KEGG   Macaca fascicularis (crab-eating macaque): 102134149
Entry
102134149         CDS       T02918                                 
Symbol
BCKDHA, BCKDE1A
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mcf  Macaca fascicularis (crab-eating macaque)
Pathway
mcf00280  Valine, leucine and isoleucine degradation
mcf00640  Propanoate metabolism
mcf00785  Lipoic acid metabolism
mcf01100  Metabolic pathways
mcf01210  2-Oxocarboxylic acid metabolism
Module
mcf_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mcf00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    102134149 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    102134149 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    102134149 (BCKDHA)
Enzymes [BR:mcf01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     102134149 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 102134149
NCBI-ProteinID: NP_001271018
Ensembl: ENSMFAG00000041490
UniProt: Q8HXY4 A0A2K5WWP9
LinkDB
Position
19:join(48541216..48541323,48554368..48554547,48554652..48554738,48560349..48560457,48565748..48565909,48568711..48568917,48569176..48569317,48569545..48569716,48570997..48571167)
AA seq 445 aa
MAVAIAAARVWRPNRGLSQAALLLLWRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLEHFDK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtagcgatcgctgcagcgagggtctggcggccaaaccgaggcctgagccaggct
gccctcttgctgctgtggcggcctggggctcggggattggctagatctcacccgcacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggctgag
tttatagacaagttggaattcatccagcccaatgttatctctggaatccccatctaccgt
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccaaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggagggcacg
cacgtggggagtgccgccgccctggacaacacagacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgcgactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcggcagatgcctgtccactacggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacacagatccctcaggcggtgggggcagcc
tacgcagccaagcgggccaatgccaacagggtcgtcatctgttacttcggtgagggggcg
gccagcgagggggatgcccacgccggcttcaacttcgcggccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcattgcggcacgaggccccgggtatggcatcatgtcaatccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacggcgcgctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcggcgtaccgctcggtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcaagagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggcagagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcactttgataagtga

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