KEGG   Lemur catta (Ring-tailed lemur): 123624071
Entry
123624071         CDS       T08326                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
lcat  Lemur catta (Ring-tailed lemur)
Pathway
lcat00280  Valine, leucine and isoleucine degradation
lcat00640  Propanoate metabolism
lcat00785  Lipoic acid metabolism
lcat01100  Metabolic pathways
lcat01210  2-Oxocarboxylic acid metabolism
Module
lcat_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:lcat00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    123624071 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    123624071 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    123624071 (BCKDHA)
Enzymes [BR:lcat01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     123624071 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 123624071
NCBI-ProteinID: XP_045387576
LinkDB
Position
19:complement(28603923..28623959)
AA seq 444 aa
MAVAVAAARVWGPGRGLGQAALLALRRPGARGLARSHPHRQQQFSSLEDKPQFPGASAEF
VDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRILYE
SQRQGRISFYMTNYGEEGTHVGSAAALDTTDLVFGQYREAGVLMYRDYPLELFMAQCYSN
VSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANKVVICYFGEGAA
SEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGLISIRVDGN
DVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPI
SRLRRYLLGRGWWDDEQEKAWRKQSRKRVMEAFEQAERKLKPNPNLLFSDVYQEMPAQLR
KQQESLARHLQTYGEHYPLDHFEK
NT seq 1335 nt   +upstreamnt  +downstreamnt
atggcggtcgcggtggctgcggccagggtctgggggccaggccgagggctgggccaggct
gccctcctggcgctgcggcggcctggggctcgggggctggctagatctcacccccacagg
cagcagcagttctcgtctctggaggacaagcctcagttcccaggggcctcggcagagttt
gtagacaaacttgaattcatccagcccaatgtcatctctggaatccccatctaccgcgtc
atggaccggcagggccagatcatcaaccccagcgaggatccccatctgccccaggagaaa
gtcctgaagttctacaagagcatgacgctgctcaacaccatggaccgcatcctctatgag
tctcagcggcagggccggatctccttctacatgaccaactatggcgaggaggggacgcac
gtggggagtgcagcggccctggacaccaccgacctggtttttggccaataccgggaggca
ggtgtgctgatgtaccgggactaccccctggaactgttcatggcccagtgctacagcaac
gtgagtgacctgggcaaggggcgccagatgcccgtccactacggttgcaaggaacgccac
tttgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcggcctac
gcggccaagcgggccaatgccaacaaggtcgtcatctgttacttcggcgagggagcagct
agcgagggggacgcccatgctggcttcaactttgccgccacgcttgagtgccccatcatc
ttcttctgccggaacaacggctacgccatctccacgcccacctctgagcagtaccgcggg
gacggcattgcggcgcgaggccccgggtacggcctcatttccatccgagtggacggcaac
gatgtgttcgccgtgtacaacgccacaaaggaggctcggcggcgggctgttgcggagaac
cagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagcgatgac
agctctgcctaccgctccgtggacgaggttaattactgggacaagcaggaccaccccatc
tcccggctgaggcgctacctgctgggccgaggctggtgggacgacgagcaggagaaggcc
tggaggaagcagtcccgcaagagggtgatggaggcctttgagcaggctgagcggaagctg
aagcccaaccccaacctgctcttctcagacgtgtatcaagagatgcccgcccagctccgc
aagcagcaggagtccctggcccgtcacctgcagacctatggggagcactaccccctggac
cactttgagaagtga

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