KEGG   Sorex fumeus (smoky shrew): 130044164
Entry
130044164         CDS       T10594                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
sfum  Sorex fumeus (smoky shrew)
Pathway
sfum00280  Valine, leucine and isoleucine degradation
sfum00640  Propanoate metabolism
sfum00785  Lipoic acid metabolism
sfum01100  Metabolic pathways
sfum01210  2-Oxocarboxylic acid metabolism
Module
sfum_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:sfum00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    130044164 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    130044164 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    130044164 (BCKDHA)
Enzymes [BR:sfum01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     130044164 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 130044164
NCBI-ProteinID: XP_055992752
LinkDB
Position
Unknown
AA seq 443 aa
MAVAAVLARVWGSRRGHFGLLFLRRPGTRGLVTSHPRRQQEQFSSLDDKPQFPGASAEFI
DKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEQVLKFYRSMTLLNTMDRILYES
QRQGRISFYMTNYGEEGTHVGSAAAMDNTDLVFGQYREAGVLMYRDYPLELFMAQCYGNV
NDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRSNDNRAVICYFGEGAAS
EGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGILSIRVDGND
VFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHPIS
RLRHYLQSRGWWDDEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPVQLRK
QQEALARHLQTYGEHYPLEHFDK
NT seq 1332 nt   +upstreamnt  +downstreamnt
atggcggtggcggctgtcctggcgagggtgtgggggtcgagacgaggccactttggcctc
ctgtttctgcggcggcctgggactcgggggctggtcacatctcacccccggaggcagcag
gagcaattctcttcactggatgacaaaccccagttcccgggggcctcggcagagttcatc
gacaagctggagttcatccagcccaatgtcatctccgggatccccatctaccgcgtcatg
gaccgccagggccagatcatcaaccctagcgaggacccccatctgcccaaggagcaggtc
ctcaagttctaccggagcatgacgctgctcaacaccatggaccgcatcctctacgagtcc
cagcggcagggccggatctccttctacatgaccaactacggcgaggagggcacgcatgtg
ggcagtgctgcggccatggacaacacggaccttgtgttcggccagtaccgggaggcaggt
gtgctgatgtaccgggattaccccttggagctgttcatggcccagtgctacggcaacgtc
aacgacctgggcaaggggcgccagatgcccgtgcactatggctgcaaggagcgccacttc
gtcaccatctcctccccattggccacgcagatcccccaggcggtgggcgctgcctacgca
gctaagcggtccaacgacaacagggccgtcatctgttacttcggcgaaggggcagccagt
gagggggacgctcatgctggcttcaacttcgccgccaccctggagtgccccatcatcttc
ttctgccgaaacaatggctacgccatctccacgcccacctcggagcagtaccgcggggac
ggcattgcggcgcgaggccccggctacggcatcttgtccatccgcgtggacggcaacgat
gtgttcgctgtgtacaacgccaccaaggaggcccggcgtcgcgccgtggccgagaaccag
cccttcctcatcgaggccatgacctacaggattgggcaccacagcaccagtgacgacagc
tctgcctaccgctctgtggatgaggtcaactactgggacaagcaggaccaccccatctca
cgactgcgccactacctgcagagccgcggctggtgggacgacgagcaggagaaggcctgg
aggaagcagtcccgcaagaaggtaatggaggccttcgagcaggccgagcggaagcccaag
cccaaccccaacctgctcttctcagacgtgtaccaagagatgccagtacagctccgcaag
cagcaggaggccctggcccgccacctgcagacctacggcgagcactaccctctggagcac
tttgacaagtga

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