Mirounga leonina (Southern elephant seal): 118022626
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Entry
118022626 CDS
T07472
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
mlx
Mirounga leonina (Southern elephant seal)
Pathway
mlx00280
Valine, leucine and isoleucine degradation
mlx00640
Propanoate metabolism
mlx00785
Lipoic acid metabolism
mlx01100
Metabolic pathways
mlx01210
2-Oxocarboxylic acid metabolism
Module
mlx_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mlx00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
118022626 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
118022626 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
118022626 (BCKDHA)
Enzymes [BR:
mlx01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
118022626 (BCKDHA)
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Paralog
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
118022626
NCBI-ProteinID:
XP_034879167
LinkDB
All DBs
Position
Unknown
AA seq
446 aa
AA seq
DB search
MAVAAAAARVWGSSRGLGQAGLLLLRRPGARGLARSLPQRQAQQHFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPVYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNSSDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKPKPSPSLLFSDVYQEMPAQ
LRKQQEALARHLQTYGEHYPLDHFEK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcggtggcggctgcagcagcgagggtctggggctcaagtcgaggcttgggccaggct
ggcctcctgctcctgcggcggcctggggctcgggggctggccagatctctcccccagaga
caggcgcagcagcacttcccgtccctggatgacaagccccagttcccaggggcctcggcg
gagtttgtagacaagctagaattcatccagcccaatgtcatctctgggatccccgtctac
cgtgtcatggatcgccagggccagatcatcaaccccagcgaggatccccatctgccccag
gagaaggtgctcaagttttacaagagcatgactttgctcaacaccatggaccgcatcctc
tatgagtcccagcgacagggccggatctccttctacatgaccaactacggcgaggagggg
acgcacgtggggagcgcagcagcgctggacaacacggacctggtgttcggccagtaccgg
gaggcaggtgtgctcatgtaccgggactaccccctggagctgttcatggcccagtgctac
ggcaattcgagtgacctgggcaagggccgccagatgcccgtgcactacggctgcaaggag
cgccactttgtcaccatctcctctccgctggccacgcagatcccgcaggcggtgggggcg
gcctacgcagccaagcgggccaacgccaacagggtggtcatctgctacttcggggagggg
gcggccagcgagggggacgcacacgccggcttcaacttcgccgccaccctcgagtgcccc
atcatcttcttctgccggaacaacggctatgccatctccacgcccacctcagagcagtac
cgcggggacggcatcgctgcccgaggccccggctatggcatcatgtccatccgcgtggat
ggcaacgacgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgcgctgtggcg
gagaaccagcccttcctcatcgaggccatgacctacaggatcggccaccacagcactagt
gatgacagctcagcctaccgctcggtggacgaggtcaattactgggacaagcaggaccac
cctatctcccggctgcgccactacctgcagagccggggctggtgggacgacgagcaggag
aaggcctggaggaagcagtcccgcaaaaaggtgatggaggcctttgagcaggcggagcgg
aagccaaagcccagccccagcctgctcttctcagacgtgtaccaggagatgcccgcccag
ctccgcaagcagcaggaggccctggcccggcacctccagacctacggggagcactacccc
ctggaccactttgagaagtga
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