KEGG   Pipistrellus kuhlii (Kuhl's pipistrelle): 118702313
Entry
118702313         CDS       T07682                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
pkl  Pipistrellus kuhlii (Kuhl's pipistrelle)
Pathway
pkl00280  Valine, leucine and isoleucine degradation
pkl00640  Propanoate metabolism
pkl00785  Lipoic acid metabolism
pkl01100  Metabolic pathways
pkl01210  2-Oxocarboxylic acid metabolism
Module
pkl_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:pkl00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    118702313 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    118702313 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    118702313 (BCKDHA)
Enzymes [BR:pkl01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     118702313 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 118702313
NCBI-ProteinID: XP_036264052
LinkDB
Position
Unknown
AA seq 448 aa
MALAAGGARMWMWGPSRGLGRAGFQLLRRLGSRGLAVSHSQRQQQQHFSSLDDKPQFPGA
SAEFIDKLEFMQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKSMTLLNTMDR
ILYESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDFPLEQFMNQ
CYGNVNDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRIVICYFG
EGAASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIR
VDGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQ
DHPISRLRQYMQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPNPNLLFSDVYQEMP
AQLRKQQESLARHLQTYGEHYPLDHFEK
NT seq 1347 nt   +upstreamnt  +downstreamnt
atggcgttggcggccggtggagcgcggatgtggatgtggggaccgagtagaggcttgggc
cgggctggctttcagctcctgcggcggcttgggtctcgggggctggctgtgtctcattcg
cagagacagcagcagcagcacttctcatccctggatgacaagccccagttcccaggggcc
tcagcagagttcatagacaagctggaattcatgcaacccaatgtcatctctgggatcccc
atctaccgtgtcatggatcggcagggtcagatcatcaaccccagtgaggatccccatctg
ccgcaggagaaggtgctcaagttctataagagcatgacgctgctgaacaccatggatcgc
atcctctatgagtcccagcggcagggccggatctccttctacatgaccaactatggtgag
gaagggacgcacgtggggagtgcagcagccctggacaacactgacctggtgtttggccag
taccgagaggcaggtgtgctgatgtatcgggacttccccctggaacagttcatgaaccag
tgctacggcaacgtgaacgacctgggtaaggggcgccagatgcccgtccactatggctgc
aaggagcgtcacttcgtcaccatctcctctccactggccacacagattcctcaggcggtg
ggagcagcctacgcagccaagcgggccaatgccaacaggattgtcatctgctactttggt
gagggggcagccagtgagggggatgcccatgccggtttcaacttcgctgccacccttgag
tgccccatcatcttcttctgccgaaacaatggctatgccatttccacacccacctctgag
cagtaccgcggggatggcatcgcggctcgaggccccgggtacggcatcttgtcaatccgt
gtggatggcaatgatgtgttcgctgtgtataatgccaccaaggaggcccggcggcgggcc
gtggcggagaaccagcccttcctcattgaagccatgacctataggattgggcaccacagc
accagtgacgacagctcggcataccgctcggtggacgaggtcaattactgggacaagcag
gaccaccccatctccaggctgaggcagtacatgcagagccgcggctggtgggatgacgag
caggagaaggcctggaggaagcagtcccgcaagaaggtgatggaggccttcgagcaggcc
gagcggaagctgaagcccaatcccaatctgctcttctcggatgtgtatcaggagatgcct
gcccagctccgcaagcagcaggagtccttggcccgtcacctccagacctatggcgagcac
tatcccctggaccactttgagaagtga

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