ORTHOLOGY: K18162
Help
Entry
K18162 KO
Symbol
NDUFAF5
Name
NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
Pathway
map04714
Thermogenesis
Disease
H00473
Mitochondrial complex I deficiency
Brite
KEGG Orthology (KO) [BR:
ko00001
]
09150 Organismal Systems
09159 Environmental adaptation
04714 Thermogenesis
K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5
09180 Brite Hierarchies
09182 Protein families: genetic information processing
03029 Mitochondrial biogenesis
K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5
Mitochondrial biogenesis [BR:
ko03029
]
Mitochondrial quality control factors
Mitochondrial respiratory chain complex assembly factors
Complex-I assembly factors
K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5
BRITE hierarchy
Genes
HSA:
79133
(NDUFAF5)
PPS:
100988527
(NDUFAF5)
GGO:
101136645
(NDUFAF5)
PON:
100172355
(NDUFAF5)
PPYG:
129022071
(NDUFAF5)
NLE:
100587530
(NDUFAF5)
HMH:
116460879
(NDUFAF5)
SSYN:
129474366
(NDUFAF5)
MCC:
694292
(NDUFAF5)
MCF:
102119816
(NDUFAF5)
MTHB:
126929386
MNI:
105481497
(NDUFAF5)
CSAB:
103214452
(NDUFAF5)
CATY:
105582066
(NDUFAF5)
PANU:
101010757
(NDUFAF5)
TGE:
112633022
(NDUFAF5)
MLEU:
105550316
(NDUFAF5)
RRO:
104655751
(NDUFAF5)
RBB:
108527878
(NDUFAF5)
TFN:
117068441
(NDUFAF5)
PTEH:
111546433
(NDUFAF5)
CANG:
105527227
(NDUFAF5)
CJC:
100405232
(NDUFAF5)
SBQ:
101039392
(NDUFAF5)
ANAN:
105732734
(NDUFAF5)
CSYR:
103259459
(NDUFAF5)
MMUR:
105880070
(NDUFAF5)
LCAT:
123622824
(NDUFAF5)
PCOQ:
105807133
(NDUFAF5)
OGA:
100947029
(NDUFAF5)
MMU:
69487
(Ndufaf5)
MCAL:
110289506
(Ndufaf5)
MPAH:
110318019
(Ndufaf5)
RNO:
296190
(Ndufaf5)
MCOC:
116091024
(Ndufaf5)
ANU:
117704163
(Ndufaf5)
ASYL:
127685980
(Ndufaf5)
MUN:
110551771
(Ndufaf5)
CGE:
100770742
(Ndufaf5)
MAUA:
101839991
(Ndufaf5)
PROB:
127221375
(Ndufaf5)
PLEU:
114688129
114702959
MORG:
121460464
(Ndufaf5)
MFOT:
126496740
AAMP:
119814722
(Ndufaf5)
HGL:
101704983
(Ndufaf5)
CPOC:
100728734
(Ndufaf5)
CCAN:
109688318
(Ndufaf5)
DORD:
105981710
(Ndufaf5)
DSP:
122096024
(Ndufaf5)
PLOP:
125353247
(Ndufaf5)
NCAR:
124976020
MMMA:
107140056
(Ndufaf5)
ITI:
101974060
(Ndufaf5)
OCU:
100337968
TUP:
102485829
(NDUFAF5)
GVR:
103583459
(NDUFAF5)
CFA:
477150
(NDUFAF5)
CLUD:
112673563
(NDUFAF5)
VVP:
112922747
(NDUFAF5)
VLG:
121478034
(NDUFAF5)
NPO:
129522030
(NDUFAF5)
AML:
100482342
(NDUFAF5)
UMR:
103674446
(NDUFAF5)
UAH:
113258328
(NDUFAF5)
UAR:
123799926
(NDUFAF5)
ELK:
111141723
LLV:
125108418
MPUF:
101679558
(NDUFAF5)
MNP:
132021717
(NDUFAF5)
MLK:
131808118
(NDUFAF5)
NVS:
122916273
(NDUFAF5)
ORO:
101385043
(NDUFAF5)
EJU:
114216433
(NDUFAF5)
ZCA:
113937460
(NDUFAF5)
MLX:
118011227
(NDUFAF5)
NSU:
110577411
110589985
(NDUFAF5)
LWW:
102727040
(NDUFAF5)
FCA:
101096224
(NDUFAF5)
PYU:
121012503
(NDUFAF5)
PCOO:
112868985
(NDUFAF5)
PBG:
122496583
(NDUFAF5)
PVIV:
125161980
(NDUFAF5)
LRUF:
124504212
LGF:
123580521
(NDUFAF5)
AJU:
106981484
PTG:
102955251
(NDUFAF5)
PPAD:
109274843
(NDUFAF5)
PUC:
125936830
PLEZ:
122215825
(NDUFAF5)
HHV:
120221603
(NDUFAF5)
BTA:
522230
(NDUFAF5)
BOM:
102275824
(NDUFAF5)
BIU:
109567862
(NDUFAF5)
