Mauremys reevesii (Reeves's turtle): 120388958
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Entry
120388958 CDS
T07797
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
mrv
Mauremys reevesii (Reeves's turtle)
Pathway
mrv00280
Valine, leucine and isoleucine degradation
mrv00640
Propanoate metabolism
mrv00785
Lipoic acid metabolism
mrv01100
Metabolic pathways
mrv01210
2-Oxocarboxylic acid metabolism
Module
mrv_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mrv00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
120388958 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
120388958 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
120388958 (BCKDHA)
Enzymes [BR:
mrv01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
120388958 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
DUF6409
Motif
Other DBs
NCBI-GeneID:
120388958
NCBI-ProteinID:
XP_039367023
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Position
LG22:1985799..1993816
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AA seq
438 aa
AA seq
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MAAGWGLRRGLGRLLLLGGPRGARGLGTARVLRQQQEFTSLEEKPQFPGASADFVDKLDF
IQPNMISGIPIYRVMDRQGQIINPDEDPQLSQEQVLKFYKTMTLLNTMDRILYESQRQGR
ISFYMTNYGEEGTHVGSAAALDDADLVFGQYREAGVLMYRGYPLDLFMAQCYGNASDTGK
GRQMPVHYGCRDRHFVTISSPLATQIPQAVGAAYAFKRDNASRAVICYFGEGAASEGDAH
AGFNFAATLECPILFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDGNDVFAVY
NATREARRRAIAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRHH
MVGRGWWDEEQEKSWRKKSRKRVMEAFEQAERKLKPSPQHLFSDVYCEMPSHLQKQQEAL
ARHLRLYGEHYPLEHFEK
NT seq
1317 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgggctgggggctgcggcggggcctggggcggctgctgctgctggggggcccg
cggggggcccggggcctcggcaccgcccgcgtactccggcagcagcaggagttcacctcc
ctggaggagaagccgcagtttcctggagcctcggctgattttgtggacaagctggatttt
atccagcccaacatgatctcggggatccccatctaccgggtcatggaccggcaggggcag
atcatcaacccggacgaagatccccagctctcgcaggagcaggtgctgaagttctacaag
accatgacgctgctcaacacgatggaccggatcctgtacgagtcgcagaggcagggcagg
atctccttctacatgacgaactacggggaggaggggacgcacgtgggcagcgccgcggcg
ctggatgacgcagacctggtgttcgggcagtaccgggaagcaggcgtgctgatgtaccgg
ggttaccccctggacctcttcatggcccagtgctacggcaacgccagcgataccggcaaa
gggcgccagatgccagtgcactacggctgcagagaccggcacttcgtcaccatctcgtcc
ccgctggccacgcagatcccccaggccgtgggggccgcctacgccttcaagcgggacaac
gccagccgggccgtgatctgctacttcggggagggcgcggccagcgagggcgacgcccac
gccggcttcaacttcgccgccaccctggagtgccccatcctcttcttctgccgcaacaac
ggctacgccatctccacgcccacctcggagcagtaccgcggcgacggcatcgcggcccgc
gggcccggctacgggatcatgtccatccgtgtggacgggaatgacgtcttcgccgtgtac
aacgccacgcgggaggcccggcgccgggccatcgccgagaaccagcccttcctcatcgag
gccatgacctacaggattgggcaccacagcacgagtgacgacagctcggcctatcgctcg
gtggacgaggtgaactactgggacaagcaggaccaccccatctcccgcctgcggcaccac
atggtgggccggggctggtgggacgaggagcaggagaagagctggaggaagaaatcccgc
aagagggtcatggaggcctttgagcaggcggagcggaagctgaagcccagcccgcagcac
ctgttctcggacgtgtactgcgagatgccctcgcacctgcagaagcagcaggaggcgctg
gcgcggcacctccggctctacggggagcactaccccctggagcacttcgagaagtga
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