KEGG   Mustela putorius furo (domestic ferret): 101689276
Entry
101689276         CDS       T07239                                 
Symbol
MCCC1
Name
(RefSeq) methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
mpuf  Mustela putorius furo (domestic ferret)
Pathway
mpuf00280  Valine, leucine and isoleucine degradation
mpuf01100  Metabolic pathways
Module
mpuf_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mpuf00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    101689276 (MCCC1)
Enzymes [BR:mpuf01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     101689276 (MCCC1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 RimK ATPgrasp_ST ATP-grasp_3 BT_MCC_alpha GARS_A ATP-grasp_4 PTS_EIIA_1 NQRA_N RnfC_N HlyD_D23 DUF2118 Orn_DAP_Arg_deC
Other DBs
NCBI-GeneID: 101689276
NCBI-ProteinID: XP_004745140
Ensembl: ENSMPUG00000002371
UniProt: A0A8U0TCQ0
LinkDB
Position
Unknown
AA seq 725 aa
MAAASAVSVLLVAAERSRWLRVPGLLLPSRRWTWKQRTMKYATTTGQNIAKLLIANRGEI
ACRVIRTAKKMGIQSVAVYSDADRNSMHVDMADEAYSIGPAPSQQSYLSMEKIIHVAKTS
AAQAIHPGYGFLSENTEFAELCKQEGILFIGPPSSAIKDMGIKSTSKSIMAAAGVPVVEG
YHGEDQSDQCLREHAGRIGYPVMIKAVRGGGGKGMRIVRSEEEFQEQLESARREAKKSFN
DDAMLIEKFVDTPRHVEVQVFGDYHGNAVYLFERDCSVQRRHQKIIEEAPGPGIKPEIRK
KLGEAAVRAAKAVNYVGAGTVEFIMDSKHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQL
RIAAGEKIPLSQEEITLQGHSFEARIYAEDPDNNFMPGAGPLVHLSTPQADLCTRIETGV
RQGDEVSVHYDPMIAKLVVWGADRQAALTKLRYSLRQYNIVGLHTNIDFLLNLSGHPEFE
AGNVHTDFIAQHHKELFPSRKATAKEFLCQAALGLILQEKAVSDIFNVQSQDQYSPFASS
SGRRLNISYTRNITLRDGKNNVAIAVTYNHDGSYSMRIEDETFQVLGDLCTEGDYTYLKC
SVNGVASKTKLIILENTIYLFSMEGSTQIGIPVPKYLSSVSSDGTQEGAIAPMTGTIEKI
FVKVGDKVKAGDSLMVMIAMKMEHTIKAPKDGTIKTVFYKEGSQANRHALLIEFEEEASD
QRKAK
NT seq 2178 nt   +upstreamnt  +downstreamnt
atggccgcagcctctgcggtgtcggtgctgctagtagcggcggagaggagccggtggctg
cgagtcccgggcctgctgctgccgtccaggagatggacttggaagcagagaaccatgaag
tatgcaacgaccacaggacaaaacattgccaagctcctcattgcaaacagaggagaaatt
gcctgcagggtgatacgaacagccaaaaaaatgggtatacagtccgtggctgtgtatagt
gacgccgacaggaattccatgcatgttgacatggcagatgaagcatattccatcggcccc
gctccctctcagcagagctacctttctatggagaaaatcattcacgtggccaagacctct
gctgcccaggctatccatccaggatatggttttctttccgaaaacacggaatttgccgaa
ctgtgtaaacaagaaggaattctttttataggtcctccttcatctgcaattaaagacatg
ggtataaagagcacatccaaatccataatggctgctgccggagtgcctgttgtggaaggt
tatcatggcgaggaccagtcagaccagtgcctgagggagcacgcggggagaatcggttat
cctgtcatgattaaagctgtccgtggtggaggagggaaaggcatgaggattgtcagatcc
gaagaggaatttcaagaacagttagaatcagcacggagagaagctaagaaatctttcaat
gatgatgcgatgctgattgagaagtttgtagacactccaaggcatgtagaagtccaggtg
tttggtgactaccatggcaatgctgtgtacttgtttgaaagagactgtagtgtacagagg
aggcatcagaagatcattgaggaagccccagggcctggtattaaacctgaaataagaaaa
aagcttggagaagctgcagtcagagctgctaaagctgtaaattatgttggagcaggaact
gtggagtttattatggactcaaagcacaatttctacttcatggaaatgaatacaaggctg
caagtggaacatcctgttactgagatgatcacaggaactgacttggtggagtggcagctt
aggattgcagcaggagagaagattcctttgagccaggaagaaataactctgcagggccat
tcctttgaagctagaatatatgcagaagatcctgacaataacttcatgccgggggctggg
ccattagtgcatctctccacccctcaggcagacctttgcactaggattgaaactggagtg
agacaaggagatgaggtttcagtgcattacgacccaatgattgcaaagctggttgtatgg
ggtgcagatcgccaggcagccttaacaaaactgaggtatagccttcgtcagtacaatata
gtcggactgcataccaacattgacttcctccttaacctgtctggccacccagagtttgag
gctgggaatgtgcacacagatttcatcgctcaacaccacaaagaactgtttcccagtagg
aaggccacagctaaggagtttttatgccaggcagctctgggtctcatcctccaggagaaa
gctgtgtctgatattttcaatgttcagtcacaagatcagtactccccttttgcatccagc
agtggaagaagactgaatatctcttacacaagaaacataactctgagggatggtaaaaac
aatgtagccatagctgtaacatataaccatgatgggtcctatagcatgcggattgaagat
gaaactttccaagtccttggtgatctttgtactgagggagactacacttacctgaaatgt
tctgttaatggagttgctagtaaaactaagctaattatcctggaaaatactatttaccta
ttttccatggaaggaagtacacagattggcattccagtccccaaatacttgtcttcagtg
agctcagatggaactcaggaaggagccatagctcctatgacgggtaccattgaaaagata
tttgtgaaagttggagacaaagtaaaagctggagattctctaatggttatgattgccatg
aaaatggagcacaccataaaggctccaaaggatggcacgatcaagaccgtgttctacaaa
gaaggttctcaggccaacagacacgctcttttaatcgagtttgaggaagaggcatctgac
caaagaaaagcaaaataa

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