BBIS:
104991600
(NDUFAF5)
CHX:
102186133
(NDUFAF5)
OAS:
101111213
(NDUFAF5)
BTAX:
128058521
(NDUFAF5)
CSUM:
138091358
(NDUFAF5)
ODA:
120869165
(NDUFAF5)
CCAD:
122448055
(NDUFAF5)
MREE:
136159084
(NDUFAF5)
OVR:
110147343
(NDUFAF5)
MBEZ:
129556433
(NDUFAF5)
SSC:
100520522
(NDUFAF5)
CFR:
102504024
(NDUFAF5)
CBAI:
105083134
(NDUFAF5)
CDK:
105088314
(NDUFAF5)
VPC:
102543478
(NDUFAF5)
BACU:
103013094
(NDUFAF5)
BMUS:
118881817
(NDUFAF5)
LVE:
103086707
(NDUFAF5)
OOR:
101276610
(NDUFAF5)
LALB:
132505784
(NDUFAF5)
DLE:
111185016
(NDUFAF5)
PCAD:
102991403
(NDUFAF5)
PSIU:
116740202
(NDUFAF5)
NASI:
112393285
(NDUFAF5)
ECB:
100063169
(NDUFAF5)
EPZ:
103559906
(NDUFAF5)
EAI:
106825794
(NDUFAF5)
MYB:
102261542
(NDUFAF5)
MYD:
102757779
(NDUFAF5)
MMYO:
118662941
(NDUFAF5)
MLF:
102421060
(NDUFAF5)
MDT:
132239344
(NDUFAF5)
MYUM:
139013685
(NDUFAF5)
PKL:
118707624
(NDUFAF5)
EFUS:
103285687
(NDUFAF5)
MNA:
107536348
(NDUFAF5)
DRO:
112303837
(NDUFAF5)
SHON:
118976664
(NDUFAF5)
AJM:
119040922
(NDUFAF5)
PDIC:
114506880
(NDUFAF5)
PHAS:
123815196
(NDUFAF5)
MMF:
118619168
(NDUFAF5)
PPAM:
129070881
(NDUFAF5)
HAI:
109378985
(NDUFAF5)
RFQ:
117015928
(NDUFAF5)
PALE:
102881066
(NDUFAF5)
PGIG:
120611894
(NDUFAF5)
PVP:
105298877
(NDUFAF5)
RAY:
107504297
(NDUFAF5)
TOD:
119232494
(NDUFAF5)
SARA:
101558434
(NDUFAF5)
SFUM:
130030369
(NDUFAF5)
SETR:
126010764
(NDUFAF5)
LAV:
100668356
(NDUFAF5)
TMU:
101349023
ETF:
101642408
(NDUFAF5)
DNM:
101422845
(NDUFAF5)
MDO:
100033270
(NDUFAF5)
GAS:
123236906
(NDUFAF5)
SHR:
105749897
(NDUFAF5)
AFZ:
127548477
PCW:
110208296
(NDUFAF5)
TVP:
118829195
118840763
(NDUFAF5)
PBRV:
138151881
(NDUFAF5)
OAA:
100084682
(NDUFAF5)
TACU:
119932540
(NDUFAF5)
GGA:
416742
(NDUFAF5)
PCOC:
116232136
(NDUFAF5)
MGP:
100546289
(NDUFAF5)
CJO:
107310895
(NDUFAF5)
TPAI:
128082818
(NDUFAF5)
LMUT:
125689527
(NDUFAF5)
NMEL:
110395323
(NDUFAF5)
APLA:
101804936
(NDUFAF5)
ACYG:
106036592
(NDUFAF5)
CATA:
118251130
(NDUFAF5)
AFUL:
116488302
(NDUFAF5)
TGU:
100218560
(NDUFAF5)
LSR:
110469263
(NDUFAF5)
SCAN:
103819346
(NDUFAF5)
PMOA:
120505986
(NDUFAF5)
OTC:
121346957
(NDUFAF5)
PRUF:
121357109
(NDUFAF5)
ATRC:
139587756
(NDUFAF5)
GFR:
102044925
(NDUFAF5)
FAB:
101812559
(NDUFAF5)
OMA:
130250875
(NDUFAF5)
PHI:
102112251
(NDUFAF5)
PMAJ:
107202406
(NDUFAF5)
CCAE:
111926637
(NDUFAF5)
CCW:
104691535
(NDUFAF5)
CBRC:
103623010
(NDUFAF5)
ACOE:
138107598
(NDUFAF5)
ETL:
114062734
(NDUFAF5)
ZAB:
102073815
(NDUFAF5)
ZLE:
135446040
(NDUFAF5)
ACHL:
103799850
(NDUFAF5)
SVG:
106865157
(NDUFAF5)
MMEA:
130575251
(NDUFAF5)
HRT:
120750957
(NDUFAF5)
SATI:
136359667
(NDUFAF5)
CCIC:
134042740
(NDUFAF5)
FPG:
101923411
(NDUFAF5)
FCH:
102047254
(NDUFAF5)
CCRI:
104165108
(NDUFAF5)
NNT:
104400000
(NDUFAF5)
SHAB:
115609229
(NDUFAF5)
ACUN:
113477998
(NDUFAF5)
ACHC:
115344941
(NDUFAF5)
HALD:
104318076
(NDUFAF5)
HLE:
104836445
(NDUFAF5)
AGEN:
126038220
HHAR:
128140424
(NDUFAF5)
CSTI:
104550495
(NDUFAF5)
LDI:
104350777
(NDUFAF5)
MNB:
103773736
(NDUFAF5)
PPUS:
135176795
(NDUFAF5)
BRHI:
104496907
(NDUFAF5)
EGZ:
104122529
(NDUFAF5)
NNI:
104022488
(NDUFAF5)
PCRI:
104037581
(NDUFAF5)
