Entry |
|
Symbol |
BCKDHA
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
pbrv Petaurus breviceps papuanus (sugar glider)
|
Pathway |
pbrv00280 | Valine, leucine and isoleucine degradation |
|
Module |
pbrv_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:pbrv00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
138153906 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
138153906 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
138153906 (BCKDHA)
Enzymes [BR:pbrv01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
138153906 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
Unknown
|
AA seq |
439 aa
MAAAAAAARAWALRGGLALARRGPRGLAGSAACWQQEDFSSLDEKPQFPGASAEFVDKLD
FIKPNVISGIPVYRVMDRQGQILNASEDPQLPPEAVLKLYKSMTLLNTMDRILYESQRQG
RISFYMTNYGEEGTHVGSAAALDDTDLVFGQYREAGVLMYRGYPLDLFMSQCYGNSSDPS
KGRQMPVHYGCKEKNFVTISSPLATQIPQAVGAAYAAKRANSNQAVICYFGEGAASEGDA
HAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGITSIRVDGNDVFAV
YNATREARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPISRLRH
YMLSQGWWDEEQEKAWRKQSRKKVMEAFEEAERKLKPPLGLIFSDVYQEMPAQLQKQQEA
LTRHLQAYGEHYPLDHFEQ |
NT seq |
1320 nt +upstreamnt +downstreamnt
atggcggcggcggcggcggcggcaagagcctgggccctgcgaggggggctggccttggcc
cggcgggggcctcgcggattggcgggttccgccgcctgttggcagcaagaagatttctca
tccctggatgaaaaaccccagttccctggtgcctctgctgagttcgtggataagctagac
ttcattaaacccaatgtcatttctggcatccctgtctaccgggtaatggatcgccagggc
cagatcctcaatgccagcgaggacccccagctgcctccagaggcggtcctgaagctgtat
aaaagtatgaccctgctcaacaccatggacagaatcctctatgagtcccagaggcagggc
cggatctccttctacatgaccaactatggggaggagggtacccatgtgggcagtgcagcc
gccctggatgacacagacctggtgtttgggcagtaccgggaggcaggagtgctgatgtac
cgtggctaccccctggatctgttcatgtcccagtgctatggcaactcgagcgaccccagc
aaggggcgccagatgcccgtccactatggctgcaaggaaaagaactttgtcaccatctcc
tcccccctggccacacagatccctcaggcggtcggagcagcctatgcagccaagagggcc
aattccaaccaggctgtgatctgctactttggggagggggcagccagtgagggcgatgcc
catgctggcttcaactttgctgccaccttggagtgccccatcatcttcttctgtcgcaac
aatggctacgccatctccacgcccacctcagaacagtatcggggtgatggcattgcggcc
cgagggcctggctacggcatcacgtccatccgggtagacggcaatgacgtgtttgccgtg
tacaacgcgaccagagaggcccggcggcgggcagtggcagagaaccagcccttcctcatc
gaggccatgacctacaggattggccaccacagcaccagtgatgacagctcggcttatcgt
tctgtggatgaagtaaattactgggacaaacaagaccaccccatctcccggctacgccac
tacatgctgagccaaggctggtgggatgaggagcaggagaaagcctggcggaagcagtcc
aggaagaaggtgatggaggccttcgaagaggctgaacgaaagctaaagcccccacttggc
ctcatcttctcagacgtataccaagagatgccagcccagctccagaagcagcaggaagcc
ttaacccgccacctgcaggcatatggggagcactaccctctggaccattttgaacagtga |