KEGG   Otolemur garnettii (small-eared galago): 100948382
Entry
100948382         CDS       T07855                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X3
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
oga  Otolemur garnettii (small-eared galago)
Pathway
oga00280  Valine, leucine and isoleucine degradation
oga00640  Propanoate metabolism
oga00785  Lipoic acid metabolism
oga01100  Metabolic pathways
oga01210  2-Oxocarboxylic acid metabolism
Module
oga_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:oga00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    100948382 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    100948382 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    100948382 (BCKDHA)
Enzymes [BR:oga01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     100948382 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 100948382
NCBI-ProteinID: XP_003802125
Ensembl: ENSOGAG00000016071
LinkDB
Position
Unknown
AA seq 446 aa
MAGAIAAARVWGPSRGLGQAALLALRRPGTRGLATSYPHRQQQQQFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINSSEDPHLPQEKVLKLYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVNDQGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLLSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPNLLFSDVYQEMPAQ
LRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcgggagcgatcgccgcggccagggtctgggggccaagccgaggcctgggccaggct
gccctcctggcgctgcggcggcctgggactcgggggctagctacatcttatccccacagg
cagcaacagcagcagttctcatctctggatgacaagccacagttcccaggggcctcagca
gagtttatagacaagcttgaattcatccagcccaatgtcatctctggaatccccatctac
cgcgtcatggaccggcagggtcagatcatcaactccagcgaggatccccatctaccccaa
gagaaggtcctgaagttgtacaagagcatgacgcttctcaacaccatggaccgcatcctg
tatgagtctcagcggcagggccggatctccttctacatgaccaactatggagaggagggg
acacatgtggggagtgcagccgctctggataacacggacctggtttttggccaataccgg
gaggcaggtgtgctgatgtatcgggactaccccctggagctattcatggcacaatgctat
ggcaatgtaaatgaccagggcaaggggcgccagatgcctgtccactatggttgcaaggaa
cgccactttgtcaccatctcctctccactggccacgcagatccctcaggctgtgggggca
gcctatgctgccaagcgggccaatgccaacagggttgtcatttgttacttcggcgagggg
gccgccagcgaaggggatgcccacgccggcttcaactttgccgccacacttgagtgcccc
atcatcttcttctgccggaacaatggctatgccatttccacgcccacatccgagcagtac
cgcggggatggcattgcggcacgaggccctgggtatggcatcatgtcgatccgcgtggac
ggtaacgatgtgttcgctgtgtacaatgctacaaaggaggcccggcggcgggctgtggca
gagaaccagcccttcctcattgaggccatgacttacaggattgggcaccacagcactagt
gatgacagctctgcataccgctcagtggacgaagtcaattactgggacaagcaggaccac
cccatctcccggctgagacactacctgctgagccgtggctggtgggacgatgaacaagag
aaagcatggaggaagcagtcccgcaagaaggtcatggaggcttttgagcaggctgagcgg
aagctgaagcctaatcccaacctgctcttctcggatgtgtatcaggagatgcctgcccag
ctccgcaagcagcaggagtccctggctcgtcacctgcagacctatggggaacactatccc
ttggatcactttgagaagtga

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