Entry |
|
Symbol |
BCKDHA, BCKDE1A
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
mcf Macaca fascicularis (crab-eating macaque)
|
Pathway |
mcf00280 | Valine, leucine and isoleucine degradation |
mcf01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
mcf_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:mcf00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
102134149 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
102134149 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
102134149 (BCKDHA)
Enzymes [BR:mcf01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
102134149 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
19:join(48541216..48541323,48554368..48554547,48554652..48554738,48560349..48560457,48565748..48565909,48568711..48568917,48569176..48569317,48569545..48569716,48570997..48571167)
|
AA seq |
445 aa
MAVAIAAARVWRPNRGLSQAALLLLWRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLEHFDK |
NT seq |
1338 nt +upstreamnt +downstreamnt
atggcggtagcgatcgctgcagcgagggtctggcggccaaaccgaggcctgagccaggct
gccctcttgctgctgtggcggcctggggctcggggattggctagatctcacccgcacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggctgag
tttatagacaagttggaattcatccagcccaatgttatctctggaatccccatctaccgt
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccaaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggagggcacg
cacgtggggagtgccgccgccctggacaacacagacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgcgactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcggcagatgcctgtccactacggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacacagatccctcaggcggtgggggcagcc
tacgcagccaagcgggccaatgccaacagggtcgtcatctgttacttcggtgagggggcg
gccagcgagggggatgcccacgccggcttcaacttcgcggccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcattgcggcacgaggccccgggtatggcatcatgtcaatccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacggcgcgctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcggcgtaccgctcggtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcaagagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggcagagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcactttgataagtga |