Trachypithecus francoisi (Francois's langur): 117075807
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Entry
117075807 CDS
T07225
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
KO
K00166
2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:
1.2.4.4
]
Organism
tfn
Trachypithecus francoisi (Francois's langur)
Pathway
tfn00280
Valine, leucine and isoleucine degradation
tfn00640
Propanoate metabolism
tfn00785
Lipoic acid metabolism
tfn01100
Metabolic pathways
tfn01210
2-Oxocarboxylic acid metabolism
Module
tfn_M00036
Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:
tfn00001
]
09100 Metabolism
09101 Carbohydrate metabolism
00640 Propanoate metabolism
117075807 (BCKDHA)
09105 Amino acid metabolism
00280 Valine, leucine and isoleucine degradation
117075807 (BCKDHA)
09108 Metabolism of cofactors and vitamins
00785 Lipoic acid metabolism
117075807 (BCKDHA)
Enzymes [BR:
tfn01000
]
1. Oxidoreductases
1.2 Acting on the aldehyde or oxo group of donors
1.2.4 With a disulfide as acceptor
1.2.4.4 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
117075807 (BCKDHA)
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Paralog
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Motif
Pfam:
E1_dh
TPP_enzyme_C
DXP_synthase_N
Motif
Other DBs
NCBI-GeneID:
117075807
NCBI-ProteinID:
XP_033054416
LinkDB
All DBs
Position
Unknown
AA seq
445 aa
AA seq
DB search
MAVAIAAGRVWRPNRGLSQAAVLLLWRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSVRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLEHFDK
NT seq
1338 nt
NT seq
+upstream
nt +downstream
nt
atggcggtagcgatcgccgcagggagggtctggcggccaaaccgaggcctgagccaggct
gccgtcttgctgctgtggcggcctggggctcggggactggctagatctcacccacacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggctgag
tttatagacaagttggaattcatccagcccaatgttatctctggaatccccatctaccgt
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccaaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggagggcacg
cacgtggggagtgccgccgccctggacaacacagacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgcgactaccccctggaactattcatggcccagtgttatggc
aacatcagtgacttgggcaaggggcgccagatgcctgtccactatggctgcaaagaacgc
cacttcgtcactatctcctctccattggccacacagatccctcaggcggtgggggcagcc
tatgcagccaagcgggccaatgccaacagggtcgtcatctgttactttggtgagggggcg
gccagcgagggggatgcccacgccggcttcaacttcgcggccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcatcgcggcacgaggccccgggtatggcatcatgtcagtccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacggcgggctgtggcagag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcggcgtaccgctcggtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctactaagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcacttcgataagtga
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