KEGG   Orcinus orca (killer whale): 101285178
Entry
101285178         CDS       T05247                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
oor  Orcinus orca (killer whale)
Pathway
oor00280  Valine, leucine and isoleucine degradation
oor00640  Propanoate metabolism
oor00785  Lipoic acid metabolism
oor01100  Metabolic pathways
oor01210  2-Oxocarboxylic acid metabolism
Module
oor_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:oor00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    101285178 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    101285178 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    101285178 (BCKDHA)
Enzymes [BR:oor01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     101285178 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N DDE_Tnp_IS66
Other DBs
NCBI-GeneID: 101285178
NCBI-ProteinID: XP_004271293
LinkDB
Position
20:47402788..47421664
AA seq 445 aa
MAVAAAAARVWGSSRGLGRVGLLLLRRPGARGLARSHPQRQQQHFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPTQL
RKQQESLARHLQAYGEHYPLDHFEK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgccgcggcgagggtctggggatcaagtcgaggcttgggccgggtt
ggccttctcctcctgcggcggccaggggctcgtgggctggctagatcacatccccagagg
cagcagcagcacttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctgaagttctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcagccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactatcccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccatgccggcttcaacttcgccgccaccctcgagtgccccatc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccattcgtgtggatggc
aatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagcgac
gacagctcagcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
ctgaagcccagccccagcctgctcttctcagatgtgtatcaggagatgcctacccagctc
cgcaagcagcaggagtctttggcccgtcatctccaggcctatggggaacactaccccctg
gatcacttcgagaagtga

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