| Entry |
|
| Symbol |
MOCS3, UBA4
|
| Name |
|
| Pathway |
|
| Reaction |
| R07459 | ATP:[sulfur-carrier protein] adenylyltransferase |
| R07461 | [enzyme]-S-sulfanyl-L-cysteine:adenylyl-[sulfur-carrier protein] sulfurtransferase |
|
| Disease |
| H02311 | Molybdenum cofactor deficiency |
|
| Brite |
KEGG Orthology (KO) [BR:ko00001]
09120 Genetic Information Processing
09123 Folding, sorting and degradation
04122 Sulfur relay system
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03016 Transfer RNA biogenesis
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
04121 Ubiquitin system
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
Enzymes [BR:ko01000]
2. Transferases
2.7 Transferring phosphorus-containing groups
2.7.7 Nucleotidyltransferases
2.7.7.80 molybdopterin-synthase adenylyltransferase
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
2.8 Transferring sulfur-containing groups
2.8.1 Sulfurtransferases
2.8.1.11 molybdopterin synthase sulfurtransferase
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
Transfer RNA biogenesis [BR:ko03016]
Eukaryotic type
tRNA modification factors
Thiolation factors
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
Ubiquitin system [BR:ko04121]
Ubiquitin-activating enzymes (E1)
UBL-activating enzymes
K11996 MOCS3, UBA4; adenylyltransferase and sulfurtransferase
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| Other DBs |
|
| Genes |
» show all
|
| Reference |
|
| Authors |
Matthies A, Nimtz M, Leimkuhler S |
| Title |
Molybdenum cofactor biosynthesis in humans: identification of a persulfide group in the rhodanese-like domain of MOCS3 by mass spectrometry. |
| Journal |
|
| Sequence |
|
| Reference |
|
| Authors |
Marelja Z, Stocklein W, Nimtz M, Leimkuhler S |
| Title |
A novel role for human Nfs1 in the cytoplasm: Nfs1 acts as a sulfur donor for MOCS3, a protein involved in molybdenum cofactor biosynthesis. |
| Journal |
|
| Sequence |
|
| Reference |
|
| Authors |
Schlieker CD, Van der Veen AG, Damon JR, Spooner E, Ploegh HL |
| Title |
A functional proteomics approach links the ubiquitin-related modifier Urm1 to a tRNA modification pathway. |
| Journal |
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| Sequence |
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| LinkDB |
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