KEGG   Macrotis lagotis (bilby): 141509533
Entry
141509533         CDS       T11097                                 
Symbol
BCKDHA
Name
(RefSeq) LOW QUALITY PROTEIN: 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mlao  Macrotis lagotis (bilby)
Pathway
mlao00280  Valine, leucine and isoleucine degradation
mlao00640  Propanoate metabolism
mlao00785  Lipoic acid metabolism
mlao01100  Metabolic pathways
mlao01210  2-Oxocarboxylic acid metabolism
Module
mlao_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mlao00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    141509533 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    141509533 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    141509533 (BCKDHA)
Enzymes [BR:mlao01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     141509533 (BCKDHA)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C
Other DBs
NCBI-GeneID: 141509533
NCBI-ProteinID: XP_074075252
LinkDB
Position
1:903348946..903356460
AA seq 592 aa
MPGALGEHARGRCLLGHVVSVHFNLPPSLPPAPADGCSAARAAGEGARGTVATLFAVAGR
HAFPQPRPRPRPEKAISCPERRRDRKGARPYPGPGPAEGRGVRGPDLPGLTAPPRARGVW
LTRGGGTGRAAAAQAGQRRRHRAGTAPLQMAMAAAAAAAAARAWALRGGLVWARRGPRGL
AGSATHRQQENFSSLDEKPQFPGASAEFVDKLDFIKPNVISGIPIYRVMDRQGQIINVSE
DPQLPQEVVLKLYRSMTLLNTMDRILYESQRQGRISFYMTNYGEEGTHVGSAAALEDTDL
VFGQYREAGVLMYRGFPLELFMSQCYGNSGDPSKGRQMPVHYGCRERNFVTISSPLATQI
PQAVGAAYAAKRANSNQAVICYFGEGAASEGDAHAGFNFAATLECPIIFFCRNNGYAIST
PTSEQYRGDGIAARGPGYGIMSIRVDGNDVFAVYNATREARRRAVAENQPFLIEAMTYRI
GHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRQYMLSRGWWDEEQEKAWRKQSRKKVMEA
FEEAERKRKPPLGLIFSDVYQEMPAQLQKQQEALARHLQTYGEHYPLDHYEQ
NT seq 1779 nt   +upstreamnt  +downstreamnt
atgcccggagccctcggggagcatgcgcgaggtcgttgtttgctcgggcacgtggtttcg
gtccacttcaacctccctccctccctccccccagctcctgcggacggctgcagcgccgca
cgagcggcgggagagggcgctcgcggcacggtggcgacactgtttgccgtggccggacgc
cacgctttccctcagccccgcccccggccgaggccggagaaggctattagttgtccagag
cggaggcgggaccggaagggcgcgaggccctatcccggcccgggcccggccgaggggcgg
ggcgtccgaggacccgacctccccgggctgaccgcgccgccgagggcccgaggggtgtgg
ctgacgcggggcggcggcacaggccgggcagcggcggcacaggccgggcagcggcggcgg
caccgcgcgggcacggctccgctccagatggcgatggcggcggcggcggcggcggcggcg
gcgcgagcctgggccctgcgaggggggctggtgtgggcccggcgcgggccccgcggactg
gcgggatccgccacccataggcagcaggaaaatttttcatccctggatgaaaagccccag
ttccctggtgcctctgctgagtttgtggataagctagacttcattaagcccaatgtcatt
tctggcatccccatctaccgggtgatggatcgtcaggggcagatcatcaatgtcagcgaa
gatcctcagctgcctcaggaggtggttctgaagctgtacagaagtatgacccttctcaac
accatggatcggatcctctatgagtcccagaggcagggccggatctccttctacatgacc
aactacggggaggagggcactcacgtgggcagtgcagctgccctggaggacacagacctg
gtgtttggccaataccgagaagcaggagtgctgatgtaccggggtttccccctggagctg
ttcatgtcccagtgctatggcaactcaggagaccccagcaagggccgccagatgccagtc
cactatggctgcagggaaaggaactttgtcaccatctcctccccactggccacgcagatc
ccacaggcggttggagcagcctacgcagccaagagggccaactccaaccaggctgtgatc
tgctactttggggagggggcagccagtgagggtgatgcccatgctggcttcaactttgct
gccaccttggagtgtcccatcatcttcttctgccgcaacaacggctacgccatctctact
cccacctcagagcagtatcggggtgatggcattgctgcccgaggccctggctatggcatc
atgtccatccgagtggacggcaatgatgtgtttgcagtgtacaatgccaccagagaggcc
cggcggcgagcagtggctgagaaccagcccttcctcatcgaggccatgacttacaggata
gggcaccacagcaccagtgacgacagctcggcctatcgttctgtggacgaggtgaactat
tgggacaagcaagaccaccccatctcccggctgcgccagtacatgctgagccgagggtgg
tgggatgaggagcaggagaaggcctggaggaaacagtccagaaagaaggtgatggaggcc
tttgaagaggctgaacgaaagcggaagcctccccttggcctcatcttttcagatgtgtac
caagagatgccagcccaactccagaaacagcaggaagccttggcccgccacctgcagacc
tatggcgagcactacccactggaccattatgagcagtga

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