KEGG   Microcebus murinus (gray mouse lemur): 105869117
Entry
105869117         CDS       T07238                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
mmur  Microcebus murinus (gray mouse lemur)
Pathway
mmur00280  Valine, leucine and isoleucine degradation
mmur00640  Propanoate metabolism
mmur00785  Lipoic acid metabolism
mmur01100  Metabolic pathways
mmur01210  2-Oxocarboxylic acid metabolism
Module
mmur_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mmur00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    105869117 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    105869117 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    105869117 (BCKDHA)
Enzymes [BR:mmur01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     105869117 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 105869117
NCBI-ProteinID: XP_012616197
Ensembl: ENSMICG00000002010
UniProt: A0A8C5W5T9
LinkDB
Position
22:complement(22085526..22107013)
AA seq 446 aa
MAVVVAAARFWGPSRGLGQAALLALRRPGARGLARSHPHRQQQQQFSSLEDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPQLPQEQVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVSDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGLISIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRRYLLGRGWWDDEQEKAWRKQSRKRVMEAFEQAERKLKPNPNLLFSDVYQEMPVQ
LRKQQESLSRHLQTYGEHYPLDHFEK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcggtagtggtcgctgcggccaggttctgggggccaagccgaggcctgggccaggct
gccctcctggcgctgcggcggcccggagctcgggggctggctagatctcacccccacagg
cagcagcagcagcagttctcatctctggaggacaagcctcagttcccaggggcctcggca
gagttcatagacaaactggaattcatccagcccaatgtcatctccggaatccccatctac
cgcgtcatggaccggcagggccagatcatcaaccccagcgaggacccccaactgccccag
gagcaagtcctgaagttctacaagagcatgacgctgctcaacaccatggaccgcatcctc
tatgagtctcagcggcagggccggatctccttctacatgaccaactacggcgaggagggg
acgcacgtggggagcgcagcggccctggacaacacggacctggtttttggccagtaccgg
gaggcaggtgtgctgatgtaccgcgactaccccctggaactgttcatggctcagtgctac
ggcaacgtgagtgaccctggcaaggggcgccagatgcccgtccactacggttgcaaggag
cgccacttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcg
gcctacgcggccaagcgggccaacgccaacagggtggtcatctgttacttcggcgagggg
gcagccagcgagggggacgcccacgccggcttcaacttcgccgccacacttgagtgtccc
atcatcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtac
cgcggggatggcattgcggcacgaggccctgggtacggcctcatttccatccgcgtggac
ggcaacgatgtattcgccgtgtacaacgccacaaaggaggcccggcggcgggctgttgcg
gagaaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagt
gatgacagctctgcctaccgctccgtggatgaggtcaattactgggacaagcaggaccac
cccatctcccggctgaggcgctacctgctgggccgaggctggtgggacgacgagcaggag
aaggcctggaggaagcagtcccgcaagagggtgatggaggcctttgagcaggccgagcgg
aagctgaagcccaaccccaacctgctcttctcagatgtgtatcaagagatgcctgtccag
ctccgcaagcagcaggagtccctgtcccgtcacctgcagacctacggggagcactacccc
ctggaccactttgagaagtga

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