KEGG   Mirounga angustirostris (Northern elephant seal): 123855692
Entry
123855692         CDS       T11530                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mano  Mirounga angustirostris (Northern elephant seal)
Pathway
mano00280  Valine, leucine and isoleucine degradation
mano00640  Propanoate metabolism
mano00785  Lipoic acid metabolism
mano01100  Metabolic pathways
mano01210  2-Oxocarboxylic acid metabolism
Module
mano_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mano00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    123855692 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    123855692 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    123855692 (BCKDHA)
Enzymes [BR:mano01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     123855692 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 123855692
NCBI-ProteinID: XP_045747546
LinkDB
Position
Unknown
AA seq 446 aa
MAVAAAAARVWGSSRGLGQAGLLLLRRPGARGLARSLPQRQAQQHFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPVYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNSSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKPKPSPSLLFSDVYQEMPAQ
LRKQQEALARHLQTYGEHYPLDHFEK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgcagcagcgagggtctggggctcaagtcgaggcttgggccaggct
ggcctcctgctcctgcggcggcctggggctcgggggctggccagatctctcccccagaga
caggcgcagcagcacttcccgtccctggatgacaagccccagttcccaggggcctcggcg
gagtttgtagacaagctagaattcatccagcccaatgtcatctctgggatccccgtctac
cgtgtcatggatcgccagggccagatcatcaaccccagcgaggatccccacctgccccag
gagaaggtgctcaagttttacaagagcatgactttgctcaacaccatggaccgcatcctc
tatgagtcccagcgacagggccggatctccttctacatgaccaactacggcgaggagggg
acgcacgtggggagcgcagcagcgctggacaacacggacctggtgttcggccagtaccgg
gaggcaggtgtgctcatgtaccgggactaccccctggagctgttcatggcccagtgctac
ggcaattcgagtgacctgggcaagggccgccagatgcctgtgcactacggctgcaaggag
cgccactttgtcaccatctcctctccgctggccacgcagatcccgcaggcggtgggggcg
gcctacgcagccaagcgggccaacgccaacagggtggtcatctgctacttcggggagggg
gcggccagcgagggggacgcacacgccggcttcaacttcgccgccaccctcgagtgcccc
atcatcttcttctgccggaacaacggctatgccatctccacgcccacctcagagcagtac
cgcggggacggcatcgctgcccgaggccccggctatggcatcatgtccatccgcgtggat
ggcaacgacgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgcgctgtggcg
gagaaccagcccttcctcatcgaggccatgacctacaggatcggccaccacagcactagt
gatgacagctcagcctaccgctcggtggacgaggtcaattactgggacaagcaggaccac
cccatctcccggctgcgccactacctgcagagccggggctggtgggacgacgagcaggag
aaggcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggcggagcgg
aagccaaagcccagccccagcctgctcttctcagacgtgtaccaggagatgcccgcccag
ctccgcaagcagcaggaggccctggcccggcacctccagacctacggggagcactacccc
ctggaccactttgagaagtga

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