Entry |
|
Symbol |
BCKDHA
|
Name |
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
|
KO |
K00166 | 2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4] |
|
Organism |
pyu Puma yagouaroundi (jaguarundi)
|
Pathway |
pyu00280 | Valine, leucine and isoleucine degradation |
pyu01210 | 2-Oxocarboxylic acid metabolism |
|
Module |
pyu_M00036 | Leucine degradation, leucine => acetoacetate + acetyl-CoA |
|
Brite |
KEGG Orthology (KO) [BR:pyu00001]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
121018489 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
121018489 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
121018489 (BCKDHA)
Enzymes [BR:pyu01000]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
121018489 (BCKDHA)
|
SSDB |
|
Motif |
|
Other DBs |
|
LinkDB |
|
Position |
Unknown
|
AA seq |
446 aa
MAVAAVAAKLRGSGRGLGQAGVLLLRRLGARGLARYHPQRQEQQHFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPVYRVMDRQGQIINPSEDPHLPQETVLKFYKSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALDSTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNASDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEG
AASEGDAHAGFNFAATLECPVIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYLQGRGWWDDEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQ
LRKQQESLARHLQAYGEHYPLDHFEK |
NT seq |
1341 nt +upstreamnt +downstreamnt
atggcggtggcggctgttgcggcgaagctccggggctcaggtcgaggcttgggccaggct
ggcgtcctgctcctgcggcggcttggtgctcgggggctggctagatatcacccccagagg
caggagcagcagcactttccatccctggatgacaagccccagttccccggggcctcggcg
gagtttgtagacaagctagaattcatccagcccaatgtcatctctgggatccccgtctat
cgcgtcatggaccggcagggccagatcatcaaccccagcgaggatccccacctgccccag
gagacggtgctcaagttctacaagagcatgactctgctcaacaccatggaccgcatcctc
tacgagtcccagcggcagggccggatctccttctacatgaccaactatggcgaggagggg
acacatgtggggagtgcggcagcgctggacagcacggacctggtgtttggccagtaccgg
gaggcaggtgtgctaatgtaccgggactaccccctggagctgttcatggcccagtgctat
ggcaacgcgagcgacctgggcaaggggcgccagatgcccgtgcactatggctgcaaggag
cgccacttcgtcaccatctcctcgccactggccacgcagatcccgcaggcggtgggggcg
gcctatgcggccaagcgtgccaacgccaacagagtggtcatctgttacttcggggagggg
gcggccagcgagggggatgcccacgccggcttcaacttcgccgccaccctcgagtgcccg
gtcatcttcttctgccggaacaacggctatgccatctccacgcccacctctgagcagtac
cgcggggacggcatcgctgctcgaggcccgggctacggcatcatgtccatccgcgtggac
ggcaacgatgtgtttgccgtgtacaacgccaccaaggaggcccggcggcgggccgtggct
gagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagt
gacgacagctcggcctaccgctcggtggacgaggtcaattactgggacaagcaggaccac
cccatctcccggctgcggcactacctgcagggccgaggctggtgggacgacgagcaggag
aaggcctggagaaagcagtcccgcaagaaggtgatggaggcctttgagcaggcggagcgg
aagccgaagcccaaccccaacctgctcttctctgacgtgtaccaggagatgccggcccag
cttcgcaagcagcaggagtccctggcccggcacctccaggcttacggcgagcactacccc
ctggaccacttcgagaagtga |