Oryctolagus cuniculus (rabbit): 100352048
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Entry
100352048 CDS
T03373
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X2
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
ocu
Oryctolagus cuniculus (rabbit)
Pathway
ocu00280
Valine, leucine and isoleucine degradation
ocu00640
Propanoate metabolism
ocu00785
Lipoic acid metabolism
ocu01100
Metabolic pathways
ocu01210
2-Oxocarboxylic acid metabolism
Module
ocu_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
ocu00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100352048
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100352048
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100352048
Enzymes [BR:
ocu01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100352048
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
100352048
NCBI-ProteinID:
XP_002722340
Ensembl:
ENSOCUG00000023789
LinkDB
All DBs
Position
Unknown
AA seq
443 aa
AA seq
DB search
MALAISAARVWGPRRQAVPLLLRQLGARGLTRSLPRWQQQQQFSSLDDKPQFPGASAEFI
DKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYQSMTLLNTMDRILYES
QRQGRISFYMTNYGEEGTHVGSAAALENTDLVFGQYREAGVLMYRDYPLELFMAQCYGNV
SDRGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGAAS
EGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDGND
VFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPIS
RLRHFLLSRGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPPQLRK
QQESLARHLQTYGEHYPLDHFDK
NT seq
1332 nt
NT seq
+upstream
nt +downstream
nt
atggcgttagcgatttccgcggcgagggtctgggggcctaggcgccaggctgtgcccctg
ttgctgcggcagcttggggcgcgggggctgactagatccctccccaggtggcagcagcag
cagcagttctcctccctggacgacaagccgcagttccccggggcctcggcggagttcata
gacaagctcgagttcatccagcccaatgtcatctcgggcatccccatctaccgcgtcatg
gaccggcagggccagatcatcaaccccagcgaggacccccacctgccccaggagaaggtg
ctgaagttctaccagagcatgacgctgctcaacaccatggaccgcatcctctacgagtcc
cagcggcagggccggatctccttctacatgaccaactacggtgaggagggcacacatgtg
gggagtgcggccgccctggaaaacacagacctggtgtttggccagtatcgggaggcaggc
gtgctgatgtaccgggactaccccctggagctgttcatggcccagtgctatggcaatgtg
agcgaccggggcaaggggcgccagatgcccgtccactacggctgcaaggagcgccacttt
gtcaccatctcctctccactggcaacgcagatccctcaggcggtgggggcagcctacgcc
gccaagcgggccaacgccaacagggtcgtcatctgctacttcggggagggggcggccagc
gagggggatgcccacgcaggcttcaacttcgccgccacactcgagtgtcccatcatcttc
ttctgccggaacaatggctacgccatctccacgcccacctctgagcagtaccgcggggac
ggcatcgcggcacgtggccctggctacggcatcatgtcaatccgcgtggacggcaacgac
gtgtttgccgtgtacaacgccacgaaggaggcccggcggcgggcagtggccgagaaccag
cccttcctcattgaggccatgacctacagaatcggccaccacagcaccagtgacgacagc
tccgcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccaccccatctcc
cggctgcggcacttcctgctgagccgcggctggtgggacgaggagcaggagaaggcctgg
aggaagcagtctcgcaagaaggtgatggaagccttcgagcaggccgagcggaagctgaag
cccagccccagcctgctcttctcggacgtgtatcaggagatgcccccccagctccgcaag
cagcaagagtccctggcccggcacctgcagacctacggggagcactaccccctggaccac
ttcgacaagtga
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