PADL:
103913113
(NDUFAF5)
AFOR:
103901649
(NDUFAF5)
FGA:
104073854
(NDUFAF5)
GSTE:
104252085
(NDUFAF5)
CLV:
102083570
(NDUFAF5)
MUI:
104533696
(NDUFAF5)
PGUU:
104467535
(NDUFAF5)
PLET:
104625334
(NDUFAF5)
EHS:
104508457
(NDUFAF5)
CMAC:
104473852
(NDUFAF5)
CUCA:
104055446
(NDUFAF5)
TEO:
104370001
(NDUFAF5)
BREG:
104629601
(NDUFAF5)
OHA:
104329130
(NDUFAF5)
ACAR:
104518299
(NDUFAF5)
CPEA:
104390983
(NDUFAF5)
CVF:
104295667
(NDUFAF5)
RTD:
128907184
(NDUFAF5)
CRID:
134512471
(NDUFAF5)
AAM:
106498786
(NDUFAF5)
AROW:
112975913
(NDUFAF5)
NPD:
112958966
(NDUFAF5)
TGT:
104572484
(NDUFAF5)
DNE:
112980083
(NDUFAF5)
SCAM:
104143490
(NDUFAF5)
ASN:
102380664
(NDUFAF5)
AMJ:
102570302
(NDUFAF5)
CPOO:
109319512
(NDUFAF5)
GGN:
109296732
(NDUFAF5)
PSS:
102446494
(NDUFAF5)
CMY:
102946792
(NDUFAF5)
CCAY:
125633401
(NDUFAF5)
DCC:
119852522
(NDUFAF5)
CPIC:
101949279
(NDUFAF5)
TST:
117874240
(NDUFAF5)
CABI:
116830405
(NDUFAF5)
MRV:
120400327
(NDUFAF5)
ACS:
100554145
(ndufaf5)
ASAO:
132781678
(NDUFAF5)
PVT:
110083095
(NDUFAF5)
SUND:
121925683
PBI:
103053118
(NDUFAF5)
PMUR:
107293239
(NDUFAF5)
CTIG:
120297629
(NDUFAF5)
TSR:
106545588
(NDUFAF5)
PGUT:
117674412
(NDUFAF5)
APRI:
131197562
(NDUFAF5)
PTEX:
113444195
(NDUFAF5)
NSS:
113412715
(NDUFAF5)
VKO:
123035861
(NDUFAF5)
PMUA:
114593683
(NDUFAF5)
PRAF:
128409992
(NDUFAF5)
ZVI:
118082481
(NDUFAF5)
HCG:
128340003
(NDUFAF5)
STOW:
125435185
(NDUFAF5)
EMC:
129331964
(NDUFAF5)
XLA:
108716573
(ndufaf5.L)
XTR:
549152
(ndufaf5)
NPR:
108785222
(NDUFAF5)
RTEM:
120937797
(NDUFAF5)
BBUF:
120999103
(NDUFAF5)
BGAR:
122934212
(NDUFAF5)
PWL:
138295667
(NDUFAF5)
MUO:
115465684
(NDUFAF5)
GSH:
117358187
(NDUFAF5)
DRE:
794020
(ndufaf5)
SRX:
107747410
(ndufaf5)
107756989
SANH:
107675590
107684300
SGH:
107583196
107594415
CCAR:
109072131
(ndufaf5)
CAUA:
113044002
113044101
CGIB:
127949022
PTET:
122329747
LROH:
127183399
(ndufaf5)
OMC:
131540309
(ndufaf5)
PPRM:
120489730
(ndufaf5)
RKG:
130087338
(ndufaf5)
MAMB:
125271904
(ndufaf5)
CIDE:
127494847
CERY:
137031594
(ndufaf5)
MASI:
127445129
TROS:
130553284
(ndufaf5)
TDW:
130434972
(ndufaf5)
MANU:
129444097
(ndufaf5)
PDAB:
135785780
(ndufaf5)
IPU:
108258626
IFU:
128602345
(ndufaf5)
PHYP:
113537375
(ndufaf5)
SMEO:
124377774
124378602
TFD:
113663577
(ndufaf5)
TVC:
132839445
(ndufaf5)
CGAR:
128506622
(ndufaf5)
NGRA:
132866798
(ndufaf5)
TRN:
134328556
(ndufaf5)
AMEX:
103024722
(ndufaf5)
CMAO:
118797909
(ndufaf5)
EEE:
113579675
(ndufaf5)
CHAR:
105901563
(ndufaf5)
SPIL:
134087315
(ndufaf5)
TRU:
101063459
(ndufaf5)
TFS:
130527500
(ndufaf5)
TNG:
GSTEN00003845G001
LCO:
104938382
(ndufaf5)
NCC:
104959710
TBEN:
117481787
CGOB:
115006319
(ndufaf5)
PGEO:
117450549
(ndufaf5)
GACU:
117533562
117533563
EMAC:
134864206
(ndufaf5)
ELY:
117254918
(ndufaf5)
EFO:
125886378
(ndufaf5)
SLUC:
116059803
(ndufaf5)
ESP:
116679453
(ndufaf5)
PFLV:
114568381
(ndufaf5)
GAT:
120825337
(ndufaf5)
PPUG:
119218002
(ndufaf5)
AFB:
129096179
(ndufaf5)
129117001
CLUM:
117733275
(ndufaf5)
PSWI:
130189938
(ndufaf5)
CANA:
137798756
(ndufaf5)
CVE:
137884670
(ndufaf5)
MSAM:
119914922
(ndufaf5)
SCHU:
122873085
