KEGG   Hyla sarda (Sardinian treefrog): 130290329
Entry
130290329         CDS       T11475                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
hsq  Hyla sarda (Sardinian treefrog)
Pathway
hsq00280  Valine, leucine and isoleucine degradation
hsq00640  Propanoate metabolism
hsq00785  Lipoic acid metabolism
hsq01100  Metabolic pathways
hsq01210  2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:hsq00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    130290329 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    130290329 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    130290329 (BCKDHA)
Enzymes [BR:hsq01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     130290329 (BCKDHA)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C
Other DBs
NCBI-GeneID: 130290329
NCBI-ProteinID: XP_056393787
LinkDB
Position
9:complement(136894696..136916636)
AA seq 431 aa
MAALRTLLRVRAAVGWRIVGGRQATRSRSEFTSLEEKPQFPGASAVFVDSLEFIQPNVIS
GIPIYRVMDRQGQIINPSEDPNIPKEKVLKFYHTMTLLNTMDRILYESQRQGRISFYMTN
YGEEGTHVGSAAALSDTDLVFGQYREAGVLMYRGYPLDLFMAQCYGNSLDPGKGRQMPVH
YGSKDLNFVTISSPLATQIPQAVGAAYAMKRENADRAVICYFGEGAASEGDAHAAFNFSA
TLECPVLFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDGNDVFAVYNATKEAR
RRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRHYMMHNGWW
DDEQEKIWRKKSRKMVMEAFEKAERERKPSIQHMFTDVYAEMPPSLKKQEESLKKHLKVY
GEHYPMDSYEH
NT seq 1296 nt   +upstreamnt  +downstreamnt
atggcggcgctgaggacgttgttgagggtccgggcagcggttggatggagaatagtcggg
gggagacaggcgacccgctcccgcagtgagttcacctcattggaggaaaagcctcagttt
cctggagcctctgcagtttttgtggactctctggagttcatccaacccaatgtcatctcc
gggatccccatctacagggtgatggaccgtcaggggcagattattaaccccagcgaagac
cccaatatccctaaggagaaagtcctaaagttctatcacacgatgacgctgctgaacacc
atggatagaatcctgtatgagtctcagaggcagggaagaatttcattctatatgacaaac
tacggagaggaggggacgcacgtgggcagtgctgccgccctgagtgacacagaccttgta
ttcgggcagtatcgggaggcaggagtcctgatgtacagagggtatcctcttgatcttttc
atggcgcagtgctatggtaattccttagatcctggcaaaggaagacaaatgcctgtacac
tacggctctaaggacttaaactttgtgaccatttcctcaccattggcaacacagattcca
caagctgtgggtgcggcctatgccatgaaacgggaaaatgcagaccgcgctgtcatctgc
tacttcggtgaaggagccgcaagtgagggagatgcccatgctgcttttaacttttctgct
actttggagtgccccgtgcttttcttctgcaggaacaatggctacgccatatctacccct
acttctgagcagtatcgtggggatggcattgctgccagaggtcctggttatggcatcatg
tcaattcgagtggatggtaatgatgtctttgcagtgtacaatgccaccaaagaggcaaga
cggagagcagtggcagagaaccagccgttcctgatagaagccatgacatacaggattggg
caccacagcaccagcgatgacagctctgcctaccgctctgtagatgaggtgaattactgg
gacaagcaggaccaccctatttctcggcttcgtcactacatgatgcacaatggctggtgg
gatgatgaacaggagaaaatatggaggaagaagtcacgaaaaatggttatggaagctttt
gaaaaggccgagcgcgaacgtaagcccagcatccaacacatgttcacagacgtctacgcc
gagatgccgccgagtcttaagaaacaggaggagtccttgaaaaaacatctgaaggtttat
ggggaacattatcctatggacagctatgaacactaa

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