Scophthalmus maximus (turbot): 118299639
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Entry
118299639 CDS
T09850
Symbol
bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
smau
Scophthalmus maximus (turbot)
Pathway
smau00280
Valine, leucine and isoleucine degradation
smau00640
Propanoate metabolism
smau00785
Lipoic acid metabolism
smau01100
Metabolic pathways
smau01210
2-Oxocarboxylic acid metabolism
Module
smau_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
smau00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
118299639 (bckdha)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
118299639 (bckdha)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
118299639 (bckdha)
Enzymes [BR:
smau01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
118299639 (bckdha)
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Motif
Pfam:
E1_dh
DXP_synthase_N
TPP_enzyme_C
Motif
Other DBs
NCBI-GeneID:
118299639
NCBI-ProteinID:
XP_035479409
UniProt:
A0A2U9B408
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Position
11:6418271..6422855
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AA seq
446 aa
AA seq
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MAAVSGINKMYGVCLHAVRVTAGLRAARLLQHRAFRVGAVHQQQPFDSSLEKPQFPGASA
EFIDNLEFIQPNVISGIPIYRVMDRQGNIINPSQDPQLSKETVLNFYQKMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHIGSAAALDPNDIVFGQYREAGVLMYRGFPLDMFMAQCY
ANADDLGKGRQMPVHYGSKDLNFVTISSPLATQIPQAAGAAYAVKRENMNRAVICYFGEG
AASEGDAHAGFNFSATLECPLIFFCRNNGYAISTPTNEQYRGDGIAARGPGYGMMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRHYMTARSWWSEDDERSWRKQSRKMVMEAFEKAEKRLKPSPELLFTDVYQEMTPN
LDKQRQSMWRHVQQYKEHYPLDLYDK
NT seq
1341 nt
NT seq
+upstream
nt +downstream
nt
atggcagctgtgagcggcattaacaagatgtacggagtgtgtttgcacgccgttcgcgtg
actgcaggactgcgggcagcgaggctgcttcaacacagagccttccgagtcggggctgtg
caccagcagcagccctttgactcatcactggaaaagccacagttccccggagcctcagct
gagtttattgataatctggagttcatccagcccaatgtcatctctggaatcccaatttac
cgggtgatggacaggcaaggaaatatcatcaacccctctcaagaccctcagctctcaaaa
gagacagttttgaacttttatcagaagatgactctgctgaacacaatggaccgtattctt
tacgagtcccagagacagggtcggatctccttctacatgaccaactatggtgaggagggg
acacatatcggtagtgctgctgctcttgacccaaatgacattgtctttggtcaataccga
gaagctggagtgttgatgtaccgtggttttcctctggatatgttcatggctcagtgctac
gccaacgcagatgaccttggcaagggtcgacagatgcccgtccactatggctccaaagac
ctgaactttgtcaccatctcctctcctctggccacacagattccccaggcggctggagct
gcatacgcggtcaagagagaaaacatgaaccgtgccgtaatctgttattttggagaggga
gcagcaagtgaaggggacgcacacgctggtttcaatttctctgccaccctcgagtgccca
ctgatatttttctgtcgcaacaacggatacgccatctctacccccaccaacgagcagtac
aggggagacggcattgctgctcgtggtccgggttatggcatgatgtccatccgtgtcgat
ggcaatgatgtgtttgctgtgtacaatgccacaaaagaagctcgacgtagggctgtagct
gagaaccagccgttcctcattgaggcaatgacctacagaattggccaccacagcaccagt
gacgacagctcagcgtaccggtcggtggacgaggtgaactactgggacaagcaggaccat
cccatctccaggctgagacattacatgacggcccgcagctggtggagcgaagacgacgag
aggagctggaggaagcagtctcgcaagatggtgatggaggcattcgagaaggccgagaaa
cgcctgaagcccagtcctgagctgctgttcacagacgtgtaccaggagatgacgcccaac
ctggacaagcagagacagtccatgtggaggcacgtgcagcagtacaaagagcactaccca
cttgatctgtatgataaataa
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