| Hydrolysis of ganglioside |
| GM2A activation of HEXA and HEXB |
| Loss of GM2A activation |
| Hydrolysis of GA1 |
| Hydrolysis of globoside |
| Hydrolysis of lactosylceramide |
| Glucosylceramide synthesis in GBA deficiency |
| Saposin stimulation of GBA and GALC |
| Loss of saposin stimulation |
| Hydrolysis of galabiosylceramide |
| Hydrolysis of psychosine |
| Hydrolysis of galactosylceramide sulfate |
| Hydrolysis of sphingomyelin |