Phocoena sinus (vaquita): 116763499
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Entry
116763499 CDS
T07759
Symbol
BCKDHB
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1
KO
K00167
2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:
1.2.4.4
]
Organism
psiu
Phocoena sinus (vaquita)
Pathway
psiu00280
Valine, leucine and isoleucine degradation
psiu00640
Propanoate metabolism
psiu00785
Lipoic acid metabolism
psiu01100
Metabolic pathways
psiu01210
2-Oxocarboxylic acid metabolism
Module
psiu_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
psiu00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
116763499 (BCKDHB)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
116763499 (BCKDHB)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
116763499 (BCKDHB)
Enzymes [BR:
psiu01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
116763499 (BCKDHB)
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Motif
Pfam:
Transket_pyr
Transketolase_C
Motif
Other DBs
NCBI-GeneID:
116763499
NCBI-ProteinID:
XP_032507203
Ensembl:
ENSPSNG00000009418
UniProt:
A0A8C9BNK5
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Position
12:complement(75431816..75726959)
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AA seq
392 aa
AA seq
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MAATAVTAGRLLRLRAAGAEGHWRRLRGAGLPGGFLQPASADGDAAQRRQVAHFTFQPDP
EPLEYGQTQKMNLFQAVTSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVF
NTPLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSL
TIRSPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEP
KILYRAAVEQVPIEPYNIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAHEKLGVSCE
VIDLRTIIPWDVDTVCKSVIKTGRLLVSHEAPLTGGFASEISSTVQEECFLNLEAPISRV
CGYDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq
1179 nt
NT seq
+upstream
nt +downstream
nt
atggcggcgacggcggtcacggctggcaggctactgcggctccgcgcggccggggccgag
ggacactggcgtcggctgcgtggcgcggggctgccggggggcttcctgcagcccgcctcg
gccgacggggatgcggcccagaggcggcaggtggctcacttcactttccagcctgacccg
gagccactggagtacgggcaaactcagaaaatgaatctcttccaggcagtaacaagtgcc
ttagataactcactggccaaagaccctactgcagtaatatttggtgaagatgttgccttt
ggtggagtctttagatgtactgttggcttgcgagacaagtatggtaaagatagagttttt
aacaccccattgtgtgaacaaggaattgttggatttggaattggaattgcagtcactggt
gctaccgccattgcggaaattcagtttgcagattatattttccctgcttttgatcagatt
gttaatgaagccgctaagtatcgctatcgctctggggatctttttaattgtggaagcctc
accatccggtccccttggggctgtgtcggccatggggctctctaccattcccagagtcct
gaagctttttttgcccactgcccaggaatcaaggtggttatacccagaagccctttccag
gccaagggacttcttttgtcatgcatagaggataaaaatccttgtatattttttgaacct
aaaatactttacagggcagcagtggagcaggttcccatagaaccatacaacatcccactg
tcccaggccgaagtcatccaagaagggagtgatgtcactctagttgcctggggcactcag
gttcatgtgatccgagaggtggcttccatggctcacgagaagcttggagtgtcttgtgag
gtcattgatctgaggactataataccttgggatgtggatacagtttgcaagtctgtgatc
aaaacagggcggctgctagttagtcacgaggctcccttgacgggcggctttgcctctgag
atcagctcgacggttcaggaagaatgtttcctgaacctggaggctcctatatcgagggta
tgtgggtatgacacgccgttccctcacatttttgagccgttctacatcccagacaaatgg
aagtgctatgacgcccttcgaaaaatgatcaactattga
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