KEGG   Phocoena sinus (vaquita): 116743983
Entry
116743983         CDS       T07759                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
psiu  Phocoena sinus (vaquita)
Pathway
psiu00280  Valine, leucine and isoleucine degradation
psiu00640  Propanoate metabolism
psiu00785  Lipoic acid metabolism
psiu01100  Metabolic pathways
psiu01210  2-Oxocarboxylic acid metabolism
Module
psiu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:psiu00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    116743983 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    116743983 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    116743983 (BCKDHA)
Enzymes [BR:psiu01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     116743983 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 116743983
NCBI-ProteinID: XP_032469148
Ensembl: ENSPSNG00000017396
UniProt: A0A8C9CQ32
LinkDB
Position
19:complement(11527522..11545930)
AA seq 457 aa
MAVAAAAARVWGSSRGLGRVGLLLLRRSGARGLARSHPQRQQQPFSSLDDKPQFPGASAE
FVDKLDFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKMGCKCLPESVHCPPRPWSSDTRSTAAQWAGQ
TLVSGSMCFLALPLTTSSWAHPFSSCLGLLTSELPAS
NT seq 1374 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgccgcggcgagggtttggggatcaagtcgaggcttgggccgggtt
ggccttctccttctgcggcgctcaggggctcgtgggctggctagatcacatccccagagg
cagcagcagcccttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttgtagacaagctcgatttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctcaaattctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcggccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactaccccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccacgccggcttcaacttcgcggccaccctcgagtgccccgtc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccattcgcgtggacggc
aatgatgttttcgctgtgtacaatgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggattggacaccacagcaccagcgac
gacagctcagcgtaccgctcagtggatgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaaaaagatggggtgtaagtgtctgccagagtctgtgcac
tgccctcctcggccctggtcgtcagacaccagaagcactgcggcccagtgggcagggcag
accctggtgtcaggcagcatgtgcttcctggctctgcccctgaccacgtcctcgtgggca
catcccttctcttcgtgcctcggtctcctcacctctgagctgcctgcttcttag

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