Otolemur garnettii (small-eared galago): 100948382
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Entry
100948382 CDS
T07855
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X3
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
oga
Otolemur garnettii (small-eared galago)
Pathway
oga00280
Valine, leucine and isoleucine degradation
oga00640
Propanoate metabolism
oga00785
Lipoic acid metabolism
oga01100
Metabolic pathways
oga01210
2-Oxocarboxylic acid metabolism
Module
oga_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
oga00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100948382 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100948382 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100948382 (BCKDHA)
Enzymes [BR:
oga01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100948382 (BCKDHA)
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Paralog
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
100948382
NCBI-ProteinID:
XP_003802125
Ensembl:
ENSOGAG00000016071
LinkDB
All DBs
Position
Unknown
AA seq
446 aa
AA seq
DB search
MAGAIAAARVWGPSRGLGQAALLALRRPGTRGLATSYPHRQQQQQFSSLDDKPQFPGASA
EFIDKLEFIQPNVISGIPIYRVMDRQGQIINSSEDPHLPQEKVLKLYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVNDQGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLLSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPNLLFSDVYQEMPAQ
LRKQQESLARHLQTYGEHYPLDHFEK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcgggagcgatcgccgcggccagggtctgggggccaagccgaggcctgggccaggct
gccctcctggcgctgcggcggcctgggactcgggggctagctacatcttatccccacagg
cagcaacagcagcagttctcatctctggatgacaagccacagttcccaggggcctcagca
gagtttatagacaagcttgaattcatccagcccaatgtcatctctggaatccccatctac
cgcgtcatggaccggcagggtcagatcatcaactccagcgaggatccccatctaccccaa
gagaaggtcctgaagttgtacaagagcatgacgcttctcaacaccatggaccgcatcctg
tatgagtctcagcggcagggccggatctccttctacatgaccaactatggagaggagggg
acacatgtggggagtgcagccgctctggataacacggacctggtttttggccaataccgg
gaggcaggtgtgctgatgtatcgggactaccccctggagctattcatggcacaatgctat
ggcaatgtaaatgaccagggcaaggggcgccagatgcctgtccactatggttgcaaggaa
cgccactttgtcaccatctcctctccactggccacgcagatccctcaggctgtgggggca
gcctatgctgccaagcgggccaatgccaacagggttgtcatttgttacttcggcgagggg
gccgccagcgaaggggatgcccacgccggcttcaactttgccgccacacttgagtgcccc
atcatcttcttctgccggaacaatggctatgccatttccacgcccacatccgagcagtac
cgcggggatggcattgcggcacgaggccctgggtatggcatcatgtcgatccgcgtggac
ggtaacgatgtgttcgctgtgtacaatgctacaaaggaggcccggcggcgggctgtggca
gagaaccagcccttcctcattgaggccatgacttacaggattgggcaccacagcactagt
gatgacagctctgcataccgctcagtggacgaagtcaattactgggacaagcaggaccac
cccatctcccggctgagacactacctgctgagccgtggctggtgggacgatgaacaagag
aaagcatggaggaagcagtcccgcaagaaggtcatggaggcttttgagcaggctgagcgg
aagctgaagcctaatcccaacctgctcttctcggatgtgtatcaggagatgcctgcccag
ctccgcaagcagcaggagtccctggctcgtcacctgcagacctatggggaacactatccc
ttggatcactttgagaagtga
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