(ndufaf5)
SPUL:
138594788
(ndufaf5)
LMIX:
132993205
(ndufaf5)
ALAT:
119024081
(ndufaf5)
ASTR:
137599708
137599994
MZE:
101488053
(ndufaf5)
ONL:
100693648
(ndufaf5)
OAU:
116316243
(ndufaf5)
OLA:
101161215
(ndufaf5)
OML:
112143455
(ndufaf5)
CSAI:
133446123
(ndufaf5)
XMA:
102224877
(ndufaf5)
XCO:
114144301
(ndufaf5)
XHE:
116720119
(ndufaf5)
PRET:
103472096
(ndufaf5)
PFOR:
103156447
(ndufaf5)
PLAI:
106940199
(ndufaf5)
PMEI:
106922983
(ndufaf5)
GAF:
122828947
(ndufaf5)
PPRL:
129355578
129357054
CVG:
107094416
(ndufaf5)
CTUL:
119786988
(ndufaf5)
GMU:
124867979
(ndufaf5)
NFU:
107394237
(ndufaf5)
KMR:
108229507
(ndufaf5)
ALIM:
106535417
NWH:
119422721
(ndufaf5)
AOCE:
111563075
(ndufaf5)
EJA:
138209468
(ndufaf5)
BFRE:
138634882
(ndufaf5)
CSEM:
103383389
(ndufaf5)
POV:
109646023
(ndufaf5)
SSEN:
122761486
(ndufaf5)
SSOE:
131467093
(ndufaf5)
HHIP:
117771030
(ndufaf5)
HSP:
118118062
(ndufaf5)
PPLT:
128435574
(ndufaf5)
SMAU:
118311982
(ndufaf5)
LCF:
108888734
SDU:
111232958
(ndufaf5)
SLAL:
111653019
(ndufaf5)
XGL:
120800299
(ndufaf5)
HCQ:
109527650
(ndufaf5)
SSCV:
125968502
(ndufaf5)
PEE:
133403900
(ndufaf5)
PTAO:
133476979
(ndufaf5)
ENY:
140377901
(ndufaf5)
MALB:
109971808
(ndufaf5)
BSPL:
114857665
(ndufaf5)
SJO:
128379033
(ndufaf5)
SSCO:
133995866
(ndufaf5)
GMH:
115540032
115540043
SASA:
106586074
(ndufaf5)
STRU:
115178863
(ndufaf5)
OTW:
112222531
112230389
(ndufaf5)
OMY:
110486029
OGO:
124015335
ONE:
115103573
OKI:
109866015
OKE:
118365019
(ndufaf5)
OMM:
135522140
(ndufaf5)
OCLA:
139423864
SALP:
111982302
SNH:
120033012
CCLU:
121572402
123491423
ELS:
105021511
(ndufaf5)
OEP:
134008568
(ndufaf5)
SFM:
108926967
(ndufaf5)
PKI:
111835728
(ndufaf5)
AANG:
118221220
(ndufaf5)
AROT:
135244498
(ndufaf5)
CCOG:
133122028
(ndufaf5)
LOC:
102693913
(ndufaf5)
PSPA:
121316103
(ndufaf5)
ARUT:
117402734
(ndufaf5)
PSEX:
120516305
(ndufaf5)
LCM:
102367041
(NDUFAF5)
CMK:
103177916
(ndufaf5)
RTP:
109934242
(ndufaf5)
CPLA:
122553099
(ndufaf5)
HOC:
132819530
(ndufaf5)
LERI:
129699268
(ndufaf5)
PMRN:
116943366
(NDUFAF5)
LRJ:
133339913
133361734
BFO:
118410462
BBEL:
109470344
CIN:
100176583
SCLV:
120330168
SPU:
754687
LPIC:
129265401
AJJ:
139971798
APLC:
110978148
ARUN:
117300087
AAMU:
139947872
AFIL:
140152528
AJC:
117111944
SKO:
100377475
PFLL:
139148940
DME:
Dmel_CG8067
(CG8067)
DER:
6549514
DSE:
6609077
DSI:
Dsimw501_GD10997
(Dsim_GD10997)
DYA:
Dyak_GE12576
DAN:
6496560
6505766
DSR:
110178261
DPO:
4804876
DPE:
6602093
DMN:
108158526
117192442
DWI:
6652313
DGR:
6569062
DMO:
Dmoj_GI21212
DAZ:
108615948
DNV:
108655243
DHE:
111592228
DVI:
6624962
CCAT:
101450335
BOD:
106619889
BDR:
105228661
RZE:
108364351
108382179
AOQ:
129246013
ALUD:
128867640
TDA:
119685419
119685441
MDE:
101891536
SCAC:
106089691
LCQ:
111682382
LSQ:
119600095
CVJ:
135959648
GFS:
119636373
ECOE:
129949980
CLON:
129611627
HIS:
119654974
AGA:
1271116
ACOZ:
120955159
AARA:
120900353
AMER:
121598862
ASTE:
118504101
AMAP:
126568354
AFUN:
125768975
AMRS:
128707857
AALI:
118463302
ACOS:
131272110
AAG:
5579830
AALB:
109398921
115254125
ASUA:
134225811
CQU:
CpipJ_CPIJ019831
CPII:
