| Entry |
|
| Symbol |
PMPCB, MAS1
|
| Name |
mitochondrial-processing peptidase subunit beta [EC: 3.4.24.64]
|
| Disease |
| H01894 | Multiple mitochondrial dysfunctions syndrome |
|
| Brite |
KEGG Orthology (KO) [BR:ko00001]
09180 Brite Hierarchies
09181 Protein families: metabolism
01002 Peptidases and inhibitors
K17732 PMPCB, MAS1; mitochondrial-processing peptidase subunit beta
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K17732 PMPCB, MAS1; mitochondrial-processing peptidase subunit beta
Enzymes [BR:ko01000]
3. Hydrolases
3.4 Acting on peptide bonds (peptidases)
3.4.24 Metalloendopeptidases
3.4.24.64 mitochondrial processing peptidase
K17732 PMPCB, MAS1; mitochondrial-processing peptidase subunit beta
Peptidases and inhibitors [BR:ko01002]
Metallo peptidases
Family M16: pitrilysin family
K17732 PMPCB, MAS1; mitochondrial-processing peptidase subunit beta
Mitochondrial biogenesis [BR:ko03029]
Mitochondrial protein import machinery
Matrix
Other matrix factors
K17732 PMPCB, MAS1; mitochondrial-processing peptidase subunit beta
|
| Genes |
» show all
|
| Reference |
|
| Authors |
Witte C, Jensen RE, Yaffe MP, Schatz G |
| Title |
MAS1, a gene essential for yeast mitochondrial assembly, encodes a subunit of the mitochondrial processing protease. |
| Journal |
|
| Sequence |
|
| Reference |
|
| Authors |
Koutnikova H, Campuzano V, Koenig M |
| Title |
Maturation of wild-type and mutated frataxin by the mitochondrial processing peptidase. |
| Journal |
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| LinkDB |
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