Macaca mulatta (rhesus monkey): 708258
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Entry
708258 CDS
T01028
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X4
KO
K01968
3-methylcrotonyl-CoA carboxylase alpha subunit [EC:
6.4.1.4
]
Organism
mcc
Macaca mulatta (rhesus monkey)
Pathway
mcc00280
Valine, leucine and isoleucine degradation
mcc01100
Metabolic pathways
Module
mcc_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mcc00001
]
09100 Metabolism
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
708258 (MCCC1)
Enzymes [BR:
mcc01000
]
6. Ligases
6.4 Forming carbon-carbon bonds
6.4.1 Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
6.4.1.4 methylcrotonoyl-CoA carboxylase
708258 (MCCC1)
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Paralog
Gene cluster
GFIT
Motif
Pfam:
CPSase_L_D2
Biotin_carb_N
Biotin_carb_C
Biotin_lipoyl
Dala_Dala_lig_C
ATP-grasp
Biotin_lipoyl_2
RimK
ATP-grasp_3
ATPgrasp_ST
GARS_A
BT_MCC_alpha
ATP-grasp_4
RnfC_N
NQRA_N
Motif
Other DBs
NCBI-GeneID:
708258
NCBI-ProteinID:
XP_014986991
Ensembl:
ENSMMUG00000010553
UniProt:
A0A1D5QNQ9
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Position
2:complement(88278506..88360831)
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AA seq
731 aa
AA seq
DB search
MAAASAVSVLLVAAERNRWHRLPSLLLPPRFPGLFRTWVWRQRTMKYTTTTGRNITKVLI
ANRGEIACRVMRTARKLGVQSVAVYSEADRNSMHVDMADEAYSIGPAPSQQSYLSMEKII
QVAKTSAAQAIHPGYGFLSENMEFAELCKQEGIIFIGPPPSAIRDMGIKSTSKSIMAAAG
VPVVEGYHGEDQSDQCLKEHAGRIGYPVMIKAVRGGGGKGMRIVRSEQEFQEQLESARRE
AKKSFNDDAVLIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPAPGI
KPEVRKKLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTD
LVEWQLRIAAGEKIPLSQEEITLQGHAFEARIYAEDPSNNFMPGAGPLVHLSTPPADPST
RIETGVRQGDEVSVHYDPMIAKLVVWAADRQAALTKLRYSLRQYNIIGLHTNIDFLLNLS
GHPEFEAGNVHTDFIPQHHKELLLSRKAAAKESLCQAALGLILKEKAMTDAFTLQAHDQF
SPFSSSSGRRLNISYTRNMTLKDGKNNVAIAVTYNHDGSYSMQIEDKTFQVLGDLYSEED
CTYLKCSVNGVASKAKLIILENTIYLFSKEGSIEIDIPVPKYLSSVSSEGTQGGPLAPMT
GTIEKVFVKAGDKVKAGDSLMVMIAMKMEHTIKAPKDGTIKKVFYREGAQANRHTPLVEF
EEEESDKRESE
NT seq
2196 nt
NT seq
+upstream
nt +downstream
nt
atggcggcagcctctgcggtgtcggtgctgctggtggcggcggagaggaaccggtggcat
cgtctcccgagcctgctcctgccgccgaggtttccagggctcttcaggacatgggtgtgg
aggcaaagaaccatgaagtacacaacaaccacaggaagaaacattaccaaggtcctcatt
gcaaacagaggagaaattgcctgcagggtgatgcgcacagccagaaaactgggtgtacag
tctgtggcagtttatagtgaggctgacaggaattccatgcatgtagatatggcagatgaa
gcatattccatcggtcctgctccctcccagcagagctacctatctatggagaaaatcatt
caagtggccaagacctctgctgcacaggctatccatccaggatatggttttctttcagaa
aacatggaatttgctgaactttgtaagcaagaaggaattatttttataggccctcctcca
tctgcaattagagacatgggtataaagagcacatccaaatccataatggctgctgctgga
gtacctgttgtggagggttatcatggtgaggaccaatcagatcagtgcctgaaggaacac
gccgggagaattggctatcctgtcatgattaaagccgtccggggtggaggaggaaaagga
atgaggatcgttagatcggagcaagaatttcaagaacagttagaatcagcgcggagagaa
gctaagaagtctttcaatgatgatgctgtgctgattgagaagtttgtagacacaccgagg
catgtagaagtccaggtgtttggtgaccaccatggcaatgctgtgtacttgtttgaaaga
gactgtagtgtgcagagacgacatcagaagatcattgaggaggccccagcgcctggtatt
aaacctgaagtaagaaaaaagctgggagaagctgcagtcagagctgctaaagctgtaaat
tatgttggagcagggactgtggagtttattatggactcgaaacataatttctatttcatg
gagatgaatacaaggctgcaagtggaacatcctgttactgagatgatcacaggaactgac
ttggtggagtggcagcttagaattgcagcaggagagaagattcctttgagccaggaagaa
ataactctgcagggccatgccttcgaagctagaatatatgcagaagatcctagtaataac
ttcatgcctggggctggcccattagtgcacctctctacccctccagcagatccttccacc
aggattgaaactggagtgcggcaaggagatgaagtttccgtgcattacgaccccatgatt
gcaaagctggtcgtgtgggctgcagatcgccaggcagcattgacaaaactgaggtacagc
cttcgtcagtacaatattattggactgcacaccaacattgacttcttactcaatctgtct
ggccacccagagtttgaagctgggaacgtgcacactgatttcatccctcaacaccacaaa
gaattgttgcttagtcggaaggctgcagccaaagagtctttatgccaggcagccctgggt
ctcatcctcaaggagaaagccatgaccgacgctttcactcttcaggcacatgatcaattc
tctccattttcatctagcagtggaagaagactgaatatctcttataccagaaacatgact
cttaaagatggtaaaaacaatgtagccatagctgtaacgtataaccatgatgggtcttat
agcatgcagattgaagataaaactttccaggtccttggcgatctttacagcgaggaagac
tgcacttacctgaaatgttctgttaatggagttgctagtaaagctaagttgattatcctg
gaaaacactatttacctattttccaaggaaggaagtattgagattgacattccagtcccc
aaatacttatcttctgtgagctcagaaggaactcagggaggccccctagctcctatgact
ggaaccattgaaaaggtgtttgtcaaagctggagacaaagtgaaagcgggagattccctc
atggttatgatcgccatgaagatggagcataccataaaagctccaaaggatggcacaata
aagaaagtgttctacagagaaggtgctcaggccaacagacacactcctttagtggagttt
gaggaggaagagtcagacaaaagggaatcagaataa
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