KEGG   Oryx dammah (scimitar-horned oryx): 120872407
Entry
120872407         CDS       T07255                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
oda  Oryx dammah (scimitar-horned oryx)
Pathway
oda00280  Valine, leucine and isoleucine degradation
oda00640  Propanoate metabolism
oda00785  Lipoic acid metabolism
oda01100  Metabolic pathways
oda01210  2-Oxocarboxylic acid metabolism
Module
oda_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:oda00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    120872407 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    120872407 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    120872407 (BCKDHA)
Enzymes [BR:oda01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     120872407 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 120872407
NCBI-ProteinID: XP_040108683
LinkDB
Position
Unknown
AA seq 447 aa
MAVAAAAARVWRPSRGLGRAGLPLLRLLGARGLARSHPHRWQQQRRFSSLDDKPQFPGAS
AEFIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRDYPLELFMAQC
YGNVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGE
GAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHHLQSRGWWDDEQEKAWRKQSRRKVMEAFEQAEQKLKPNPNLIFSDVYQEMPA
QLRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgcggcggcgagggtttggagaccaagtcgaggcttaggacgggcg
ggcctcccgctcctgcggctgcttggggctcgtgggctggctagatctcacccccacagg
tggcagcaacagcggcgcttctcgtccctggatgacaagccgcagttcccaggggcctca
gcggagttcatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatc
taccgggtcatggaccggcagggccagatcatcaaccccagcgaagatccccacctgccc
caggagaaggtgctcaaattctataagagcatgaccctgctcaacaccatggaccgcatc
ctctatgagtcccagaggcagggccgcatatccttctacatgaccaactatggcgaagag
gggacgcacgtgggcagcgcggcagccctggacgacacagacctagtgtttggccagtac
cgggaggcaggtgtgctcatgtaccgagactaccccctggagctgttcatggcccagtgc
tacggcaacgtgagcgacctgggcaaggggcgccagatgcccgtccactacggctgcagg
gagcgccacttcgtcaccatctcctctccactggccacgcagatcccccaggcggtcggg
gcagcctacgcagccaagcgggccaacgccaacagggtggtcatctgttacttcggagag
ggggcggccagtgagggggacgcccacgccggcttcaacttcgccgccaccctcgagtgc
cccatcatcttcttctgtcggaacaacggctatgccatctccacgcccacctcggagcag
taccgcggggacggcatcgcggctcgaggccccgggtacggcatcctgtccatccgcgtg
gacggcaatgatgtgtttgccgtgtacaatgccaccaaggaggcccggcggcgggccgtg
gcggagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcacc
agtgatgacagctcggcgtaccgctcagtggatgaggtcaactactgggacaagcaggac
caccccatctcccggctgcggcatcacctgcagagccgcggctggtgggatgacgagcag
gagaaagcctggaggaagcagtcccgcaggaaggtaatggaggcctttgagcaggctgag
cagaagctgaagcccaaccccaacttgatcttctcggatgtgtatcaggagatgcctgcc
cagctccgcaagcagcaggagtctctggcacgtcacctccagacctatggcgaacactac
cccctggaccacttcgagaagtga

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