KEGG   Poecilia reticulata (guppy): 103475058
Entry
103475058         CDS       T05149                                 
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
pret  Poecilia reticulata (guppy)
Pathway
pret00280  Valine, leucine and isoleucine degradation
pret00640  Propanoate metabolism
pret00785  Lipoic acid metabolism
pret01100  Metabolic pathways
pret01210  2-Oxocarboxylic acid metabolism
Module
pret_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:pret00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    103475058 (bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    103475058 (bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    103475058 (bckdha)
Enzymes [BR:pret01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     103475058 (bckdha)
SSDB
Motif
Pfam: E1_dh DXP_synthase_N TPP_enzyme_C
Other DBs
NCBI-GeneID: 103475058
NCBI-ProteinID: XP_008424666
UniProt: A0A3P9PQT8
LinkDB
Position
LG13:29816931..29827771
AA seq 447 aa
MAAVSSMSRISGLCRHAVRQTAALKSPRLLQRRSFRVTAVQQQQEPFDSSLEKPQFPGAS
AEFVDHLEFIQPNVISGIPVYRVMDRQGKIINPSEDPQLSKETVLNFYQKMTLLNTMDRI
LYESQRQGRISFYMTNYGEEGTHIGSAAALESNDLVFGQYREAGVLMYRGFPLDLFMAQC
YANADDLGKGRQMPVHYGSKDLHFVTISSPLATQIPQAVGAAYALKRENMNRAVICYFGE
GAASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMMSIRV
DGNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQD
HPISRLRHYMTARSWWSEDDERSWRKQSRKTVMEAFEKAERRLKPNPELLFTDVYQEMVP
SLAKQRESLFRHVQQYKEHYPLDLYEK
NT seq 1344 nt   +upstreamnt  +downstreamnt
atggcggctgttagcagtatgagcagaatatctgggttatgtcgtcatgctgtccggcaa
acggctgcactgaagtcgccgaggctgctgcagcgtcggtccttcagagtcactgctgtg
cagcagcagcaggagccctttgactcgtctctggaaaagccccagtttcccggcgcctct
gcagagttcgtggaccatcttgaattcattcagcccaatgttatttccgggattcccgtg
taccgggtgatggacaggcagggcaagataatcaacccctctgaggacccccagctctcc
aaagagacggttctaaacttctaccagaagatgacgctgctgaacacaatggaccggatt
ctctacgagtctcagagacagggtcgaatctccttctacatgaccaactacggagaggag
gggacgcacatcggcagcgctgcagctctcgagtctaatgacttggtttttggtcaatac
agagaagctggagtgctgatgtaccgcggtttccccctggatctgttcatggctcagtgc
tacgccaacgccgacgacctcgggaaaggtcgccagatgcccgtccactacggctccaag
gatctgcacttcgtcaccatctcgtctcctctggccacgcagattcctcaggcggtggga
gctgcgtacgccctgaagagggagaacatgaaccgcgcggtgatctgttacttcggggag
ggagcggccagcgaaggggacgctcacgccggcttcaacttctcagcgacactcgagtgt
ccgctgatcttcttctgtcgcaacaacggctacgcgatctccaccccgaccaacgagcag
tacagaggcgacggcatcgctgctcgagggcctggttatggcatgatgtccatccgtgtc
gacgggaacgacgtgttcgccgtctacaacgccacaaaggaagcgcggcgcagggctgtg
gctgaaaaccagcctttccttatcgaggcgatgacttacagaatcgggcaccacagcacc
agcgacgacagctcggcctaccgctccgtggacgaggtgaactactgggacaagcaggac
cacccaatctcccggctgagacactacatgacggcgcgcagctggtggagcgaggacgac
gagcgcagctggaggaaacagtcacgcaagactgtgatggaggcgtttgagaaggcggag
aggcgcctgaagcccaacccagagctgctgttcaccgacgtctaccaggagatggtcccc
agtctggccaagcagagggagtccctgttcaggcacgtccagcagtacaaagagcactac
cccctcgacctgtacgagaaataa

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