Orcinus orca (killer whale): 101285178
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Entry
101285178 CDS
T05247
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
oor
Orcinus orca (killer whale)
Pathway
oor00280
Valine, leucine and isoleucine degradation
oor00640
Propanoate metabolism
oor00785
Lipoic acid metabolism
oor01100
Metabolic pathways
oor01210
2-Oxocarboxylic acid metabolism
Module
oor_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
oor00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
101285178 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
101285178 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
101285178 (BCKDHA)
Enzymes [BR:
oor01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
101285178 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
DDE_Tnp_IS66
Motif
Other DBs
NCBI-GeneID:
101285178
NCBI-ProteinID:
XP_004271293
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Position
20:47402788..47421664
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AA seq
445 aa
AA seq
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MAVAAAAARVWGSSRGLGRVGLLLLRRPGARGLARSHPQRQQQHFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPTQL
RKQQESLARHLQAYGEHYPLDHFEK
NT seq
1338 nt
NT seq
+upstream
nt +downstream
nt
atggcggtggcggctgccgcggcgagggtctggggatcaagtcgaggcttgggccgggtt
ggccttctcctcctgcggcggccaggggctcgtgggctggctagatcacatccccagagg
cagcagcagcacttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttatagacaagctcgagttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctgaagttctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcagccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactatcccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccatgccggcttcaacttcgccgccaccctcgagtgccccatc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccattcgtgtggatggc
aatgatgtgtttgctgtgtacaacgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagcgac
gacagctcagcgtaccgctcagtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
ctgaagcccagccccagcctgctcttctcagatgtgtatcaggagatgcctacccagctc
cgcaagcagcaggagtctttggcccgtcatctccaggcctatggggaacactaccccctg
gatcacttcgagaagtga
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