KEGG   Trachypithecus francoisi (Francois's langur): 117075807
Entry
117075807         CDS       T07225                                 
Symbol
BCKDHA
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
tfn  Trachypithecus francoisi (Francois's langur)
Pathway
tfn00280  Valine, leucine and isoleucine degradation
tfn00640  Propanoate metabolism
tfn00785  Lipoic acid metabolism
tfn01100  Metabolic pathways
tfn01210  2-Oxocarboxylic acid metabolism
Module
tfn_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:tfn00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    117075807 (BCKDHA)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    117075807 (BCKDHA)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    117075807 (BCKDHA)
Enzymes [BR:tfn01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     117075807 (BCKDHA)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 117075807
NCBI-ProteinID: XP_033054416
LinkDB
Position
Unknown
AA seq 445 aa
MAVAIAAGRVWRPNRGLSQAAVLLLWRPGARGLARSHPHRQQQQFSSLDDKPQFPGASAE
FIDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPKEKVLKLYKSMTLLNTMDRILY
ESQRQGRISFYMTNYGEEGTHVGSAAALDNTDLVFGQYREAGVLMYRDYPLELFMAQCYG
NISDLGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANRVVICYFGEGA
ASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSVRVDG
NDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDHP
ISRLRHYLLSQGWWDEEQEKAWRKQSRKKVMEAFEQAERKPKPNPNLLFSDVYQEMPAQL
RKQQESLARHLQTYGEHYPLEHFDK
NT seq 1338 nt   +upstreamnt  +downstreamnt
atggcggtagcgatcgccgcagggagggtctggcggccaaaccgaggcctgagccaggct
gccgtcttgctgctgtggcggcctggggctcggggactggctagatctcacccacacagg
cagcagcagcagttctcatctctggatgacaagccccagttcccaggggcctcggctgag
tttatagacaagttggaattcatccagcccaatgttatctctggaatccccatctaccgt
gtcatggaccggcaaggccagatcatcaaccccagcgaggacccccacctgccaaaggag
aaggtgctgaagctctacaagagcatgacactgcttaacaccatggaccgcatcctctat
gagtctcagcggcagggccggatctccttctacatgaccaactatggcgaggagggcacg
cacgtggggagtgccgccgccctggacaacacagacctggtgtttggccagtaccgggag
gcaggtgtgctgatgtatcgcgactaccccctggaactattcatggcccagtgttatggc
aacatcagtgacttgggcaaggggcgccagatgcctgtccactatggctgcaaagaacgc
cacttcgtcactatctcctctccattggccacacagatccctcaggcggtgggggcagcc
tatgcagccaagcgggccaatgccaacagggtcgtcatctgttactttggtgagggggcg
gccagcgagggggatgcccacgccggcttcaacttcgcggccacacttgagtgccccatc
atcttcttctgccggaacaatggctacgccatctccacgcccacctccgagcagtatcgc
ggcgatggcatcgcggcacgaggccccgggtatggcatcatgtcagtccgcgtggatggt
aatgatgtgtttgctgtgtacaatgccacaaaggaggcccgacggcgggctgtggcagag
aaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagtgac
gacagttcggcgtaccgctcggtggacgaggtcaattactgggacaagcaggaccacccc
atctcccggctgcggcactacctactaagccaaggctggtgggatgaggagcaggagaag
gcctggaggaagcagtcccgcaagaaggtgatggaggcctttgagcaggccgagcggaag
cccaaacccaaccccaacctgctcttctcagacgtgtatcaggagatgcccgcccagctc
cgcaagcagcaggagtccctggcccgccacctgcagacctacggggagcactacccactg
gagcacttcgataagtga

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