Lemur catta (Ring-tailed lemur): 123624071
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Entry
123624071 CDS
T08326
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
lcat
Lemur catta (Ring-tailed lemur)
Pathway
lcat00280
Valine, leucine and isoleucine degradation
lcat00640
Propanoate metabolism
lcat00785
Lipoic acid metabolism
lcat01100
Metabolic pathways
lcat01210
2-Oxocarboxylic acid metabolism
Module
lcat_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
lcat00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
123624071 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
123624071 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
123624071 (BCKDHA)
Enzymes [BR:
lcat01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
123624071 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
123624071
NCBI-ProteinID:
XP_045387576
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Position
19:complement(28603923..28623959)
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AA seq
444 aa
AA seq
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MAVAVAAARVWGPGRGLGQAALLALRRPGARGLARSHPHRQQQFSSLEDKPQFPGASAEF
VDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRILYE
SQRQGRISFYMTNYGEEGTHVGSAAALDTTDLVFGQYREAGVLMYRDYPLELFMAQCYSN
VSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANKVVICYFGEGAA
SEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGLISIRVDGN
DVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPI
SRLRRYLLGRGWWDDEQEKAWRKQSRKRVMEAFEQAERKLKPNPNLLFSDVYQEMPAQLR
KQQESLARHLQTYGEHYPLDHFEK
NT seq
1335 nt
NT seq
+upstream
nt +downstream
nt
atggcggtcgcggtggctgcggccagggtctgggggccaggccgagggctgggccaggct
gccctcctggcgctgcggcggcctggggctcgggggctggctagatctcacccccacagg
cagcagcagttctcgtctctggaggacaagcctcagttcccaggggcctcggcagagttt
gtagacaaacttgaattcatccagcccaatgtcatctctggaatccccatctaccgcgtc
atggaccggcagggccagatcatcaaccccagcgaggatccccatctgccccaggagaaa
gtcctgaagttctacaagagcatgacgctgctcaacaccatggaccgcatcctctatgag
tctcagcggcagggccggatctccttctacatgaccaactatggcgaggaggggacgcac
gtggggagtgcagcggccctggacaccaccgacctggtttttggccaataccgggaggca
ggtgtgctgatgtaccgggactaccccctggaactgttcatggcccagtgctacagcaac
gtgagtgacctgggcaaggggcgccagatgcccgtccactacggttgcaaggaacgccac
tttgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcggcctac
gcggccaagcgggccaatgccaacaaggtcgtcatctgttacttcggcgagggagcagct
agcgagggggacgcccatgctggcttcaactttgccgccacgcttgagtgccccatcatc
ttcttctgccggaacaacggctacgccatctccacgcccacctctgagcagtaccgcggg
gacggcattgcggcgcgaggccccgggtacggcctcatttccatccgagtggacggcaac
gatgtgttcgccgtgtacaacgccacaaaggaggctcggcggcgggctgttgcggagaac
cagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagcgatgac
agctctgcctaccgctccgtggacgaggttaattactgggacaagcaggaccaccccatc
tcccggctgaggcgctacctgctgggccgaggctggtgggacgacgagcaggagaaggcc
tggaggaagcagtcccgcaagagggtgatggaggcctttgagcaggctgagcggaagctg
aagcccaaccccaacctgctcttctcagacgtgtatcaagagatgcccgcccagctccgc
aagcagcaggagtccctggcccgtcacctgcagacctatggggagcactaccccctggac
cactttgagaagtga
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