQPNVIS
GIPIYRVMDRQGQIINPSEDPNIPKEKVLKFYHTMTLLNTMDRILYESQRQGRISFYMTN
YGEEGTHVGSAAALSDTDLVFGQYREAGVLMYRGYPLDLFMAQCYGNSLDPGKGRQMPVH
YGSKDLNFVTISSPLATQIPQAVGAAYAMKRENADRAVICYFGEGAASEGDAHAAFNFSA
TLECPVLFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDGNDVFAVYNATKEAR
RRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRHYMMHNGWW
DDEQEKIWRKKSRKMVMEAFEKAERERKPSIQHMFTDVYAEMPPSLKKQEESLKKHLKVY
GEHYPMDSYEH
NT seq
1296 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgctgaggacgttgttgagggtccgggcagcggttggatggagaatagtcggg
gggagacaggcgacccgctcccgcagtgagttcacctcattggaggaaaagcctcagttt
cctggagcctctgcagtttttgtggactctctggagttcatccaacccaatgtcatctcc
gggatccccatctacagggtgatggaccgtcaggggcagattattaaccccagcgaagac
cccaatatccctaaggagaaagtcctaaagttctatcacacgatgacgctgctgaacacc
atggatagaatcctgtatgagtctcagaggcagggaagaatttcattctatatgacaaac
tacggagaggaggggacgcacgtgggcagtgctgccgccctgagtgacacagaccttgta
ttcgggcagtatcgggaggcaggagtcctgatgtacagagggtatcctcttgatcttttc
atggcgcagtgctatggtaattccttagatcctggcaaaggaagacaaatgcctgtacac
tacggctctaaggacttaaactttgtgaccatttcctcaccattggcaacacagattcca
caagctgtgggtgcggcctatgccatgaaacgggaaaatgcagaccgcgctgtcatctgc
tacttcggtgaaggagccgcaagtgagggagatgcccatgctgcttttaacttttctgct
actttggagtgccccgtgcttttcttctgcaggaacaatggctacgccatatctacccct
acttctgagcagtatcgtggggatggcattgctgccagaggtcctggttatggcatcatg
tcaattcgagtggatggtaatgatgtctttgcagtgtacaatgccaccaaagaggcaaga
cggagagcagtggcagagaaccagccgttcctgatagaagccatgacatacaggattggg
caccacagcaccagcgatgacagctctgcctaccgctctgtagatgaggtgaattactgg
gacaagcaggaccaccctatttctcggcttcgtcactacatgatgcacaatggctggtgg
gatgatgaacaggagaaaatatggaggaagaagtcacgaaaaatggttatggaagctttt
gaaaaggccgagcgcgaacgtaagcccagcatccaacacatgttcacagacgtctacgcc
gagatgccgccgagtcttaagaaacaggaggagtccttgaaaaaacatctgaaggtttat
ggggaacattatcctatggacagctatgaacactaa
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