Entry |
|
Symbol |
BCKDHA
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
pon Pongo abelii (Sumatran orangutan)
|
Pathway |
pon00280 | Valine, leucine and isoleucine degradation |
pon01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
pon_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:pon00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
100462553 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
100462553 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
100462553 (BCKDHA)
Enzymes [BR:pon01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
100462553 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
20:47161644..47191065
|
AA seq |
445 aa
MAVAIAAARVWRPNRGLSQAALLLLRRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLEHFDK |
NT seq |
1338 nt +upstreamnt +downstreamnt
atggccgtagcgatcgctgcagcgagggtctggcggccaaaccgtggcctgagccaggct
gccctcctgctgctgcggcggcctggggctcggggactggctagatctcacccccacagg
cagcagcagcagttttcatctctggatgacaagccccagttcccaggggcctcggcggag
tttatagataagttggaattcatccagcccaacgtcatctctggaatccctatctaccgc
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccgaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggtgaggagggcacg
cacgtggggagtgccgccgccctggacaacacagacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgggactaccccctggaactattcatggcccagtgctatggc
aacatcagtgacttgggcaaggggcgccagatgcccgtccactatggctgcaaggaacgc
cacttcgtcactatctcctctccactggccacgcagatccctcaggcggtgggggcggcc
tacgcagccaagcgggccaacgccaacagggtcgtcatctgttacttcggcgagggggcg
gccagtgagggggacgcccatgccggcttcaacttcgctgccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcaatatcgc
ggcgatggtattgcagcacgaggccccgggtatggcatcatgtcaatccgtgtggatggt
aatgatgtgtttgctgtgtacaacgccacaaaggaggcccgacggcgggctgtggcagag
aaccagcccttcctcatcgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcagcgtaccgctcggtggacgaggtcaattactgggataagcaggaccacccc
atctcccggctgcggcactacctgctgagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcatttcgataagtga |