KEGG   Pongo pygmaeus (Bornean orangutan): 129038209
Entry
129038209         CDS       T10128                                 
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X2
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
ppyg  Pongo pygmaeus (Bornean orangutan)
Pathway
ppyg00280  Valine, leucine and isoleucine degradation
ppyg00640  Propanoate metabolism
ppyg00785  Lipoic acid metabolism
ppyg01100  Metabolic pathways
ppyg01210  2-Oxocarboxylic acid metabolism
Module
ppyg_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:ppyg00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    129038209 (BCKDHB)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    129038209 (BCKDHB)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    129038209 (BCKDHB)
Enzymes [BR:ppyg01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     129038209 (BCKDHB)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C
Other DBs
NCBI-GeneID: 129038209
NCBI-ProteinID: XP_054346911
LinkDB
Position
5:79633061..79885351
AA seq 392 aa
MALVAAAAGWLLRLRAAGAEGHWRRLRGAGLARGFLHPAATVEDAAQRRQVAHFTFQPDP
EPREYGQTQKMNLFQSVSSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAAEEVPIEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAKEKLEVSCE
VIDLRTIIPWDVDTICKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1179 nt   +upstreamnt  +downstreamnt
atggcgcttgtggcggcggctgccggctggctactcaggctcagggcggcaggggctgag
gggcactggcgtcggctccgtggcgcggggctggcgcggggctttctgcaccccgccgcg
actgtcgaggatgcggcccagaggcggcaggtggctcattttacttttcagccagatccg
gagccccgggagtacgggcaaactcagaaaatgaatcttttccagtcagtatcaagtgcc
ttggataactcattggccaaagatcctactgcagtaatatttggtgaagatgttgccttt
ggtggagtctttagatgcactgttggcttgcgagacaaatatggaaaagatagagttttt
aataccccattgtgtgaacaaggaatcgttggatttggaatcggaattgcggtcactgga
gctactgccattgcggaaattcagtttgcagattatattttccctgcatttgatcagatt
gttaatgaagctgccaagtatcgctatcgctctggggatctttttaactgtggaagcctc
actatccggtccccttggggctgtgttggtcatggggctctctatcattctcagagtcct
gaagcattttttgcccattgcccaggaatcaaggtggttatacccagaagccctttccag
gccaaaggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagcggaagaggtccctatagaaccatacaacattccactg
tcccaggccgaagtcatacaggaagggagtgatgttacgctagttgcctggggcactcag
gttcatgtgatccgagaggtagcttccatggcaaaagaaaagcttgaagtgtcttgtgaa
gtcattgatctgaggactataataccttgggatgtggacacaatttgtaagtctgtgatc
aaaacagggcgactgctaatcagtcacgaggctcccttgacaggcggctttgcatcggaa
atcagctctacagttcaggaggaatgtttcttgaacctagaggctcctatatcaagagta
tgtggttatgacacaccatttcctcacatttttgaaccattctacatcccagacaaatgg
aagtgttatgatgcccttcgaaaaatgatcaactattga

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