120419932
CNS:
116340187
BCOO:
119071260
LLL:
129795647
PPAP:
129801846
AME:
100576544
ACER:
108000419
ALAB:
122711764
ADR:
102670771
AFLR:
100868103
BIM:
100746498
BBIF:
117211197
BVK:
117238543
BVAN:
117160383
BHUN:
126875408
BTER:
100644505
BAFF:
126926522
BPYO:
122577207
BPAS:
132915497
FVI:
122530486
CCAL:
108623322
OBB:
114875776
OLG:
117609318
MGEN:
117227618
NMEA:
116424606
CGIG:
122395662
SOC:
105193647
MPHA:
105828550
AEC:
105150666
ACEP:
105626943
PBAR:
105430676
VEM:
105568990
COBS:
139107202
TLN:
139814260
HST:
105189085
DQU:
106747976
CFO:
105250155
FEX:
115236719
PMEC:
138939043
LHU:
105668762
PGC:
109854960
OBO:
105278549
PCF:
106790615
PFUC:
122525586
VPS:
122633357
VCRB:
124429494
VVE:
124953771
NVI:
100116856
CSOL:
105365931
TPRE:
106657946
111693424
LHT:
122497822
LBD:
127288584
MDL:
103580165
CGLO:
123261319
FAS:
105270930
DAM:
107041140
AGIF:
122858800
CINS:
118071125
VCAN:
122419023
CCIN:
107271402
DSM:
124409282
NPT:
124216859
NFB:
124180205
NLO:
107220981
NVG:
124303614
AROA:
105683758
TCA:
660400
TMOL:
138135975
DPA:
109538774
ESIM:
136414120
EFOR:
136339220
SOY:
115880823
AGRG:
126736537
ATD:
109593963
CSET:
123314926
HAXR:
123676270
AGB:
108916557
LDC:
111510959
DVV:
126886902
NVL:
108559759
APLN:
108733416
PPYR:
116163391
OTU:
111416066
BMOR:
105842276
BMAN:
114244184
MSEX:
115447184
119191064
BANY:
112045118
MJU:
123870661
NIQ:
126778888
VCD:
124541903
MCIX:
123668240
PMAC:
106715611
PPOT:
106109584
PXU:
106124522
BPHI:
137922814
PRAP:
110998227
PBX:
123717355
PNAP:
125055067
ZCE:
119838133
119838160
CCRC:
123704292
LSIN:
126964472
AAGE:
121727243
HAW:
110381172
HZE:
124643795
TNL:
113498678
SLIU:
111354879
OFU:
114352663
ONU:
135085688
ATRA:
106143085
GMW:
128200252
PXY:
105381492
PGW:
126379242
LGLY:
125240319
CSTB:
134753654
CFEL:
113385796
113386806
CCRN:
123298521
API:
100159314
DNX:
107162940
AGS:
114125869
RMD:
113553299
ACOO:
126840150
DVT:
126905814
BTAB:
109042667
DCI:
103517257
CLEC:
106672811
HHAL:
106685700
NLU:
111063917
HVI:
124364229
MQU:
129000167
129001454
PHU:
Phum_PHUM283320
FOC:
113206397
TPAL:
117640866
ZNE:
110827474
CSEC:
111870725
SGRE:
126268200
BROR:
134539563
IEL:
124154008
HAMR:
139687521
FCD:
110851819
DPX:
DAPPUDRAFT_124486
DAPPUDRAFT_52557
DMK:
116918450
DPZ:
124342760
AFRA:
136032332
PVM:
113815495
PJA:
122250735
PCHN:
125043936
PMOO:
119585644
HAME:
121872588
PCLA:
123755334
CQD:
128696535
PTRU:
123504719
ESN:
126996501
MNZ:
135214375
MRJ:
136854750
PORN:
139761663
HAZT:
108667121
EAF:
111705224
LSM:
121115860
TCF:
131884109
PPOI:
119105322
DSV:
119457833
RSAN:
119375562
RMP:
119166804
VJA:
111259440
TUT:
107370880
DPTE:
113791612
DFR:
124499337
CSCU:
111629047
CVS:
136974305
ABRU:
129975599
UDV:
129227308
SDM:
118187380
LPOL:
106467628
PMEO:
129594533
129602269
CEL:
CELE_K09E4.3
(K09E4.3)
CBR:
CBG_20848
CRQ:
GCK72_006576
NAI:
NECAME_19671
BMY:
BM_BM9759
(Bm9759)
LOA:
LOAG_03676
HRO:
HELRODRAFT_96859
LGI:
LOTGIDRAFT_121553
PVUL:
126820573
PCAN:
112571369
LSAX:
138951996
BGT:
106055421
GAE:
121370073
121391448
HRF:
124134816
HRJ:
124261581
HASI:
