Phocoena sinus (vaquita): 116743983
Help
Entry
116743983 CDS
T07759
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
psiu
Phocoena sinus (vaquita)
Pathway
psiu00280
Valine, leucine and isoleucine degradation
psiu00640
Propanoate metabolism
psiu00785
Lipoic acid metabolism
psiu01100
Metabolic pathways
psiu01210
2-Oxocarboxylic acid metabolism
Module
psiu_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
psiu00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
116743983 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
116743983 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
116743983 (BCKDHA)
Enzymes [BR:
psiu01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
116743983 (BCKDHA)
BRITE hierarchy
SSDB
Ortholog
Paralog
Gene cluster
GFIT
Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
116743983
NCBI-ProteinID:
XP_032469148
Ensembl:
ENSPSNG00000017396
UniProt:
A0A8C9CQ32
LinkDB
All DBs
Position
19:complement(11527522..11545930)
Genome browser
AA seq
457 aa
AA seq
DB search
MAVAAAAARVWGSSRGLGRVGLLLLRRSGARGLARSHPQRQQQPFSSLDDKPQFPGASAE
FVDKLDFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEKVLKFYKTMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRNYPLELFMAQCYG
NVSDLGKGRQMPVHYGCRERHFVTISSPLATQIPQAVGAAYAAKRANANRVIICYFGEGA
ASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLQSCGWWDDEQEKAWRKQSRKKMGCKCLPESVHCPPRPWSSDTRSTAAQWAGQ
TLVSGSMCFLALPLTTSSWAHPFSSCLGLLTSELPAS
NT seq
1374 nt
NT seq
+upstream
nt +downstream
nt
atggcggtggcggctgccgcggcgagggtttggggatcaagtcgaggcttgggccgggtt
ggccttctccttctgcggcgctcaggggctcgtgggctggctagatcacatccccagagg
cagcagcagcccttctcgtccctggatgacaagccccagttcccaggggcctcggcggag
tttgtagacaagctcgatttcatccagcccaatgtcatctctgggatccccatctaccgc
gtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccaggag
aaggtgctcaaattctacaagaccatgacgctgctcaacaccatggaccgcatcctctat
gagtcccagagacagggccggatatccttctacatgaccaactatggtgaggaggggacg
cacgtggggagtgcagcggccctggacagcacggacctggtgtttggccagtaccgggag
gcaggcgtgctcatgtaccggaactaccccctggaactgttcatggcccagtgctacggc
aacgtgagcgacctgggcaaggggcgccagatgcccgtccactatggctgcagggagcgc
catttcgtcaccatctcctctccactggccacgcagatccctcaggcggtgggggcagcc
tacgcggccaagcgggccaacgccaacagggtcatcatctgttacttcggagagggcgcg
gccagtgagggggacgcccacgccggcttcaacttcgcggccaccctcgagtgccccgtc
atcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtaccgc
ggggatggcatcgcggctcgaggccccggatacggcatcctgtccattcgcgtggacggc
aatgatgttttcgctgtgtacaatgccaccaaggaggcccggcggcgggccgtggcggag
aaccagcccttcctcattgaggccatgacctacaggattggacaccacagcaccagcgac
gacagctcagcgtaccgctcagtggatgaggtcaattactgggacaagcaggaccacccc
atctcccggctgaggcactacctgcagagctgtggctggtgggacgatgagcaggagaag
gcctggaggaagcagtcccgcaaaaagatggggtgtaagtgtctgccagagtctgtgcac
tgccctcctcggccctggtcgtcagacaccagaagcactgcggcccagtgggcagggcag
accctggtgtcaggcagcatgtgcttcctggctctgcccctgaccacgtcctcgtgggca
catcccttctcttcgtgcctcggtctcctcacctctgagctgcctgcttcttag
DBGET
integrated database retrieval system