KEGG   Phocoena phocoena (harbor porpoise): 136140405
Entry
136140405         CDS       T11058                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
pphc  Phocoena phocoena (harbor porpoise)
Pathway
pphc00280  Valine, leucine and isoleucine degradation
pphc00640  Propanoate metabolism
pphc00785  Lipoic acid metabolism
pphc01100  Metabolic pathways
pphc01210  2-Oxocarboxylic acid metabolism
Module
pphc_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:pphc00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    136140405 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    136140405 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    136140405 (BCKDHA)
Enzymes [BR:pphc01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     136140405 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N DDE_Tnp_IS66
Other DBs
NCBI-GeneID: 136140405
NCBI-ProteinID: XP_065754570
LinkDB
Position
20:complement(11724497..11742903)
AA seq 445 aa
MAVAAAAARVWGSSRGLGRVGLLLLRRSGARGLARSHPQRQQQPFSSLDDKPQFPGASAE
FVDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPTQL
RKQQESLARHLQTYGEHYPLDHFEK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgccgcggcgagggtttggggatcgagtcgaggcttgggccgggtt
ggccttctccttctgcggcgctcaggggctcgtgggctggctagatcacatcctcagagg
cagcagcagcccttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttgtagacaagctcgagttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctcaaattctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcagccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactaccccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccacgccggcttcaacttcgcggccaccctcgagtgccccgtc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccatccgcgtggatggc
aatgatgttttcgctgtgtacaacgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggattggacaccacagcaccagcgac
gacagctcagcgtaccgctcagtggatgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
ctgaagcccagccccagcctgctcttctcagacgtgtatcaggagatgcctacccagctc
cgcaagcagcaggagtctttggcccgtcacctccagacctatggggaacactaccccctg
gatcacttcgagaagtga

DBGET integrated database retrieval system