137293600
HCRA:
139442683
CRG:
105320200
CANU:
128176431
CVN:
111128270
OED:
125649740
MYI:
110466378
PMAX:
117324100
AIRR:
138319714
MCAF:
127698489
MMER:
123541264
RPHI:
132742183
DPOL:
127857954
MAEA:
128208919
OBI:
106869034
OSN:
115210650
LJP:
135463591
LAK:
106155688
SMM:
Smp_003940
SHX:
MS3_00020005
(NDUFAF5)
OVI:
T265_01085
EGL:
EGR_06783
LLON:
135485435
NVE:
5514108
EPA:
110254122
ATEN:
116298016
ADF:
107341834
AMIL:
114975301
MCAZ:
138049935
MFOO:
137984963
PDAM:
113681830
SPIS:
111333329
DGT:
114536822
XEN:
124441817
HMG:
100210831
HSY:
130613899
RES:
135696775
TAD:
TRIADDRAFT_18584
AQU:
100633398
100638411
ATH:
AT1G22800
ALY:
9326597
CRB:
17897796
CSAT:
104740987
104756630
104776402
EUS:
EUTSA_v10007396mg
BRP:
103840826
BNA:
106401655
106407892
106429811
BOE:
106343788
RSZ:
108813761
THJ:
104800087
CIT:
102623554
CIC:
CICLE_v10020832mg
PVY:
116136048
MINC:
123228616
TCC:
18592851
GRA:
105783452
GHI:
107895063
107895094
107920758
HSYR:
120123451
DZI:
111276788
111277678
EGR:
104450732
RARG:
115727049
GMX:
100785627
100798873
GSJ:
114379832
114410501
PVU:
137834574
VRA:
106759974
VAR:
108332383
VUN:
114173575
VUM:
124827262
CCAJ:
109805594
APRC:
113858197
MTR:
11414139
TPRA:
123885444
123916540
CAM:
101502351
PSAT:
127086358
VVO:
131593541
LJA:
130745593
ADU:
107482421
AIP:
107638280
AHF:
112740906
112795625
LANG:
109337082
109361553
PCIN:
129299180
129312698
QSA:
O6P43_030046
FVE:
101313804
AANS:
126796054
RCN:
112180842
PPER:
18791205
PMUM:
103319508
PAVI:
110752003
PDUL:
117634292
MDM:
103402114
103441846
MSYL:
126601837
126631847
PXB:
103947935
103952500
103967471
PCOX:
137711760
137717242
ZJU:
107421436
MNT:
21408201
CSAV:
115713085
CSV:
101206614
CMO:
103498701
BHJ:
120079627
MCHA:
111012031
CMAX:
111472597
CMOS:
111432759
CPEP:
111796799
RCU:
8265000
MEAN:
126667925
JCU:
105638191
HBR:
110640592
MESC:
110606567
POP:
18104330
PEU:
105115350
PALZ:
118035502
PNZ:
133669983
JRE:
108985931
CILL:
122307386
CAVE:
132180250
AGLU:
133859577
QSU:
112006545
QLO:
115958961
115959060
TWL:
120007117
VVI:
100255004
VRI:
117907896
SLY:
101254842
SPEN:
107032179
SOT:
102602645
SSTN:
125865859
SDUL:
129876618
CANN:
107846078
LBB:
132632740
132632781
NTA:
107760732
107794599
NSY:
104210638
NTO:
104102603
NAU:
109226014
INI:
109161725
ITR:
115998289
SIND:
105155801
OEU:
111403697
111403698
EGT:
105959959
SSPL:
121797380
121800046
SMIL:
131003738
SHIS:
125192767
APAN:
127264353
HAN:
118483202
ECAD:
122596043
LSV:
111880579
CCAV:
112506523
112522637
DCR:
108225046
CSIN:
114299331
RVL:
131311519
AEW:
130776427
DLT:
127807345
BVG:
104895720
SOE:
110790807
CQI:
110735723
ATRI:
130814493
MOF:
131162343
NNU:
104590322
MING:
122090177
TSS:
122669403
PSOM:
113283330
113356536
OSA:
9272455
OBR:
102708112
OGL:
127756986
BDI:
100837327
ATS:
109742224
TDC:
119316257
119324455
TAES:
123076201
123112184
123132473
123136543
123144050
TUA:
125529216
125538078
LPER:
127299582
LRD:
124652760
124652954
SBI:
8082817
ZMA:
100276173
MFLO:
136502535
136502839
136508016
136508136
SITA:
101778734
SVS:
117863702
PVIR:
120666645
120696938
