Phocoena phocoena (harbor porpoise): 136140405
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Entry
136140405 CDS
T11058
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
pphc Phocoena phocoena (harbor porpoise)
Pathway
pphc00280
Valine, leucine and isoleucine degradation
pphc00640
Propanoate metabolism
pphc00785
Lipoic acid metabolism
pphc01100
Metabolic pathways
pphc01210
2-Oxocarboxylic acid metabolism
Module
pphc_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
pphc00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
136140405 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
136140405 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
136140405 (BCKDHA)
Enzymes [BR:
pphc01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
136140405 (BCKDHA)
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
DDE_Tnp_IS66
Motif
Other DBs
NCBI-GeneID:
136140405
NCBI-ProteinID:
XP_065754570
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All DBs
Position
20:complement(11724497..11742903)
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AA seq
445 aa
AA seq
DB search
MAVAAAAARVWGSSRGLGRVGLLLLRRSGARGLARSHPQRQQQPFSSLDDKPQFPGASAE
FVDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKVMEAFEQAERKLKPSPSLLFSDVYQEMPTQL
RKQQESLARHLQTYGEHYPLDHFEK
NT seq
1338 nt
NT seq
+upstream
nt +downstream
nt
atggcggtggcggctgccgcggcgagggtttggggatcgagtcgaggcttgggccgggtt
ggccttctccttctgcggcgctcaggggctcgtgggctggctagatcacatcctcagagg
cagcagcagcccttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttgtagacaagctcgagttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctcaaattctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcagccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactaccccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccacgccggcttcaacttcgcggccaccctcgagtgccccgtc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccatccgcgtggatggc
aatgatgttttcgctgtgtacaacgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggattggacaccacagcaccagcgac
gacagctcagcgtaccgctcagtggatgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
ctgaagcccagccccagcctgctcttctcagacgtgtatcaggagatgcctacccagctc
cgcaagcagcaggagtctttggcccgtcacctccagacctatggggaacactaccccctg
gatcacttcgagaagtga
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