Maylandia zebra (zebra mbuna): 101474711
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Entry
101474711 CDS
T02814
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
mze
Maylandia zebra (zebra mbuna)
Pathway
mze00280
Valine, leucine and isoleucine degradation
mze00640
Propanoate metabolism
mze00785
Lipoic acid metabolism
mze01100
Metabolic pathways
mze01210
2-Oxocarboxylic acid metabolism
Module
mze_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
mze00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
101474711 (bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
101474711 (bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
101474711 (bckdha)
Enzymes [BR:
mze01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
101474711 (bckdha)
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Motif
Pfam:
E1_dh
DXP_synthase_N
TPP_enzyme_C
Motif
Other DBs
NCBI-GeneID:
101474711
NCBI-ProteinID:
XP_004560526
UniProt:
A0A3P9DEA2
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Position
LG14:complement(31265972..31273291)
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AA seq
446 aa
AA seq
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MAAVSSMSKMYGLCFRAVRQTAGLKAYRLLQRRGFRVTVLQLQQTFDSSLEKPQFPGASA
EFVDQLEFIQPNVISGIPVYRVMDRQGNIINPSQDPQLSKETVLNFYQKMTMLNTMDRIL
YESQRQGRISFYMTNYGEEGTHIGSAAALDPNDLVFGQYREAGVLMYRGFPLDHFMAQCY
ANADDLGKGRQMPVHYGSKDLNFVTISSPLATQIPQAAGAAYAVKRENTNRAVICYFGEG
AASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMLSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYMTARGWWSEDDERSWRKQSRKTVMEAFERAERRLKPNPELLFTDVYQEMIPS
LNKQRESLWRHVQQYKENYPLDLYEK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcagctgtgagcagcatgagcaaaatgtatgggctctgtttccgcgctgtccgtcag
acagcaggactgaaggcatatcgactgcttcagcgcagaggcttcagggtaactgttctt
cagctgcagcagacctttgactcttcgctggaaaagccccagtttccaggagcctcggcc
gagtttgtggatcagctcgagttcatccagcccaatgtcatctctgggatcccagtgtac
cgcgtgatggacaggcagggaaatatcatcaacccctctcaagaccctcagctctccaaa
gagacagttttgaacttttatcagaagatgacgatgctgaacacaatggaccgcattctt
tatgagtctcaaagacagggtcggatctccttctacatgactaactatggtgaggagggg
acacacatcggcagtgctgctgctctggatccaaacgatctggtttttgggcaatacaga
gaagctggagtgctgatgtaccgaggctttcctctggatcacttcatggctcagtgttac
gccaatgctgatgacctcggaaagggccggcagatgcccgtccactatggctccaaagat
ctgaactttgtcaccatctcatctcctctggccacacagattcctcaggcggctggagct
gcgtatgcagtcaagagagagaacacaaaccgtgccgtcatttgctattttggagaagga
gcagctagcgaaggggatgcacacgccggcttcaacttctctgccacccttgagtgccca
ctgatatttttttgccgcaacaatggctacgccatctctacccctacaaacgaacagtat
agaggtgatggcatcgctgctcgtggtcctggttatggcatgttgtccattcgtgttgat
ggtaatgatgtgtttgctgtgtacaacgctacaaaggaagcgaggcgcagggctgtggct
gagaaccagccattcctcattgaggcaatgacctacagaattggccaccacagcaccagc
gatgacagctcggcgtaccgttcagtggatgaagtgaactattgggacaaacaggaccat
cccatttccaggctgagacattacatgacagcccgcggatggtggagtgaagatgacgag
aggagctggcgaaaacaatcgcgcaagacggtgatggaggcgtttgagagggctgaaagg
cggctcaaacccaatcctgaactgttgttcacagacgtgtaccaggagatgatacccagc
ctgaacaagcagagagagtccctgtggagacatgtgcagcagtacaaagagaactaccca
ctagacttgtatgaaaaataa
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