PHAI:
112885260
PAUA:
133905488
PDA:
103711090
EGU:
105038550
MUS:
103968407
ZOF:
122021466
122025162
DCT:
110102854
PEQ:
110027408
AOF:
109830205
MSIN:
131242783
ACAK:
137946292
NCOL:
116256975
ATR:
18433654
CJF:
131036811
SMO:
SELMODRAFT_117268
SELMODRAFT_132719
PPP:
112279464
CRE:
CHLRE_13g584750v5
VCN:
VOLCADRAFT_58666
MNG:
MNEG_4038
CSL:
COCSUDRAFT_18638
CVR:
CHLNCDRAFT_142766
APRO:
F751_6439
OLU:
OSTLU_89745
OTA:
OT_ostta14g01980
BPG:
Bathy12g01110
MIS:
MICPUN_109347
MPP:
MICPUCDRAFT_44473
CME:
CYME_CMM259C
GSL:
Gasu_27580
CCP:
CHC_T00003070001
DHA:
DEHA2G01914g
PIC:
PICST_58842
PGU:
PGUG_00681
SPAA:
SPAPADRAFT_62057
LEL:
PVL30_002005
LBG:
92207579
(LODBEIA_P23830)
CAL:
CAALFM_C301120WA
(CaO19.2514)
CTP:
CTRG_02632
COT:
CORT_0B04340
CDU:
CD36_81020
CTEN:
18248252
(PSN45_001973)
CLU:
CLUG_02652
CLUS:
A9F13_07g02101
CAUR:
CJI96_0000465
PPA:
PAS_chr3_0319
PKZ:
C5L36_0B02433
BNN:
FOA43_004293
BBRX:
BRETT_002090
OPA:
HPODL_02047
YLI:
2909080
(YALI2_C01167g)
SLB:
AWJ20_934
NCR:
NCU03439
NTE:
NEUTE1DRAFT84650
(NEUTE1DRAFT_84650)
SMP:
10801944
(SMAC4_09494)
PAN:
PODANSg6932
PBEL:
QC761_0088450
PPSD:
QC762_604000
PPSP:
QC763_0088890
PPSA:
QC764_604000
TTT:
THITE_164707
MTM:
MYCTH_2311545
CTHR:
CTHT_0005530
RTHE:
98127661
(VTJ83DRAFT_6319)
MGR:
MGG_09494
PPEI:
PpBr36_03160
PGRI:
PgNI_01538
TMN:
UCRPA7_8237
SSCK:
SPSK_09372
FGR:
FGSG_00823
FPU:
FPSE_00629
FPOA:
FPOAC1_000869
FVN:
FVRRES_01035
FVR:
FVEG_00736
FOX:
FOXG_00779
NHE:
NECHADRAFT_75103
FFC:
NCS54_00123900
FKR:
NCS57_00121600
FMU:
J7337_001254
TRE:
TRIREDRAFT_55205
TRR:
M419DRAFT_71836
TATV:
25777377
(TrAtP1_005791)
TASP:
36608751
(TrAFT101_005111)
MAW:
19247225
(J3458_022161)
MAJ:
MAA_01690
MBRN:
26247373
(NDUFAF5)
PCHM:
VFPPC_05271
CMT:
CCM_04790
AMUS:
LMH87_010113
PLJ:
28889173
(PLICBS_008360)
PTKZ:
JDV02_006285
VAL:
VDBG_01567
VDA:
VDAG_01986
CFJ:
CFIO01_04290
CLUP:
CLUP02_01462
CHIG:
CH63R_10360
CDET:
87943464
(CDEST_06961)
SAPO:
SAPIO_CDS2854
ELA:
UCREL1_7459
PFY:
PFICI_09094
SSL:
SS1G_06065
BFU:
BCIN_05g03650
MBE:
MBM_04136
PSCO:
LY89DRAFT_648410
GLZ:
GLAREA_07331
ANI:
ANIA_04918
AFM:
AFUA_3G10710
ACT:
ACLA_038600
NFI:
NFIA_066580
AOR:
AO090003000616
ANG:
An02g06370
AFV:
AFLA_001067
ALUC:
AKAW2_21104S
ACHE:
ACHE_21040A
APUU:
APUU_30941A
PCS:
N7525_000910
PDP:
PDIP_74900
POU:
POX_b02794
TMF:
EYB26_000836
TRG:
TRUGW13939_03822
CIM:
CIMG_03752
CPW:
9694009
(D8B26_003250)
URE:
UREG_07528
ABE:
ARB_05685
TVE:
TRV_04300
PBL:
PAAG_07184
PBN:
PADG_00944
AJE:
HCAG_06611
BGH:
BDBG_02908
PNO:
SNOG_11685
PTE:
PTT_07201
PTRR:
6340171
(PtrM4_004060)
BZE:
COCCADRAFT_109130
BSC:
COCSADRAFT_40212
BOR:
COCMIDRAFT_106426
AALT:
CC77DRAFT_983533
ADAC:
96084470
(ACET3X_004148)
ARAB:
EKO05_0003392
ZTR:
MYCGRDRAFT_70703
PFJ:
MYCFIDRAFT_26854
FFU:
CLAFUR5_01785
CBET:
CB0940_00425
BCOM:
BAUCODRAFT_99597
NPA:
UCRNP2_1760
TML:
GSTUM_00003095001
CNE:
CNI01100
CNB:
CNBH1050
CNG:
CNAG_04447
CGI:
CGB_H1630W
CDEU:
CNBG_2615
CDEP:
91086931
(L203_102720)
KMG:
30165817
(I203_103298)
KNE:
92181280
(IAR55_004022)
TMS:
TREMEDRAFT_31269
CCAC:
CcaHIS019_0209910
(CcaverHIS019_0209910)
