KEGG   Oryctolagus cuniculus (rabbit): 100352048
Entry
100352048         CDS       T03373                                 
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X2
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
ocu  Oryctolagus cuniculus (rabbit)
Pathway
ocu00280  Valine, leucine and isoleucine degradation
ocu00640  Propanoate metabolism
ocu00785  Lipoic acid metabolism
ocu01100  Metabolic pathways
ocu01210  2-Oxocarboxylic acid metabolism
Module
ocu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:ocu00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100352048
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100352048
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100352048
Enzymes [BR:ocu01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100352048
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 100352048
NCBI-ProteinID: XP_002722340
Ensembl: ENSOCUG00000023789
LinkDB
Position
Unknown
AA seq 443 aa
MALAISAARVWGPRRQAVPLLLRQLGARGLTRSLPRWQQQQQFSSLDDKPQFPGASAEFI
DKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYQSMTLLNTMDRILYES
QRQGRISFYMTNYGEEGTHVGSAAALENTDLVFGQYREAGVLMYRDYPLELFMAQCYGNV
SDRGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGAAS
EGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDGND
VFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPIS
RLRHFLLSRGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPPQLRK
QQESLARHLQTYGEHYPLDHFDK
NT seq 1332 nt   +upstreamnt  +downstreamnt
atggcgttagcgatttccgcggcgagggtctgggggcctaggcgccaggctgtgcccctg
ttgctgcggcagcttggggcgcgggggctgactagatccctccccaggtggcagcagcag
cagcagttctcctccctggacgacaagccgcagttccccggggcctcggcggagttcata
gacaagctcgagttcatccagcccaatgtcatctcgggcatccccatctaccgcgtcatg
gaccggcagggccagatcatcaaccccagcgaggacccccacctgccccaggagaaggtg
ctgaagttctaccagagcatgacgctgctcaacaccatggaccgcatcctctacgagtcc
cagcggcagggccggatctccttctacatgaccaactacggtgaggagggcacacatgtg
gggagtgcggccgccctggaaaacacagacctggtgtttggccagtatcgggaggcaggc
gtgctgatgtaccgggactaccccctggagctgttcatggcccagtgctatggcaatgtg
agcgaccggggcaaggggcgccagatgcccgtccactacggctgcaaggagcgccacttt
gtcaccatctcctctccactggcaacgcagatccctcaggcggtgggggcagcctacgcc
gccaagcgggccaacgccaacagggtcgtcatctgctacttcggggagggggcggccagc
gagggggatgcccacgcaggcttcaacttcgccgccacactcgagtgtcccatcatcttc
ttctgccggaacaatggctacgccatctccacgcccacctctgagcagtaccgcggggac
ggcatcgcggcacgtggccctggctacggcatcatgtcaatccgcgtggacggcaacgac
gtgtttgccgtgtacaacgccacgaaggaggcccggcggcgggcagtggccgagaaccag
cccttcctcattgaggccatgacctacagaatcggccaccacagcaccagtgacgacagc
tccgcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccaccccatctcc
cggctgcggcacttcctgctgagccgcggctggtgggacgaggagcaggagaaggcctgg
aggaagcagtctcgcaagaaggtgatggaagccttcgagcaggccgagcggaagctgaag
cccagccccagcctgctcttctcggacgtgtatcaggagatgcccccccagctccgcaag
cagcaagagtccctggcccggcacctgcagacctacggggagcactaccccctggaccac
ttcgacaagtga

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