KEGG   Neomonachus schauinslandi (Hawaiian monk seal): 110583115
Entry
110583115         CDS       T08474                                 
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
nsu  Neomonachus schauinslandi (Hawaiian monk seal)
Pathway
nsu00280  Valine, leucine and isoleucine degradation
nsu00640  Propanoate metabolism
nsu00785  Lipoic acid metabolism
nsu01100  Metabolic pathways
nsu01210  2-Oxocarboxylic acid metabolism
Module
nsu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:nsu00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    110583115 (BCKDHB)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    110583115 (BCKDHB)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    110583115 (BCKDHB)
Enzymes [BR:nsu01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     110583115 (BCKDHB)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C Toxin_YhaV
Other DBs
NCBI-GeneID: 110583115
NCBI-ProteinID: XP_021548859
UniProt: A0A2Y9HHI9
LinkDB
Position
8:complement(77165809..77378839)
AA seq 392 aa
MAALAATAGGLLRLRAAGAEGQWRRLRGAGLLRGLLQPDSATGVAAQRRHVAHFTFQPDP
EPQEYGQTQKMNLFQAVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRAPWGCVGHGALYHSQSPEAFFAHCPGIKVVVPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPVEPYSIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCE
VIDLRTILPWDMDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcggcgttagcggcgactgcgggcgggctgttgaggctacgtgcggccggggcggaa
ggacagtggcgtcggcttcgaggcgcggggctgctgcggggcttgctgcagccggactcg
gccactggggttgcggcgcagaggaggcatgtggctcacttcactttccagccggacccg
gagccccaggagtatgggcaaactcagaaaatgaatcttttccaggcggtaacaagtgcc
ttggataactcattggctaaagatcctactgcagtaatatttggtgaagatgtcgccttt
ggaggagtctttagatgtacggttggcttgcgagacaagtatggaaaagatagagttttc
aacacgccgttgtgtgaacaaggaatcgttgggtttggaattgggattgcagtcactgga
gcgaccgctattgcagaaattcagtttgcagattatattttccctgctttcgatcagatt
gttaatgaagctgccaagtaccgctatcgctctggggatctttttaattgtggaagcctc
actatccgggccccttggggctgtgtcggccatggggctctttatcattctcagagtcct
gaagctttttttgctcactgcccaggaatcaaggtggttgtacccagaagccctttccag
gccaagggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagtggagcaggttcctgtagaaccatacagcattcccctg
tcccaggccgaagtcattcaggaagggagtgacgtgactctagttgcctggggcactcag
gttcatgtgatccgagaggtggcttccatggctcaagagaagcttggagtgtcttgtgaa
gtcattgatctgaggactatcctaccttgggacatggatacagtttgcaagtctgtgatc
aaaacagggcgactgctaatcagtcacgaggctcccttgacaggcggctttgcatcggag
atcagctctacagttcaggaagaatgtttcctgaacctagaggctcctatatcaagagta
tgtgggtatgacacaccgtttcctcatattttcgaaccattctacatcccagacaaatgg
aaatgctatgatgcccttcgaaaaatgatcaactattga

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