TVS:
TRAVEDRAFT_162531
DSQ:
DICSQDRAFT_161107
PCO:
PHACADRAFT_115300
SHS:
STEHIDRAFT_120302
HIR:
HETIRDRAFT_314737
PSQ:
PUNSTDRAFT_100849
ADL:
AURDEDRAFT_133612
FME:
FOMMEDRAFT_88475
GTR:
GLOTRDRAFT_113823
RSX:
RhiXN_03967
LBC:
LACBIDRAFT_246207
CCI:
CC1G_01401
ABP:
AGABI1DRAFT72662
(AGABI1DRAFT_72662)
ABV:
AGABI2DRAFT188569
(AGABI2DRAFT_188569)
PCUB:
JR316_0004443
MRR:
Moror_15109
MORE:
E1B28_004737
CPUT:
CONPUDRAFT_136795
SLA:
SERLADRAFT_462630
WSE:
WALSEDRAFT_52084
WIC:
J056_000920
MGL:
MGL_3292
MRT:
MRET_2403
MSYM:
MSY001_3097
PTRC:
PtA15_6A559
PSTR:
Pst134EA_002650
MLR:
MELLADRAFT_49715
RIE:
OCT59_016503
MBR:
MONBRDRAFT_22072
SRE:
PTSG_06639
DDI:
DDB_G0287769
DPP:
DICPUDRAFT_97998
DFA:
DFA_07267
ACAN:
ACA1_057440
TET:
TTHERM_00784310
PTM:
GSPATT00003835001
PTI:
PHATRDRAFT_11990
FCY:
FRACYDRAFT_170904
PIF:
PITG_19224
PSOJ:
PHYSODRAFT_503509
SPAR:
SPRG_02860
NGR:
NAEGRDRAFT_69724
EHX:
EMIHUDRAFT_430881
EMIHUDRAFT_99156
GTT:
GUITHDRAFT_72589
RBE:
RBE_0577
RBO:
A1I_03300
RIC:
BA173_06695
PTC:
phytr_2650
AMA:
AM527
AMF:
AMF_392
AMW:
U370_01980
AMP:
U128_02020
ACN:
ACIS_00777
APH:
APH_0766
APY:
YYU_03595
APD:
YYY_03590
APHA:
WSQ_03595
AOH:
AOV_01815
ERU:
Erum3550
ERW:
ERWE_CDS_03620
ERG:
ERGA_CDS_03580
ECN:
Ecaj_0339
ECH:
ECH_0725
ECHA:
ECHHL_0642
ECHJ:
ECHJAX_0410
ECHL:
ECHLIB_0407
ECHS:
ECHOSC_0655
ECHV:
ECHSTV_0400
ECHW:
ECHWAK_0407
ECHP:
ECHWP_0638
EMR:
EMUR_01760
EHH:
EHF_0636
NSE:
NSE_0668
NRI:
NRI_0645
NHM:
NHE_0632
NEF:
GP480_02700
RBT:
NOVO_06660
REN:
EF513_06750
NAF:
GQ61_04145
SXA:
FMM02_09290
SJP:
SJA_C1-26470
SINB:
SIDU_01580
SCH:
Sphch_1511
SBD:
ATN00_18980
SPMI:
K663_04735
SPHB:
EP837_00738
SPHR:
BSY17_2222
SPHT:
K426_15185
SHYD:
CJD35_10000
SCLO:
SCLO_1014410
SFLA:
SPHFLASMR4Y_00202
SPHY:
CHN51_12565
SMIC:
SmB9_11990
(bioC)
GBE:
GbCGDNIH1_0593
GBH:
GbCGDNIH2_0593
GBC:
GbCGDNIH3_0593
GBS:
GbCGDNIH4_0593
GXY:
GLX_05670
GXL:
H845_1681
KNA:
B0W47_02670
KEU:
S101446_00949
(bioC)
KSC:
CD178_02389
KRE:
GWK63_08490
ASV:
WG31_06125
AACE:
A0U92_07870
APOM:
CPF11_01830
ATO:
CIW82_12470
ACET:
DS739_05840
COQ:
D9V35_00695
COMM:
GN303_00890
EBLA:
JGUZn3_19260
KHA:
IFJ82_07835
RGI:
RGI145_07440
ROS:
CTJ15_09975
RMUC:
FOB66_09485
AZL:
AZL_001590
ALI:
AZOLI_2833
ATI:
AL072_03800
AHU:
A6A40_11305
AZM:
DM194_10875
AOZ:
HUE56_11060
NAO:
Y958_12240
NCB:
C0V82_22260
RPM:
RSPPHO_01492
MGY:
MGMSRv2__3574
MGRY:
MSR1_32840
(bioC_3)
MAGX:
XM1_3838
(ndufaf5)
THAL:
A1OE_387
EFK:
P856_229
FER:
FNB15_01355
DEX:
HWD60_18165
DVN:
HQ394_03555
MAG:
amb1605
HJO:
AY555_00625
TXI:
TH3_14895
THAC:
CSC3H3_13270
TII:
DY252_07170
MAGQ:
MGMAQ_2917
TMO:
TMO_0357
ECOG:
FIV45_17815
» show all
Taxonomy
UniProt
Reference
PMID:
18940309
Authors
Sugiana C, Pagliarini DJ, McKenzie M, Kirby DM, Salemi R, Abu-Amero KK, Dahl HH, Hutchison WM, Vascotto KA, Smith SM, Newbold RF, Christodoulou J, Calvo S, Mootha VK, Ryan MT, Thorburn DR
Title
Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease.
Journal
Am J Hum Genet 83:468-78 (2008)
DOI:
10.1016/j.ajhg.2008.09.009
Sequence
[hsa:
79133
]
LinkDB
All DBs
DBGET
integrated database retrieval system